Left Ventricular Ring-like Pattern: The Arrhythmic Tale of a Scarred Heart

Cardiac magnetic resonance (CMR) imaging provides significant advantages in the non-invasive diagnosis of cardiac diseases. An emerging phenotype is increasingly being described in CMR reports, the LGE “ring-like” pattern, which resembles a circumferential/semi-circumferential LV scar. Different con...

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Main Authors: Vanda Parisi, Claudio Bergami, Ferdinando Pasquale, Maria Alessandra Schiavo, Irene Ruotolo, Naomi Fanciullo, Nicolò Sini, Matteo Ziacchi, Mauro Biffi, Raffaello Ditaranto, Maddalena Graziosi, Elena Biagini
Format: Article
Language:English
Published: MDPI AG 2025-07-01
Series:Journal of Cardiovascular Development and Disease
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Online Access:https://www.mdpi.com/2308-3425/12/7/275
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author Vanda Parisi
Claudio Bergami
Ferdinando Pasquale
Maria Alessandra Schiavo
Irene Ruotolo
Naomi Fanciullo
Nicolò Sini
Matteo Ziacchi
Mauro Biffi
Raffaello Ditaranto
Maddalena Graziosi
Elena Biagini
author_facet Vanda Parisi
Claudio Bergami
Ferdinando Pasquale
Maria Alessandra Schiavo
Irene Ruotolo
Naomi Fanciullo
Nicolò Sini
Matteo Ziacchi
Mauro Biffi
Raffaello Ditaranto
Maddalena Graziosi
Elena Biagini
author_sort Vanda Parisi
collection DOAJ
description Cardiac magnetic resonance (CMR) imaging provides significant advantages in the non-invasive diagnosis of cardiac diseases. An emerging phenotype is increasingly being described in CMR reports, the LGE “ring-like” pattern, which resembles a circumferential/semi-circumferential LV scar. Different conditions exhibit this fibrosis distribution, the majority of them being genetically determined and mostly involving cardiomyopathy-causative genes (desmosomal but also other non-desmosomal related genes). Furthermore, inflammatory diseases, such as myocarditis or sarcoidosis, could be responsible for LV fibrosis, potentially exhibiting an RL distribution. Given the heterogeneity of such conditions, effective patient management requires a stepwise and multiparametric diagnostic work-up that integrates clinical, instrumental, and genetic data to identify the specific aetiology and guide personalised treatments.
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publishDate 2025-07-01
publisher MDPI AG
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series Journal of Cardiovascular Development and Disease
spelling doaj-art-8a97b4e14f814c91ab85a29dd2a2f6e02025-08-20T02:45:49ZengMDPI AGJournal of Cardiovascular Development and Disease2308-34252025-07-0112727510.3390/jcdd12070275Left Ventricular Ring-like Pattern: The Arrhythmic Tale of a Scarred HeartVanda Parisi0Claudio Bergami1Ferdinando Pasquale2Maria Alessandra Schiavo3Irene Ruotolo4Naomi Fanciullo5Nicolò Sini6Matteo Ziacchi7Mauro Biffi8Raffaello Ditaranto9Maddalena Graziosi10Elena Biagini11Cardiology Unit, Cardiac Thoracic and Vascular Department, IRCCS Azienda Ospedaliero-Universitaria di Bologna, Via Giuseppe Massarenti 9, 40138 Bologna, ItalyCardiology Unit, Cardiac Thoracic and Vascular Department, IRCCS Azienda Ospedaliero-Universitaria di Bologna, Via Giuseppe Massarenti 9, 40138 Bologna, ItalyCardiology Unit, Cardiac Thoracic and Vascular Department, IRCCS Azienda Ospedaliero-Universitaria di Bologna, Via Giuseppe Massarenti 9, 40138 Bologna, ItalyCardiology Unit, Cardiac Thoracic and Vascular Department, IRCCS Azienda Ospedaliero-Universitaria di Bologna, Via Giuseppe Massarenti 9, 40138 Bologna, ItalyCardiology Unit, Cardiac Thoracic and Vascular Department, IRCCS Azienda Ospedaliero-Universitaria di Bologna, Via Giuseppe Massarenti 9, 40138 Bologna, ItalyCardiology Unit, Cardiac Thoracic and Vascular Department, IRCCS Azienda Ospedaliero-Universitaria di Bologna, Via Giuseppe Massarenti 9, 40138 Bologna, ItalyCardiology Unit, Cardiac Thoracic and Vascular Department, IRCCS Azienda Ospedaliero-Universitaria di Bologna, Via Giuseppe Massarenti 9, 40138 Bologna, ItalyCardiology Unit, Cardiac Thoracic and Vascular Department, IRCCS Azienda Ospedaliero-Universitaria di Bologna, Via Giuseppe Massarenti 9, 40138 Bologna, ItalyCardiology Unit, Cardiac Thoracic and Vascular Department, IRCCS Azienda Ospedaliero-Universitaria di Bologna, Via Giuseppe Massarenti 9, 40138 Bologna, ItalyCardiology Unit, Cardiac Thoracic and Vascular Department, IRCCS Azienda Ospedaliero-Universitaria di Bologna, Via Giuseppe Massarenti 9, 40138 Bologna, ItalyCardiology Unit, Cardiac Thoracic and Vascular Department, IRCCS Azienda Ospedaliero-Universitaria di Bologna, Via Giuseppe Massarenti 9, 40138 Bologna, ItalyCardiology Unit, Cardiac Thoracic and Vascular Department, IRCCS Azienda Ospedaliero-Universitaria di Bologna, Via Giuseppe Massarenti 9, 40138 Bologna, ItalyCardiac magnetic resonance (CMR) imaging provides significant advantages in the non-invasive diagnosis of cardiac diseases. An emerging phenotype is increasingly being described in CMR reports, the LGE “ring-like” pattern, which resembles a circumferential/semi-circumferential LV scar. Different conditions exhibit this fibrosis distribution, the majority of them being genetically determined and mostly involving cardiomyopathy-causative genes (desmosomal but also other non-desmosomal related genes). Furthermore, inflammatory diseases, such as myocarditis or sarcoidosis, could be responsible for LV fibrosis, potentially exhibiting an RL distribution. Given the heterogeneity of such conditions, effective patient management requires a stepwise and multiparametric diagnostic work-up that integrates clinical, instrumental, and genetic data to identify the specific aetiology and guide personalised treatments.https://www.mdpi.com/2308-3425/12/7/275cardiac magnetic resonanceCMRLGEscarphenotypering-like
spellingShingle Vanda Parisi
Claudio Bergami
Ferdinando Pasquale
Maria Alessandra Schiavo
Irene Ruotolo
Naomi Fanciullo
Nicolò Sini
Matteo Ziacchi
Mauro Biffi
Raffaello Ditaranto
Maddalena Graziosi
Elena Biagini
Left Ventricular Ring-like Pattern: The Arrhythmic Tale of a Scarred Heart
Journal of Cardiovascular Development and Disease
cardiac magnetic resonance
CMR
LGE
scar
phenotype
ring-like
title Left Ventricular Ring-like Pattern: The Arrhythmic Tale of a Scarred Heart
title_full Left Ventricular Ring-like Pattern: The Arrhythmic Tale of a Scarred Heart
title_fullStr Left Ventricular Ring-like Pattern: The Arrhythmic Tale of a Scarred Heart
title_full_unstemmed Left Ventricular Ring-like Pattern: The Arrhythmic Tale of a Scarred Heart
title_short Left Ventricular Ring-like Pattern: The Arrhythmic Tale of a Scarred Heart
title_sort left ventricular ring like pattern the arrhythmic tale of a scarred heart
topic cardiac magnetic resonance
CMR
LGE
scar
phenotype
ring-like
url https://www.mdpi.com/2308-3425/12/7/275
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