Hybrid Benign Peripheral Nerve Sheath Tumors: A Comprehensive Literature Review with Emphasis on Their Clinical, Morphological and Genetic Features

Hybrid Peripheral Nerve Sheath Tumors (HPNSTs) are rare benign neoplasms that exhibit a combination of histological features from multiple types of benign peripheral nerve sheath tumors, including schwannomas, neurofibromas, and perineuriomas. These tumors present a diagnostic challenge due to their...

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Main Authors: Serena Salzano, Rosario Caltabiano, Magda Zanelli, Andrea Palicelli, Maurizio Zizzo, Nektarios Koufopoulos, Ioannis Boutas, Gaetano Magro, Valeria Barresi, Giuseppe Broggi
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Language:English
Published: MDPI AG 2025-03-01
Series:Diagnostics
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Online Access:https://www.mdpi.com/2075-4418/15/7/855
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author Serena Salzano
Rosario Caltabiano
Magda Zanelli
Andrea Palicelli
Maurizio Zizzo
Nektarios Koufopoulos
Ioannis Boutas
Gaetano Magro
Valeria Barresi
Giuseppe Broggi
author_facet Serena Salzano
Rosario Caltabiano
Magda Zanelli
Andrea Palicelli
Maurizio Zizzo
Nektarios Koufopoulos
Ioannis Boutas
Gaetano Magro
Valeria Barresi
Giuseppe Broggi
author_sort Serena Salzano
collection DOAJ
description Hybrid Peripheral Nerve Sheath Tumors (HPNSTs) are rare benign neoplasms that exhibit a combination of histological features from multiple types of benign peripheral nerve sheath tumors, including schwannomas, neurofibromas, and perineuriomas. These tumors present a diagnostic challenge due to their morphological and histological variability. In this article, we aim to summarize the key morphological, histological, and molecular characteristics of HPNSTs, providing insights into their diagnostic approaches. We review the different hybrid subtypes, including schwannoma–perineurioma, schwannoma–neurofibroma, and perineurioma–neurofibroma, emphasizing their clinical features, genetic associations, and the role of surgical excision as the gold-standard treatment.
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spelling doaj-art-8a05b9ab67b14addb18700d2eb4fbedd2025-08-20T02:15:55ZengMDPI AGDiagnostics2075-44182025-03-0115785510.3390/diagnostics15070855Hybrid Benign Peripheral Nerve Sheath Tumors: A Comprehensive Literature Review with Emphasis on Their Clinical, Morphological and Genetic FeaturesSerena Salzano0Rosario Caltabiano1Magda Zanelli2Andrea Palicelli3Maurizio Zizzo4Nektarios Koufopoulos5Ioannis Boutas6Gaetano Magro7Valeria Barresi8Giuseppe Broggi9Department of Medical and Surgical Sciences and Advanced Technologies “G.F. Ingrassia”, Anatomic Pathology, University of Catania, 95123 Catania, ItalyDepartment of Medical and Surgical Sciences and Advanced Technologies “G.F. Ingrassia”, Anatomic Pathology, University of Catania, 95123 Catania, ItalyPathology Unit, Azienda USL-IRCCS di Reggio Emilia, 42123 Reggio Emilia, ItalyPathology Unit, Azienda USL-IRCCS di Reggio Emilia, 42123 Reggio Emilia, ItalySurgical Oncology Unit, Azienda USL-IRCCS di Reggio Emilia, 42123 Reggio Emilia, ItalySecond Department of Pathology, Medical School, Attikon University Hospital, National and Kapodistrian University of Athens, 15772 Athens, GreeceSecond Department of Pathology, Medical School, Attikon University Hospital, National and Kapodistrian University of Athens, 15772 Athens, GreeceDepartment of Medical and Surgical Sciences and Advanced Technologies “G.F. Ingrassia”, Anatomic Pathology, University of Catania, 95123 Catania, ItalyDepartment of Diagnostics and Public Health, University of Verona, 37134 Verona, ItalyDepartment of Medical and Surgical Sciences and Advanced Technologies “G.F. Ingrassia”, Anatomic Pathology, University of Catania, 95123 Catania, ItalyHybrid Peripheral Nerve Sheath Tumors (HPNSTs) are rare benign neoplasms that exhibit a combination of histological features from multiple types of benign peripheral nerve sheath tumors, including schwannomas, neurofibromas, and perineuriomas. These tumors present a diagnostic challenge due to their morphological and histological variability. In this article, we aim to summarize the key morphological, histological, and molecular characteristics of HPNSTs, providing insights into their diagnostic approaches. We review the different hybrid subtypes, including schwannoma–perineurioma, schwannoma–neurofibroma, and perineurioma–neurofibroma, emphasizing their clinical features, genetic associations, and the role of surgical excision as the gold-standard treatment.https://www.mdpi.com/2075-4418/15/7/855hybrid benign peripheral nerve sheath tumorsCNSschwannomaneurofibromaperineurioma
spellingShingle Serena Salzano
Rosario Caltabiano
Magda Zanelli
Andrea Palicelli
Maurizio Zizzo
Nektarios Koufopoulos
Ioannis Boutas
Gaetano Magro
Valeria Barresi
Giuseppe Broggi
Hybrid Benign Peripheral Nerve Sheath Tumors: A Comprehensive Literature Review with Emphasis on Their Clinical, Morphological and Genetic Features
Diagnostics
hybrid benign peripheral nerve sheath tumors
CNS
schwannoma
neurofibroma
perineurioma
title Hybrid Benign Peripheral Nerve Sheath Tumors: A Comprehensive Literature Review with Emphasis on Their Clinical, Morphological and Genetic Features
title_full Hybrid Benign Peripheral Nerve Sheath Tumors: A Comprehensive Literature Review with Emphasis on Their Clinical, Morphological and Genetic Features
title_fullStr Hybrid Benign Peripheral Nerve Sheath Tumors: A Comprehensive Literature Review with Emphasis on Their Clinical, Morphological and Genetic Features
title_full_unstemmed Hybrid Benign Peripheral Nerve Sheath Tumors: A Comprehensive Literature Review with Emphasis on Their Clinical, Morphological and Genetic Features
title_short Hybrid Benign Peripheral Nerve Sheath Tumors: A Comprehensive Literature Review with Emphasis on Their Clinical, Morphological and Genetic Features
title_sort hybrid benign peripheral nerve sheath tumors a comprehensive literature review with emphasis on their clinical morphological and genetic features
topic hybrid benign peripheral nerve sheath tumors
CNS
schwannoma
neurofibroma
perineurioma
url https://www.mdpi.com/2075-4418/15/7/855
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