Multifocal Intestinal Extranodal Marginal Zone Lymphoma Presenting With Autoimmune Hemolytic Anemia: A Case Report

Extranodal marginal zone lymphoma of the intestine is a rare, indolent non-Hodgkin lymphoma that often presents with nonspecific symptoms, making diagnosis challenging. We report a 74-year-old woman who presented with severe anemia attributable to autoimmune hemolytic anemia. Imaging revealed spleno...

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Main Authors: Ali Emre Bardak, Naci Senkal, Kanan Nuriyev, Alpay Medetalibeyoglu
Format: Article
Language:English
Published: American College of Physicians 2025-03-01
Series:Annals of Internal Medicine: Clinical Cases
Online Access:https://www.acpjournals.org/doi/10.7326/aimcc.2024.1222
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author Ali Emre Bardak
Naci Senkal
Kanan Nuriyev
Alpay Medetalibeyoglu
author_facet Ali Emre Bardak
Naci Senkal
Kanan Nuriyev
Alpay Medetalibeyoglu
author_sort Ali Emre Bardak
collection DOAJ
description Extranodal marginal zone lymphoma of the intestine is a rare, indolent non-Hodgkin lymphoma that often presents with nonspecific symptoms, making diagnosis challenging. We report a 74-year-old woman who presented with severe anemia attributable to autoimmune hemolytic anemia. Imaging revealed splenomegaly and intestinal wall thickening, whereas subsequent endoscopy showed ulcerated lesions in the ileocecal valve, transverse colon, and descending colon. Biopsy results confirmed extranodal marginal zone lymphoma. Treatment with the R-CHOP (rituximab, cyclophosphamide, doxorubicin, vincristine, and prednisone) regimen led to partial remission of the lymphoma and complete resolution of autoimmune hemolytic anemia.
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series Annals of Internal Medicine: Clinical Cases
spelling doaj-art-8d1ea64f4b4749fdb8f7eb514c3e7a5a2025-08-20T03:18:45ZengAmerican College of PhysiciansAnnals of Internal Medicine: Clinical Cases2767-76642025-03-014310.7326/aimcc.2024.1222Multifocal Intestinal Extranodal Marginal Zone Lymphoma Presenting With Autoimmune Hemolytic Anemia: A Case ReportAli Emre Bardak0Naci Senkal1Kanan Nuriyev2Alpay Medetalibeyoglu31Department of Internal Medicine, St. Elizabeth's Medical Center, Boston, Massachusetts2Department of Internal Medicine, Istanbul University, Istanbul Faculty of Medicine, Istanbul, Turkey3Department of Gastroenterology, Istanbul University, Istanbul Faculty of Medicine, Istanbul, Turkey2Department of Internal Medicine, Istanbul University, Istanbul Faculty of Medicine, Istanbul, TurkeyExtranodal marginal zone lymphoma of the intestine is a rare, indolent non-Hodgkin lymphoma that often presents with nonspecific symptoms, making diagnosis challenging. We report a 74-year-old woman who presented with severe anemia attributable to autoimmune hemolytic anemia. Imaging revealed splenomegaly and intestinal wall thickening, whereas subsequent endoscopy showed ulcerated lesions in the ileocecal valve, transverse colon, and descending colon. Biopsy results confirmed extranodal marginal zone lymphoma. Treatment with the R-CHOP (rituximab, cyclophosphamide, doxorubicin, vincristine, and prednisone) regimen led to partial remission of the lymphoma and complete resolution of autoimmune hemolytic anemia.https://www.acpjournals.org/doi/10.7326/aimcc.2024.1222
spellingShingle Ali Emre Bardak
Naci Senkal
Kanan Nuriyev
Alpay Medetalibeyoglu
Multifocal Intestinal Extranodal Marginal Zone Lymphoma Presenting With Autoimmune Hemolytic Anemia: A Case Report
Annals of Internal Medicine: Clinical Cases
title Multifocal Intestinal Extranodal Marginal Zone Lymphoma Presenting With Autoimmune Hemolytic Anemia: A Case Report
title_full Multifocal Intestinal Extranodal Marginal Zone Lymphoma Presenting With Autoimmune Hemolytic Anemia: A Case Report
title_fullStr Multifocal Intestinal Extranodal Marginal Zone Lymphoma Presenting With Autoimmune Hemolytic Anemia: A Case Report
title_full_unstemmed Multifocal Intestinal Extranodal Marginal Zone Lymphoma Presenting With Autoimmune Hemolytic Anemia: A Case Report
title_short Multifocal Intestinal Extranodal Marginal Zone Lymphoma Presenting With Autoimmune Hemolytic Anemia: A Case Report
title_sort multifocal intestinal extranodal marginal zone lymphoma presenting with autoimmune hemolytic anemia a case report
url https://www.acpjournals.org/doi/10.7326/aimcc.2024.1222
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