PO75 | Prophylaxis with RFXIII: a clinical case in a pediatric patient with congenital FXIII deficiency and delayed diagnosis

Background: Congenital factor XIII (FXIII) deficiency is a rare coagulation disorder characterized by muscular or mucocutaneous bleeding with life-threatening intracranial hemorrhages (ICHs), especially in cases with severe disease. The best treatment is the use of prophylactic plasma-derived or re...

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Bibliographic Details
Format: Article
Language:English
Published: PAGEPress Publications 2025-08-01
Series:Bleeding, Thrombosis and Vascular Biology
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Online Access:https://www.btvb.org/btvb/article/view/344
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