Herlyn-Werner-Wunderlich syndrome with double hematocolpos in one side hemivagina

Background: Herlyn-Werner-Wunderlich syndrome (HWWS) is an extremely rare Mullerian anomaly consisting of uterus didelphys with obstructed hemivagina and ipsilateral renal agenesis. Although few HWWS cases had been reported in the gynecological literature, most of the reported cases were combined wi...

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Main Authors: You Jin Kim, Jung Bo Yang, Ye Won Jung, Soo Youn Song, Geon Woo Lee, Heon Jong Yoo
Format: Article
Language:English
Published: IMR Press 2022-06-01
Series:Clinical and Experimental Obstetrics & Gynecology
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Online Access:https://www.imrpress.com/journal/CEOG/49/6/10.31083/j.ceog4906141
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author You Jin Kim
Jung Bo Yang
Ye Won Jung
Soo Youn Song
Geon Woo Lee
Heon Jong Yoo
author_facet You Jin Kim
Jung Bo Yang
Ye Won Jung
Soo Youn Song
Geon Woo Lee
Heon Jong Yoo
author_sort You Jin Kim
collection DOAJ
description Background: Herlyn-Werner-Wunderlich syndrome (HWWS) is an extremely rare Mullerian anomaly consisting of uterus didelphys with obstructed hemivagina and ipsilateral renal agenesis. Although few HWWS cases had been reported in the gynecological literature, most of the reported cases were combined with single hematocolpos. Case: We report here on a case of HWWS with double hematocolpos on one side of a hemivagina combined with ipsilateral renal agenesis. This is the first report of HWWS with double hematocolpos on one side of a hemivagina that was successfully treated with the resection of the vaginal septum. Conclusion: It is important to understand the pathogenesis and clinical features of these anomalies for diagnosis.
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series Clinical and Experimental Obstetrics & Gynecology
spelling doaj-art-8efa75829b534a26bfa2f9b79df814df2025-08-20T02:09:21ZengIMR PressClinical and Experimental Obstetrics & Gynecology0390-66632022-06-0149614110.31083/j.ceog4906141S0390-6663(22)01815-2Herlyn-Werner-Wunderlich syndrome with double hematocolpos in one side hemivaginaYou Jin Kim0Jung Bo Yang1Ye Won Jung2Soo Youn Song3Geon Woo Lee4Heon Jong Yoo5Department of Obstetrics & Gynecology, Chungnam National University Hospital, Chungnam National University School of medicine, 282, Munhwa-ro, 301-721 Jung-gu, Deajeon, Republic of KoreaDepartment of Obstetrics & Gynecology, Chungnam National University Hospital, Chungnam National University School of medicine, 282, Munhwa-ro, 301-721 Jung-gu, Deajeon, Republic of KoreaDepartment of Obstetrics & Gynecology, Chungnam National University Hospital, Chungnam National University School of medicine, 282, Munhwa-ro, 301-721 Jung-gu, Deajeon, Republic of KoreaDepartment of Obstetrics & Gynecology, Chungnam National University Hospital, Chungnam National University School of medicine, 282, Munhwa-ro, 301-721 Jung-gu, Deajeon, Republic of KoreaDepartment of Obstetrics & Gynecology, Chungnam National University Hospital, Chungnam National University School of medicine, 282, Munhwa-ro, 301-721 Jung-gu, Deajeon, Republic of KoreaDepartment of Obstetrics & Gynecology, Chungnam National University Hospital, Chungnam National University School of medicine, 282, Munhwa-ro, 301-721 Jung-gu, Deajeon, Republic of KoreaBackground: Herlyn-Werner-Wunderlich syndrome (HWWS) is an extremely rare Mullerian anomaly consisting of uterus didelphys with obstructed hemivagina and ipsilateral renal agenesis. Although few HWWS cases had been reported in the gynecological literature, most of the reported cases were combined with single hematocolpos. Case: We report here on a case of HWWS with double hematocolpos on one side of a hemivagina combined with ipsilateral renal agenesis. This is the first report of HWWS with double hematocolpos on one side of a hemivagina that was successfully treated with the resection of the vaginal septum. Conclusion: It is important to understand the pathogenesis and clinical features of these anomalies for diagnosis.https://www.imrpress.com/journal/CEOG/49/6/10.31083/j.ceog4906141hematocolposhereditary renal agenesisurogenital abnormalitiesherlyn-werner-wunderlich syndromemullerian anomaly
spellingShingle You Jin Kim
Jung Bo Yang
Ye Won Jung
Soo Youn Song
Geon Woo Lee
Heon Jong Yoo
Herlyn-Werner-Wunderlich syndrome with double hematocolpos in one side hemivagina
Clinical and Experimental Obstetrics & Gynecology
hematocolpos
hereditary renal agenesis
urogenital abnormalities
herlyn-werner-wunderlich syndrome
mullerian anomaly
title Herlyn-Werner-Wunderlich syndrome with double hematocolpos in one side hemivagina
title_full Herlyn-Werner-Wunderlich syndrome with double hematocolpos in one side hemivagina
title_fullStr Herlyn-Werner-Wunderlich syndrome with double hematocolpos in one side hemivagina
title_full_unstemmed Herlyn-Werner-Wunderlich syndrome with double hematocolpos in one side hemivagina
title_short Herlyn-Werner-Wunderlich syndrome with double hematocolpos in one side hemivagina
title_sort herlyn werner wunderlich syndrome with double hematocolpos in one side hemivagina
topic hematocolpos
hereditary renal agenesis
urogenital abnormalities
herlyn-werner-wunderlich syndrome
mullerian anomaly
url https://www.imrpress.com/journal/CEOG/49/6/10.31083/j.ceog4906141
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