PAUCITY OF INTRAHEPATIC BILE DUCTS

The paucity of intrahepatic bile ducts is characterized by reducing the quantity of interlobular bile ducts in re- lation to portal tracts of the liver. There are two defined forms of paucity of intrahepaticbile ducts: syndromatic, which is associated with various extrahepatic abnormalities and nons...

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Main Authors: O. E. Iryshkin, I. M. Iljinsky, O. M. Tsirulnikova
Format: Article
Language:Russian
Published: Federal Research Center of Transplantology and Artificial Organs named after V.I.Shumakov 2013-05-01
Series:Вестник трансплантологии и искусственных органов
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Online Access:https://journal.transpl.ru/vtio/article/view/125
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author O. E. Iryshkin
I. M. Iljinsky
O. M. Tsirulnikova
author_facet O. E. Iryshkin
I. M. Iljinsky
O. M. Tsirulnikova
author_sort O. E. Iryshkin
collection DOAJ
description The paucity of intrahepatic bile ducts is characterized by reducing the quantity of interlobular bile ducts in re- lation to portal tracts of the liver. There are two defined forms of paucity of intrahepaticbile ducts: syndromatic, which is associated with various extrahepatic abnormalities and nonsyndromatic, being the heterogeneous group of disorders, including congenital infections, metabolic, endocrine, immune disorders, congenital infections and various other disorders. In many instances paucity of intrahepatic bile ducts remains idiopathic. The review contains terminological issues, the description of the classification and the morphological characteristic, the dif- ferences of syndromatic and nonsyndromatic forms of paucity of intrahepatic bile ducts, and also the description of principles of differential diagnosis of paucity of intrahepatic bile ducts and biliary atresia.
format Article
id doaj-art-98660ae4fab54e6eb2d2a88d4ac37117
institution Kabale University
issn 1995-1191
language Russian
publishDate 2013-05-01
publisher Federal Research Center of Transplantology and Artificial Organs named after V.I.Shumakov
record_format Article
series Вестник трансплантологии и искусственных органов
spelling doaj-art-98660ae4fab54e6eb2d2a88d4ac371172025-08-20T03:59:56ZrusFederal Research Center of Transplantology and Artificial Organs named after V.I.ShumakovВестник трансплантологии и искусственных органов1995-11912013-05-0115213514110.15825/1995-1191-2013-2-135-14168PAUCITY OF INTRAHEPATIC BILE DUCTSO. E. Iryshkin0I. M. Iljinsky1O. M. Tsirulnikova2Academician V.I. Shumakov Federal Research Center of Transplantology and Artificial Organs (Head – academician of RAMSci, prof. S.V. Gautier), Moscow, Russian FederationAcademician V.I. Shumakov Federal Research Center of Transplantology and Artificial Organs (Head – academician of RAMSci, prof. S.V. Gautier), Moscow, Russian Federation Department of Tansplantology and Artificial organs (Head – academician of RAMSci, prof. S.V. Gautier) I.M. Sechenov First Moscow State Medical University (Rector – corresponding member of RAMSci, prof. P.V. Glybochko), Moscow, Russian FederationAcademician V.I. Shumakov Federal Research Center of Transplantology and Artificial Organs (Head – academician of RAMSci, prof. S.V. Gautier), Moscow, Russian Federation Department of Tansplantology and Artificial organs (Head – academician of RAMSci, prof. S.V. Gautier) I.M. Sechenov First Moscow State Medical University (Rector – corresponding member of RAMSci, prof. P.V. Glybochko), Moscow, Russian FederationThe paucity of intrahepatic bile ducts is characterized by reducing the quantity of interlobular bile ducts in re- lation to portal tracts of the liver. There are two defined forms of paucity of intrahepaticbile ducts: syndromatic, which is associated with various extrahepatic abnormalities and nonsyndromatic, being the heterogeneous group of disorders, including congenital infections, metabolic, endocrine, immune disorders, congenital infections and various other disorders. In many instances paucity of intrahepatic bile ducts remains idiopathic. The review contains terminological issues, the description of the classification and the morphological characteristic, the dif- ferences of syndromatic and nonsyndromatic forms of paucity of intrahepatic bile ducts, and also the description of principles of differential diagnosis of paucity of intrahepatic bile ducts and biliary atresia.https://journal.transpl.ru/vtio/article/view/125syndromatic and nonsyndromatic paucity of intrahepatic bile ductsalagille syndromebiliary atresiaextrahepatic and intrahepatic bile ducts
spellingShingle O. E. Iryshkin
I. M. Iljinsky
O. M. Tsirulnikova
PAUCITY OF INTRAHEPATIC BILE DUCTS
Вестник трансплантологии и искусственных органов
syndromatic and nonsyndromatic paucity of intrahepatic bile ducts
alagille syndrome
biliary atresia
extrahepatic and intrahepatic bile ducts
title PAUCITY OF INTRAHEPATIC BILE DUCTS
title_full PAUCITY OF INTRAHEPATIC BILE DUCTS
title_fullStr PAUCITY OF INTRAHEPATIC BILE DUCTS
title_full_unstemmed PAUCITY OF INTRAHEPATIC BILE DUCTS
title_short PAUCITY OF INTRAHEPATIC BILE DUCTS
title_sort paucity of intrahepatic bile ducts
topic syndromatic and nonsyndromatic paucity of intrahepatic bile ducts
alagille syndrome
biliary atresia
extrahepatic and intrahepatic bile ducts
url https://journal.transpl.ru/vtio/article/view/125
work_keys_str_mv AT oeiryshkin paucityofintrahepaticbileducts
AT imiljinsky paucityofintrahepaticbileducts
AT omtsirulnikova paucityofintrahepaticbileducts