Angiomatoid fibrous histiocytoma â an adolescent with an unusual presentation and course
Introduction: Angiomatoid fibrous histiocytoma is a rare soft tissue neoplasm, which usually presents as an indolent mass in children and young adults and is often mistaken for a hematoma or hemangioma. Suspecting this diagnosis from imaging findings may be challenging, leading to diagnostic delays....
Saved in:
| Main Authors: | , , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Publicaciones Permanyer
2025-07-01
|
| Series: | Portuguese Journal of Pediatrics |
| Subjects: | |
| Online Access: | https://pjp.spp.pt/frame_eng.php?id=114 |
| Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
| _version_ | 1850100712986378240 |
|---|---|
| author | Sara Isabel de Almeida Sofia Cochito Sousa Cristina Mendes Rafael Cabrera Ana Lacerda |
| author_facet | Sara Isabel de Almeida Sofia Cochito Sousa Cristina Mendes Rafael Cabrera Ana Lacerda |
| author_sort | Sara Isabel de Almeida |
| collection | DOAJ |
| description | Introduction: Angiomatoid fibrous histiocytoma is a rare soft tissue neoplasm, which usually presents as an indolent mass in children and young adults and is often mistaken for a hematoma or hemangioma. Suspecting this diagnosis from imaging findings may be challenging, leading to diagnostic delays. Prognosis is generally favorable and metastases are infrequent at presentation. Case report: We describe the case of an adolescent who presented with a two-month history of a growing mass in the left scapular region, where diagnosis was made possible through surgical biopsy. Discussion: There were loco-regional lymphatic invasions and lung metastases at admission, and despite surgery and chemotherapy the disease rapidly progressed to death.
|
| format | Article |
| id | doaj-art-9467a3f6aeb44e59985f4cacdbdb4c8f |
| institution | DOAJ |
| issn | 2184-4453 |
| language | English |
| publishDate | 2025-07-01 |
| publisher | Publicaciones Permanyer |
| record_format | Article |
| series | Portuguese Journal of Pediatrics |
| spelling | doaj-art-9467a3f6aeb44e59985f4cacdbdb4c8f2025-08-20T02:40:14ZengPublicaciones PermanyerPortuguese Journal of Pediatrics2184-44532025-07-0156310.24875/PJP.M24000458Angiomatoid fibrous histiocytoma â an adolescent with an unusual presentation and courseSara Isabel de Almeida0Sofia Cochito Sousa1Cristina Mendes2Rafael Cabrera3Ana Lacerda4Paediatric Department, Hospital Beatriz Ângelo, Loures, PortugalPaediatric Department, Hospital de Santa Maria, Centro Hospitalar Universitário Lisboa Norte, Lisbon, PortugalDepartment of Paediatric Oncology, Portuguese Institute of Oncology, Lisbon, PortugalDepartment of Paediatric Oncology, Portuguese Institute of Oncology, Lisbon, PortugalDepartment of Paediatric Oncology, Portuguese Institute of Oncology, Lisbon, PortugalIntroduction: Angiomatoid fibrous histiocytoma is a rare soft tissue neoplasm, which usually presents as an indolent mass in children and young adults and is often mistaken for a hematoma or hemangioma. Suspecting this diagnosis from imaging findings may be challenging, leading to diagnostic delays. Prognosis is generally favorable and metastases are infrequent at presentation. Case report: We describe the case of an adolescent who presented with a two-month history of a growing mass in the left scapular region, where diagnosis was made possible through surgical biopsy. Discussion: There were loco-regional lymphatic invasions and lung metastases at admission, and despite surgery and chemotherapy the disease rapidly progressed to death. https://pjp.spp.pt/frame_eng.php?id=114Child. Histiocytoma malignant fibrous. Neoplasm metastasis. Soft tissue injuries. Soft tissue neoplasms. |
| spellingShingle | Sara Isabel de Almeida Sofia Cochito Sousa Cristina Mendes Rafael Cabrera Ana Lacerda Angiomatoid fibrous histiocytoma â an adolescent with an unusual presentation and course Portuguese Journal of Pediatrics Child. Histiocytoma malignant fibrous. Neoplasm metastasis. Soft tissue injuries. Soft tissue neoplasms. |
| title | Angiomatoid fibrous histiocytoma â an adolescent with an unusual presentation and course |
| title_full | Angiomatoid fibrous histiocytoma â an adolescent with an unusual presentation and course |
| title_fullStr | Angiomatoid fibrous histiocytoma â an adolescent with an unusual presentation and course |
| title_full_unstemmed | Angiomatoid fibrous histiocytoma â an adolescent with an unusual presentation and course |
| title_short | Angiomatoid fibrous histiocytoma â an adolescent with an unusual presentation and course |
| title_sort | angiomatoid fibrous histiocytoma a an adolescent with an unusual presentation and course |
| topic | Child. Histiocytoma malignant fibrous. Neoplasm metastasis. Soft tissue injuries. Soft tissue neoplasms. |
| url | https://pjp.spp.pt/frame_eng.php?id=114 |
| work_keys_str_mv | AT saraisabeldealmeida angiomatoidfibroushistiocytomaaanadolescentwithanunusualpresentationandcourse AT sofiacochitosousa angiomatoidfibroushistiocytomaaanadolescentwithanunusualpresentationandcourse AT cristinamendes angiomatoidfibroushistiocytomaaanadolescentwithanunusualpresentationandcourse AT rafaelcabrera angiomatoidfibroushistiocytomaaanadolescentwithanunusualpresentationandcourse AT analacerda angiomatoidfibroushistiocytomaaanadolescentwithanunusualpresentationandcourse |