Successful Liposteroid Therapy for a Recurrent Idiopathic Pulmonary Hemosiderosis with Down Syndrome
Idiopathic pulmonary hemosiderosis (IPH) is a rare and life-threatening disorder. Early diagnosis and appropriate management are essential for their better prognosis and patients’ quality of life (QOL). It is considered that Down syndrome patients with IPH have a worse prognosis compared to other IP...
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| Main Authors: | , , , , , , , , |
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| Format: | Article |
| Language: | English |
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Wiley
2020-01-01
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| Series: | Case Reports in Pediatrics |
| Online Access: | http://dx.doi.org/10.1155/2020/5292947 |
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| author | Hiromi Tobai Jun Yano Norio Sato Fumitaka Amanuma Mikio Takahashi Mikiya Endo Masataka Ishimura Shouichi Ohga Hidekazu Maruyama |
| author_facet | Hiromi Tobai Jun Yano Norio Sato Fumitaka Amanuma Mikio Takahashi Mikiya Endo Masataka Ishimura Shouichi Ohga Hidekazu Maruyama |
| author_sort | Hiromi Tobai |
| collection | DOAJ |
| description | Idiopathic pulmonary hemosiderosis (IPH) is a rare and life-threatening disorder. Early diagnosis and appropriate management are essential for their better prognosis and patients’ quality of life (QOL). It is considered that Down syndrome patients with IPH have a worse prognosis compared to other IPH cases. A 2-year-old girl with Down syndrome received the diagnosis of IPH after two episodes of massive pulmonary hemorrhage requiring assist ventilation, who suffered from recurrent IPH during tapering period of oral corticosteroid, started liposteroid therapy. We report here a case of successful control of recurrent IPH and improved QOL enormously with tapering dose of corticosteroid after starting liposteroid therapy. |
| format | Article |
| id | doaj-art-93f73e61392a4e20b927f66cc857a119 |
| institution | OA Journals |
| issn | 2090-6803 2090-6811 |
| language | English |
| publishDate | 2020-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Pediatrics |
| spelling | doaj-art-93f73e61392a4e20b927f66cc857a1192025-08-20T02:10:13ZengWileyCase Reports in Pediatrics2090-68032090-68112020-01-01202010.1155/2020/52929475292947Successful Liposteroid Therapy for a Recurrent Idiopathic Pulmonary Hemosiderosis with Down SyndromeHiromi Tobai0Jun Yano1Norio Sato2Fumitaka Amanuma3Mikio Takahashi4Mikiya Endo5Masataka Ishimura6Shouichi Ohga7Hidekazu Maruyama8Department of Pediatrics, Iwate Prefectural Iwai Hospital, Ichinoseki, JapanDepartment of Pediatrics, Iwate Prefectural Iwai Hospital, Ichinoseki, JapanDepartment of Pediatrics, Iwate Prefectural Iwai Hospital, Ichinoseki, JapanDepartment of Pediatrics, Iwate Prefectural Iwai Hospital, Ichinoseki, JapanDepartment of Clinical Laboratory, Iwate Prefectural Iwai Hospital, Ichinoseki, JapanDepartment of Pediatrics, Iwate Medical University, School of Medicine, Morioka, JapanDepartment of Pediatrics, Graduate School of Medical Sciences, Kyusyu University, Fukuoka, JapanDepartment of Pediatrics, Graduate School of Medical Sciences, Kyusyu University, Fukuoka, JapanDepartment of Pediatrics, Iwate Prefectural Iwai Hospital, Ichinoseki, JapanIdiopathic pulmonary hemosiderosis (IPH) is a rare and life-threatening disorder. Early diagnosis and appropriate management are essential for their better prognosis and patients’ quality of life (QOL). It is considered that Down syndrome patients with IPH have a worse prognosis compared to other IPH cases. A 2-year-old girl with Down syndrome received the diagnosis of IPH after two episodes of massive pulmonary hemorrhage requiring assist ventilation, who suffered from recurrent IPH during tapering period of oral corticosteroid, started liposteroid therapy. We report here a case of successful control of recurrent IPH and improved QOL enormously with tapering dose of corticosteroid after starting liposteroid therapy.http://dx.doi.org/10.1155/2020/5292947 |
| spellingShingle | Hiromi Tobai Jun Yano Norio Sato Fumitaka Amanuma Mikio Takahashi Mikiya Endo Masataka Ishimura Shouichi Ohga Hidekazu Maruyama Successful Liposteroid Therapy for a Recurrent Idiopathic Pulmonary Hemosiderosis with Down Syndrome Case Reports in Pediatrics |
| title | Successful Liposteroid Therapy for a Recurrent Idiopathic Pulmonary Hemosiderosis with Down Syndrome |
| title_full | Successful Liposteroid Therapy for a Recurrent Idiopathic Pulmonary Hemosiderosis with Down Syndrome |
| title_fullStr | Successful Liposteroid Therapy for a Recurrent Idiopathic Pulmonary Hemosiderosis with Down Syndrome |
| title_full_unstemmed | Successful Liposteroid Therapy for a Recurrent Idiopathic Pulmonary Hemosiderosis with Down Syndrome |
| title_short | Successful Liposteroid Therapy for a Recurrent Idiopathic Pulmonary Hemosiderosis with Down Syndrome |
| title_sort | successful liposteroid therapy for a recurrent idiopathic pulmonary hemosiderosis with down syndrome |
| url | http://dx.doi.org/10.1155/2020/5292947 |
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