Clinical diagnosis, treatment and prognosis analysis of children with pancreatic tumours

ObjectiveTo investigate the diagnosis, treatment, and prognosis of children with pancreatic tumours.MethodsWe conducted a retrospective review of patients ≤18 years of age with pancreatic neoplasms who underwent surgery at a single institution between 2010 and 2022.ResultsThe most common histology a...

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Main Authors: Yao Zhang, Chao Yang, Zhenzhen Zhao
Format: Article
Language:English
Published: Frontiers Media S.A. 2025-06-01
Series:Frontiers in Pediatrics
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Online Access:https://www.frontiersin.org/articles/10.3389/fped.2025.1576273/full
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author Yao Zhang
Yao Zhang
Yao Zhang
Yao Zhang
Chao Yang
Chao Yang
Chao Yang
Chao Yang
Zhenzhen Zhao
Zhenzhen Zhao
Zhenzhen Zhao
Zhenzhen Zhao
author_facet Yao Zhang
Yao Zhang
Yao Zhang
Yao Zhang
Chao Yang
Chao Yang
Chao Yang
Chao Yang
Zhenzhen Zhao
Zhenzhen Zhao
Zhenzhen Zhao
Zhenzhen Zhao
author_sort Yao Zhang
collection DOAJ
description ObjectiveTo investigate the diagnosis, treatment, and prognosis of children with pancreatic tumours.MethodsWe conducted a retrospective review of patients ≤18 years of age with pancreatic neoplasms who underwent surgery at a single institution between 2010 and 2022.ResultsThe most common histology among the 48 patients was solid pseudopapillary neoplasm of the pancreas (SPN, n = 32), followed by pancreatic blastoma (PB, n = 12), B-cell lymphoblastic lymphoma (n = 1), leukaemia (n = 1), pancreatic cancer (n = 1), and pancreatic neuroendocrine tumours (n = 1). The tumours were located in the head of the pancreas in 29 patients (10 patients underwent pancreaticoduodenectomy, 9 patients underwent Whipple, 7 patients underwent pancreatic tumour resection, and 3 patients underwent laparoscopic tumour enucleation). The tumours were located in the tail of the pancreatic body in 19 patients (10 patients underwent local resection of the pancreatic tumour, 5 patients underwent resection of the pancreatic body and tail and spleen, 3 patients underwent spleen-preserving distal pancreatectomy, and 1 patient underwent laparoscopic resection of the tumour). Patients with pancreatoblastoma, acute lymphoblastic leukaemia, B lymphoblastic lymphoma or pancreatic cancer were treated with regular chemotherapy. Forty-five patients (93.75%) were currently alive and disease free, and the median follow-up was 8.2 years (IQR: 2.0–14.3). Two patients with pancreatic blastoma died during the follow-up, and 1 patient with pancreatic cancer died due to tumour recurrence and progression after treatment.ConclusionPaediatric pancreatic tumours are highly heterogeneous. Complete surgical resection that preserves organ function is the preferred treatment for children with pancreatic tumours.
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spelling doaj-art-93c64baab0254c6fa2c9eab5ddc5132d2025-08-20T02:33:00ZengFrontiers Media S.A.Frontiers in Pediatrics2296-23602025-06-011310.3389/fped.2025.15762731576273Clinical diagnosis, treatment and prognosis analysis of children with pancreatic tumoursYao Zhang0Yao Zhang1Yao Zhang2Yao Zhang3Chao Yang4Chao Yang5Chao Yang6Chao Yang7Zhenzhen Zhao8Zhenzhen Zhao9Zhenzhen Zhao10Zhenzhen Zhao11Department of Surgical Oncology, Children’s Hospital of Chongqing Medical University, National Clinical Research Center for Child Health and Disorders, Chongqing, ChinaMinistry of Education Key Laboratory of Child Development and Disorders, Chongqing, ChinaInternational Science and Technology Cooperation Base of Child Development and Critical Disorders, Chongqing, ChinaChongqing Municipal Health Commission Key Laboratory of Children’s Vital Organ Development and Diseases, Chongqing, ChinaDepartment of Surgical Oncology, Children’s Hospital of Chongqing Medical University, National Clinical Research Center for Child Health and Disorders, Chongqing, ChinaMinistry of Education Key Laboratory of Child Development and Disorders, Chongqing, ChinaInternational Science and Technology Cooperation Base of Child Development and Critical Disorders, Chongqing, ChinaChongqing Municipal Health Commission Key Laboratory of Children’s Vital Organ Development and Diseases, Chongqing, ChinaDepartment of Surgical Oncology, Children’s Hospital of Chongqing Medical University, National Clinical Research Center for Child Health and Disorders, Chongqing, ChinaMinistry of Education Key Laboratory of Child Development and Disorders, Chongqing, ChinaInternational Science and Technology Cooperation Base of Child Development and Critical Disorders, Chongqing, ChinaChongqing Municipal Health Commission Key Laboratory of Children’s Vital Organ Development and Diseases, Chongqing, ChinaObjectiveTo investigate the diagnosis, treatment, and prognosis of children with pancreatic tumours.MethodsWe conducted a retrospective review of patients ≤18 years of age with pancreatic neoplasms who underwent surgery at a single institution between 2010 and 2022.ResultsThe most common histology among the 48 patients was solid pseudopapillary neoplasm of the pancreas (SPN, n = 32), followed by pancreatic blastoma (PB, n = 12), B-cell lymphoblastic lymphoma (n = 1), leukaemia (n = 1), pancreatic cancer (n = 1), and pancreatic neuroendocrine tumours (n = 1). The tumours were located in the head of the pancreas in 29 patients (10 patients underwent pancreaticoduodenectomy, 9 patients underwent Whipple, 7 patients underwent pancreatic tumour resection, and 3 patients underwent laparoscopic tumour enucleation). The tumours were located in the tail of the pancreatic body in 19 patients (10 patients underwent local resection of the pancreatic tumour, 5 patients underwent resection of the pancreatic body and tail and spleen, 3 patients underwent spleen-preserving distal pancreatectomy, and 1 patient underwent laparoscopic resection of the tumour). Patients with pancreatoblastoma, acute lymphoblastic leukaemia, B lymphoblastic lymphoma or pancreatic cancer were treated with regular chemotherapy. Forty-five patients (93.75%) were currently alive and disease free, and the median follow-up was 8.2 years (IQR: 2.0–14.3). Two patients with pancreatic blastoma died during the follow-up, and 1 patient with pancreatic cancer died due to tumour recurrence and progression after treatment.ConclusionPaediatric pancreatic tumours are highly heterogeneous. Complete surgical resection that preserves organ function is the preferred treatment for children with pancreatic tumours.https://www.frontiersin.org/articles/10.3389/fped.2025.1576273/fullpancreatic tumourchildrentreatmentprognosisdiagnosis
spellingShingle Yao Zhang
Yao Zhang
Yao Zhang
Yao Zhang
Chao Yang
Chao Yang
Chao Yang
Chao Yang
Zhenzhen Zhao
Zhenzhen Zhao
Zhenzhen Zhao
Zhenzhen Zhao
Clinical diagnosis, treatment and prognosis analysis of children with pancreatic tumours
Frontiers in Pediatrics
pancreatic tumour
children
treatment
prognosis
diagnosis
title Clinical diagnosis, treatment and prognosis analysis of children with pancreatic tumours
title_full Clinical diagnosis, treatment and prognosis analysis of children with pancreatic tumours
title_fullStr Clinical diagnosis, treatment and prognosis analysis of children with pancreatic tumours
title_full_unstemmed Clinical diagnosis, treatment and prognosis analysis of children with pancreatic tumours
title_short Clinical diagnosis, treatment and prognosis analysis of children with pancreatic tumours
title_sort clinical diagnosis treatment and prognosis analysis of children with pancreatic tumours
topic pancreatic tumour
children
treatment
prognosis
diagnosis
url https://www.frontiersin.org/articles/10.3389/fped.2025.1576273/full
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