A Case Report of Duodenal Gangliocytic Paraganglioma – Is Duodenopancreatectomy Necessary?

Gangliocytic paraganglioma (GP) is an uncommon finding in the periampullary region of the duodenum. In the Department of General and Digestive Surgery of the Albacete University Hospital Complex, a 45-years-old patient was diagnosed with a 17x13mm hypervascular nodular lesion in the descending part...

Full description

Saved in:
Bibliographic Details
Main Authors: Antonio Valero-Liñán, José Ignacio Miota De Llama, José Gonzalez-Masiá, Toni Stoyanov, Belén Conde-Inarejos, Olga Luengo-Ballester
Format: Article
Language:English
Published: Medical University - Pleven 2019-08-01
Series:Journal of Biomedical & Clinical Research
Subjects:
Online Access:https://jbcr.arphahub.com/article/34537/download/pdf/
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1849252220818685952
author Antonio Valero-Liñán
José Ignacio Miota De Llama
José Gonzalez-Masiá
Toni Stoyanov
Belén Conde-Inarejos
Olga Luengo-Ballester
author_facet Antonio Valero-Liñán
José Ignacio Miota De Llama
José Gonzalez-Masiá
Toni Stoyanov
Belén Conde-Inarejos
Olga Luengo-Ballester
author_sort Antonio Valero-Liñán
collection DOAJ
description Gangliocytic paraganglioma (GP) is an uncommon finding in the periampullary region of the duodenum. In the Department of General and Digestive Surgery of the Albacete University Hospital Complex, a 45-years-old patient was diagnosed with a 17x13mm hypervascular nodular lesion in the descending part of the duodenum during an examination for hepatic hemangiomas. Ampullectomy was performed, followed by a favourable postoperative period. Histological analysis proved GP. There were no involvement of lymph nodes and a malignancy potential, so the clinical and radiological follow-up opted. In conclusion, because such tumours have unpredictable behavior, we recommend local resection of the tumour, except in cases in which local or ganglionic progression is suspected or confirmed, and thus cephalic pancreaticoduodenectomy (CPD) and lymphadenectomy are suggested.
format Article
id doaj-art-8f856bb845194039b1bdcb57167413cf
institution Kabale University
issn 1313-9053
language English
publishDate 2019-08-01
publisher Medical University - Pleven
record_format Article
series Journal of Biomedical & Clinical Research
spelling doaj-art-8f856bb845194039b1bdcb57167413cf2025-08-20T03:56:41ZengMedical University - PlevenJournal of Biomedical & Clinical Research1313-90532019-08-01121727510.2478/jbcr-2019-001234537A Case Report of Duodenal Gangliocytic Paraganglioma – Is Duodenopancreatectomy Necessary?Antonio Valero-LiñánJosé Ignacio Miota De LlamaJosé Gonzalez-MasiáToni StoyanovBelén Conde-InarejosOlga Luengo-BallesterGangliocytic paraganglioma (GP) is an uncommon finding in the periampullary region of the duodenum. In the Department of General and Digestive Surgery of the Albacete University Hospital Complex, a 45-years-old patient was diagnosed with a 17x13mm hypervascular nodular lesion in the descending part of the duodenum during an examination for hepatic hemangiomas. Ampullectomy was performed, followed by a favourable postoperative period. Histological analysis proved GP. There were no involvement of lymph nodes and a malignancy potential, so the clinical and radiological follow-up opted. In conclusion, because such tumours have unpredictable behavior, we recommend local resection of the tumour, except in cases in which local or ganglionic progression is suspected or confirmed, and thus cephalic pancreaticoduodenectomy (CPD) and lymphadenectomy are suggested.https://jbcr.arphahub.com/article/34537/download/pdf/gangliocytic paragangliomaduodenumperiampullar
spellingShingle Antonio Valero-Liñán
José Ignacio Miota De Llama
José Gonzalez-Masiá
Toni Stoyanov
Belén Conde-Inarejos
Olga Luengo-Ballester
A Case Report of Duodenal Gangliocytic Paraganglioma – Is Duodenopancreatectomy Necessary?
Journal of Biomedical & Clinical Research
gangliocytic paraganglioma
duodenum
periampullar
title A Case Report of Duodenal Gangliocytic Paraganglioma – Is Duodenopancreatectomy Necessary?
title_full A Case Report of Duodenal Gangliocytic Paraganglioma – Is Duodenopancreatectomy Necessary?
title_fullStr A Case Report of Duodenal Gangliocytic Paraganglioma – Is Duodenopancreatectomy Necessary?
title_full_unstemmed A Case Report of Duodenal Gangliocytic Paraganglioma – Is Duodenopancreatectomy Necessary?
title_short A Case Report of Duodenal Gangliocytic Paraganglioma – Is Duodenopancreatectomy Necessary?
title_sort case report of duodenal gangliocytic paraganglioma is duodenopancreatectomy necessary
topic gangliocytic paraganglioma
duodenum
periampullar
url https://jbcr.arphahub.com/article/34537/download/pdf/
work_keys_str_mv AT antoniovalerolinan acasereportofduodenalgangliocyticparagangliomaisduodenopancreatectomynecessary
AT joseignaciomiotadellama acasereportofduodenalgangliocyticparagangliomaisduodenopancreatectomynecessary
AT josegonzalezmasia acasereportofduodenalgangliocyticparagangliomaisduodenopancreatectomynecessary
AT tonistoyanov acasereportofduodenalgangliocyticparagangliomaisduodenopancreatectomynecessary
AT belencondeinarejos acasereportofduodenalgangliocyticparagangliomaisduodenopancreatectomynecessary
AT olgaluengoballester acasereportofduodenalgangliocyticparagangliomaisduodenopancreatectomynecessary
AT antoniovalerolinan casereportofduodenalgangliocyticparagangliomaisduodenopancreatectomynecessary
AT joseignaciomiotadellama casereportofduodenalgangliocyticparagangliomaisduodenopancreatectomynecessary
AT josegonzalezmasia casereportofduodenalgangliocyticparagangliomaisduodenopancreatectomynecessary
AT tonistoyanov casereportofduodenalgangliocyticparagangliomaisduodenopancreatectomynecessary
AT belencondeinarejos casereportofduodenalgangliocyticparagangliomaisduodenopancreatectomynecessary
AT olgaluengoballester casereportofduodenalgangliocyticparagangliomaisduodenopancreatectomynecessary