Type II Congenital Pulmonary Airway Malformation in an Esophageal Lung

A seven-month-old girl, born prematurely (birth weight 1000 g) from a twin pregnancy, was admitted to hospital due to recurrent pneumonia and atelectasis. She experienced cough and respiratory distress during feeding. The right hemithorax was smaller than the left, with diminished breath sounds and...

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Main Authors: Blanca Estela Martínez-Martínez, María Elena Yuriko Furuya, Irma Martínez-Muñiz, Mario H Vargas, Rosalinda Flores-Salgado
Format: Article
Language:English
Published: Wiley 2013-01-01
Series:Canadian Respiratory Journal
Online Access:http://dx.doi.org/10.1155/2013/581359
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author Blanca Estela Martínez-Martínez
María Elena Yuriko Furuya
Irma Martínez-Muñiz
Mario H Vargas
Rosalinda Flores-Salgado
author_facet Blanca Estela Martínez-Martínez
María Elena Yuriko Furuya
Irma Martínez-Muñiz
Mario H Vargas
Rosalinda Flores-Salgado
author_sort Blanca Estela Martínez-Martínez
collection DOAJ
description A seven-month-old girl, born prematurely (birth weight 1000 g) from a twin pregnancy, was admitted to hospital due to recurrent pneumonia and atelectasis. She experienced cough and respiratory distress during feeding. The right hemithorax was smaller than the left, with diminished breath sounds and dullness. Chest x-rays revealed decreased lung volume and multiple radiolucent images in the right lung, as well as overdistention of the left lung. An esophagogram revealed three bronchial branches arising from the lower one-third of the esophagus, corresponding to the right lung and ending in a cul-de-sac. A diagnosis of esophageal lung was established. On bronchography, the right lung was absent and the trachea only continued into the left main bronchus. Echocardiography and angiotomography revealed agenesis of the pulmonary artery right branch. The surgical finding was an esophageal right lung, which was removed; the histopathological diagnosis was type II congenital pulmonary airway malformation in an esophageal lung.
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record_format Article
series Canadian Respiratory Journal
spelling doaj-art-896ff38d744a4fa6b633b96c5fccfdec2025-02-03T05:45:46ZengWileyCanadian Respiratory Journal1198-22412013-01-01203e52e5410.1155/2013/581359Type II Congenital Pulmonary Airway Malformation in an Esophageal LungBlanca Estela Martínez-Martínez0María Elena Yuriko Furuya1Irma Martínez-Muñiz2Mario H Vargas3Rosalinda Flores-Salgado4Departamento de Neumología, Hospital de Pediatría, Centro Médico Nacional Siglo XXI, Instituto Mexicano del Seguro Social, México DF, MexicoUnidad de Investigación Médica en Enfermedades Respiratorias, Hospital de Pediatría, Centro Médico Nacional Siglo XXI, Instituto Mexicano del Seguro Social, México DF, MexicoDepartamento de Imagenología, Hospital de Pediatría, Centro Médico Nacional Siglo XXI, Instituto Mexicano del Seguro Social, México DF, MexicoUnidad de Investigación Médica en Enfermedades Respiratorias, Hospital de Pediatría, Centro Médico Nacional Siglo XXI, Instituto Mexicano del Seguro Social, México DF, MexicoDepartamento de Anatomía Patológica, Hospital de Pediatría, Centro Médico Nacional Siglo XXI, Instituto Mexicano del Seguro Social, México DF, MexicoA seven-month-old girl, born prematurely (birth weight 1000 g) from a twin pregnancy, was admitted to hospital due to recurrent pneumonia and atelectasis. She experienced cough and respiratory distress during feeding. The right hemithorax was smaller than the left, with diminished breath sounds and dullness. Chest x-rays revealed decreased lung volume and multiple radiolucent images in the right lung, as well as overdistention of the left lung. An esophagogram revealed three bronchial branches arising from the lower one-third of the esophagus, corresponding to the right lung and ending in a cul-de-sac. A diagnosis of esophageal lung was established. On bronchography, the right lung was absent and the trachea only continued into the left main bronchus. Echocardiography and angiotomography revealed agenesis of the pulmonary artery right branch. The surgical finding was an esophageal right lung, which was removed; the histopathological diagnosis was type II congenital pulmonary airway malformation in an esophageal lung.http://dx.doi.org/10.1155/2013/581359
spellingShingle Blanca Estela Martínez-Martínez
María Elena Yuriko Furuya
Irma Martínez-Muñiz
Mario H Vargas
Rosalinda Flores-Salgado
Type II Congenital Pulmonary Airway Malformation in an Esophageal Lung
Canadian Respiratory Journal
title Type II Congenital Pulmonary Airway Malformation in an Esophageal Lung
title_full Type II Congenital Pulmonary Airway Malformation in an Esophageal Lung
title_fullStr Type II Congenital Pulmonary Airway Malformation in an Esophageal Lung
title_full_unstemmed Type II Congenital Pulmonary Airway Malformation in an Esophageal Lung
title_short Type II Congenital Pulmonary Airway Malformation in an Esophageal Lung
title_sort type ii congenital pulmonary airway malformation in an esophageal lung
url http://dx.doi.org/10.1155/2013/581359
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