Multinucleate cell angiohistiocytoma: a case series and literature review

Multinucleate cell angiohistiocytoma (MCAH) is a rare benign cutaneous entity. It classically presents as slowly progressive erythematous to violaceous papules on the distal extremities of middle-aged or elderly women. The entity may clinically resemble granuloma annulare, lichen planus, and several...

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Main Authors: Carolyn Szwed, Malgorzata Maj, Lidia Rudnicka, Joanna Czuwara
Format: Article
Language:English
Published: Termedia Publishing House 2024-12-01
Series:Polish Journal of Pathology
Subjects:
Online Access:https://www.termedia.pl/Multinucleate-cell-angiohistiocytoma-a-case-series-and-literature-review,55,55291,1,1.html
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author Carolyn Szwed
Malgorzata Maj
Lidia Rudnicka
Joanna Czuwara
author_facet Carolyn Szwed
Malgorzata Maj
Lidia Rudnicka
Joanna Czuwara
author_sort Carolyn Szwed
collection DOAJ
description Multinucleate cell angiohistiocytoma (MCAH) is a rare benign cutaneous entity. It classically presents as slowly progressive erythematous to violaceous papules on the distal extremities of middle-aged or elderly women. The entity may clinically resemble granuloma annulare, lichen planus, and several cutaneous vascular proliferations. Histologically, MCAH is characterized by vascular proliferation within the upper and mid-dermis, a mild perivascular inflammatory infiltrate, and charac­teristic bizarre-shaped multinucleate cells. To date, less than 200 cases have been reported in the literature. We present five of the best examples diagnosed in our department to further elucidate this peculiar entity for pathological recognition.
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institution Kabale University
issn 1233-9687
2084-9869
language English
publishDate 2024-12-01
publisher Termedia Publishing House
record_format Article
series Polish Journal of Pathology
spelling doaj-art-985e9e364d8944529b7df8afaaf05d992025-01-27T11:36:31ZengTermedia Publishing HousePolish Journal of Pathology1233-96872084-98692024-12-0175426126710.5114/pjp.2024.14570355291Multinucleate cell angiohistiocytoma: a case series and literature reviewCarolyn SzwedMalgorzata MajLidia RudnickaJoanna CzuwaraMultinucleate cell angiohistiocytoma (MCAH) is a rare benign cutaneous entity. It classically presents as slowly progressive erythematous to violaceous papules on the distal extremities of middle-aged or elderly women. The entity may clinically resemble granuloma annulare, lichen planus, and several cutaneous vascular proliferations. Histologically, MCAH is characterized by vascular proliferation within the upper and mid-dermis, a mild perivascular inflammatory infiltrate, and charac­teristic bizarre-shaped multinucleate cells. To date, less than 200 cases have been reported in the literature. We present five of the best examples diagnosed in our department to further elucidate this peculiar entity for pathological recognition.https://www.termedia.pl/Multinucleate-cell-angiohistiocytoma-a-case-series-and-literature-review,55,55291,1,1.htmlmultinucleate cell angiohistiocytoma multinucleate cells
spellingShingle Carolyn Szwed
Malgorzata Maj
Lidia Rudnicka
Joanna Czuwara
Multinucleate cell angiohistiocytoma: a case series and literature review
Polish Journal of Pathology
multinucleate cell angiohistiocytoma
multinucleate cells
title Multinucleate cell angiohistiocytoma: a case series and literature review
title_full Multinucleate cell angiohistiocytoma: a case series and literature review
title_fullStr Multinucleate cell angiohistiocytoma: a case series and literature review
title_full_unstemmed Multinucleate cell angiohistiocytoma: a case series and literature review
title_short Multinucleate cell angiohistiocytoma: a case series and literature review
title_sort multinucleate cell angiohistiocytoma a case series and literature review
topic multinucleate cell angiohistiocytoma
multinucleate cells
url https://www.termedia.pl/Multinucleate-cell-angiohistiocytoma-a-case-series-and-literature-review,55,55291,1,1.html
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AT joannaczuwara multinucleatecellangiohistiocytomaacaseseriesandliteraturereview