Neuropsychological, neuroimage and psychiatric aspects of primary Sjögren's syndrome

We report a case of a 49-year-old woman diagnosed with primary Sjögrens Syndrome (pSS) who was submitted to extensive neuropsychobiological assessment. Examination revealed a Wechsler Adult Intelligence Scale-Revised (WAIS-R) Full Scale IQ of 97 with no Verbal/Performance IQ discrepancy and performa...

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Main Authors: Gilberto N.O. Brito, Gloria R.B. Araujo, J. Angelo Papi
Format: Article
Language:English
Published: Thieme Revinter Publicações 2002-03-01
Series:Arquivos de Neuro-Psiquiatria
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Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2002000100006&tlng=en
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author Gilberto N.O. Brito
Gloria R.B. Araujo
J. Angelo Papi
author_facet Gilberto N.O. Brito
Gloria R.B. Araujo
J. Angelo Papi
author_sort Gilberto N.O. Brito
collection DOAJ
description We report a case of a 49-year-old woman diagnosed with primary Sjögrens Syndrome (pSS) who was submitted to extensive neuropsychobiological assessment. Examination revealed a Wechsler Adult Intelligence Scale-Revised (WAIS-R) Full Scale IQ of 97 with no Verbal/Performance IQ discrepancy and performance below estimated premorbid levels on arithmetic skills, visual tracking, naming and delayed paired associate learning/memory. CT scans of the brain were normal. However, there were subcortical hyperintensities on MRI and left parieto-temporal hypoperfusion on SPECT. Neuropsychological impairment is consistent with the pattern of neuroimage findings. We hypothesize that the pathophysiological mechanisms of pSS involve direct immune attack on neurons in addition to indirect effects through small-vessel angiopathy and thereby induce natural fracture lines in behavior according to location in the central nervous system.
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spelling doaj-art-95178ac3a8f44c81939f522bc0c90c522025-08-20T02:09:58ZengThieme Revinter PublicaçõesArquivos de Neuro-Psiquiatria1678-42272002-03-01601283110.1590/S0004-282X2002000100006Neuropsychological, neuroimage and psychiatric aspects of primary Sjögren's syndromeGilberto N.O. Brito0Gloria R.B. Araujo1J. Angelo Papi2Fundação Oswaldo CruzUniversidade Federal do Rio de JaneiroUniversidade Federal do Rio de JaneiroWe report a case of a 49-year-old woman diagnosed with primary Sjögrens Syndrome (pSS) who was submitted to extensive neuropsychobiological assessment. Examination revealed a Wechsler Adult Intelligence Scale-Revised (WAIS-R) Full Scale IQ of 97 with no Verbal/Performance IQ discrepancy and performance below estimated premorbid levels on arithmetic skills, visual tracking, naming and delayed paired associate learning/memory. CT scans of the brain were normal. However, there were subcortical hyperintensities on MRI and left parieto-temporal hypoperfusion on SPECT. Neuropsychological impairment is consistent with the pattern of neuroimage findings. We hypothesize that the pathophysiological mechanisms of pSS involve direct immune attack on neurons in addition to indirect effects through small-vessel angiopathy and thereby induce natural fracture lines in behavior according to location in the central nervous system.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2002000100006&tlng=enSjögren's syndromeneuropsychologyneuropsychoimmunologyneuroimagepsychiatryneuropsychobiology
spellingShingle Gilberto N.O. Brito
Gloria R.B. Araujo
J. Angelo Papi
Neuropsychological, neuroimage and psychiatric aspects of primary Sjögren's syndrome
Arquivos de Neuro-Psiquiatria
Sjögren's syndrome
neuropsychology
neuropsychoimmunology
neuroimage
psychiatry
neuropsychobiology
title Neuropsychological, neuroimage and psychiatric aspects of primary Sjögren's syndrome
title_full Neuropsychological, neuroimage and psychiatric aspects of primary Sjögren's syndrome
title_fullStr Neuropsychological, neuroimage and psychiatric aspects of primary Sjögren's syndrome
title_full_unstemmed Neuropsychological, neuroimage and psychiatric aspects of primary Sjögren's syndrome
title_short Neuropsychological, neuroimage and psychiatric aspects of primary Sjögren's syndrome
title_sort neuropsychological neuroimage and psychiatric aspects of primary sjogren s syndrome
topic Sjögren's syndrome
neuropsychology
neuropsychoimmunology
neuroimage
psychiatry
neuropsychobiology
url http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2002000100006&tlng=en
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AT gloriarbaraujo neuropsychologicalneuroimageandpsychiatricaspectsofprimarysjogrenssyndrome
AT jangelopapi neuropsychologicalneuroimageandpsychiatricaspectsofprimarysjogrenssyndrome