Tetralogy of Fallot, Absent Vena Cava Superior, Persistent Left Vena Cava Superior, and Interrupted Vena Cava Inferior: A Case of Struggle in Open Heart Surgery
Interruption of vena cava inferior (VCI) is extremely rare, in occurrence in isolation or association with asplenia or polysplenia syndromes. In this abnormality, the infrahepatic segment of the VCI is absent, by representing the inadequacy of fusion of subcardinal embryological parts of the VCI. It...
Saved in:
| Main Authors: | , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Duzce University
2025-04-01
|
| Series: | Düzce Tıp Fakültesi Dergisi |
| Subjects: | |
| Online Access: | https://dergipark.org.tr/en/download/article-file/4346088 |
| Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
| _version_ | 1850178519885152256 |
|---|---|
| author | Hande İştar Buğra Harmandar |
| author_facet | Hande İştar Buğra Harmandar |
| author_sort | Hande İştar |
| collection | DOAJ |
| description | Interruption of vena cava inferior (VCI) is extremely rare, in occurrence in isolation or association with asplenia or polysplenia syndromes. In this abnormality, the infrahepatic segment of the VCI is absent, by representing the inadequacy of fusion of subcardinal embryological parts of the VCI. It is compensated by an azygos or hemiazygos vein that continues on the posterior wall of the thoracic cavity. In this case report, a case of incidentally diagnosed interrupted VCI in a patient diagnosed with tetralogy of Fallot (TOF), major aortopulmonary collateral artery (MAPCA), right arcus aorta, absence of right vena cava superior (VCS), and persistent left vena cava superior (PLVCS), and its successful surgical treatment was presented. If the hepatic vein confluence is of adequate size, the cannulation for cardiopulmonary bypass circuit through the hepatic vein confluence is safe in case of interrupted VCI. |
| format | Article |
| id | doaj-art-890b1c7da41448a0bca57df293018e00 |
| institution | OA Journals |
| issn | 1307-671X |
| language | English |
| publishDate | 2025-04-01 |
| publisher | Duzce University |
| record_format | Article |
| series | Düzce Tıp Fakültesi Dergisi |
| spelling | doaj-art-890b1c7da41448a0bca57df293018e002025-08-20T02:18:43ZengDuzce UniversityDüzce Tıp Fakültesi Dergisi1307-671X2025-04-0127110210410.18678/dtfd.158076997Tetralogy of Fallot, Absent Vena Cava Superior, Persistent Left Vena Cava Superior, and Interrupted Vena Cava Inferior: A Case of Struggle in Open Heart SurgeryHande İştar0https://orcid.org/0000-0002-7150-0171Buğra Harmandar1https://orcid.org/0000-0002-7487-1779Muğla Sıtkı Koçman University Medical Faculty Cardiovascular Surgery DepartmentMuğla Sıtkı Koçman University Medical Faculty Cardiovascular Surgery DepartmentInterruption of vena cava inferior (VCI) is extremely rare, in occurrence in isolation or association with asplenia or polysplenia syndromes. In this abnormality, the infrahepatic segment of the VCI is absent, by representing the inadequacy of fusion of subcardinal embryological parts of the VCI. It is compensated by an azygos or hemiazygos vein that continues on the posterior wall of the thoracic cavity. In this case report, a case of incidentally diagnosed interrupted VCI in a patient diagnosed with tetralogy of Fallot (TOF), major aortopulmonary collateral artery (MAPCA), right arcus aorta, absence of right vena cava superior (VCS), and persistent left vena cava superior (PLVCS), and its successful surgical treatment was presented. If the hepatic vein confluence is of adequate size, the cannulation for cardiopulmonary bypass circuit through the hepatic vein confluence is safe in case of interrupted VCI.https://dergipark.org.tr/en/download/article-file/4346088superior vena cavainferior vena cavapersistent left vena cava superiortetralogy of fallotsuperior vena kavainferior vena kavapersistan sol vena kava superiorfallot tetralojisi |
| spellingShingle | Hande İştar Buğra Harmandar Tetralogy of Fallot, Absent Vena Cava Superior, Persistent Left Vena Cava Superior, and Interrupted Vena Cava Inferior: A Case of Struggle in Open Heart Surgery Düzce Tıp Fakültesi Dergisi superior vena cava inferior vena cava persistent left vena cava superior tetralogy of fallot superior vena kava inferior vena kava persistan sol vena kava superior fallot tetralojisi |
| title | Tetralogy of Fallot, Absent Vena Cava Superior, Persistent Left Vena Cava Superior, and Interrupted Vena Cava Inferior: A Case of Struggle in Open Heart Surgery |
| title_full | Tetralogy of Fallot, Absent Vena Cava Superior, Persistent Left Vena Cava Superior, and Interrupted Vena Cava Inferior: A Case of Struggle in Open Heart Surgery |
| title_fullStr | Tetralogy of Fallot, Absent Vena Cava Superior, Persistent Left Vena Cava Superior, and Interrupted Vena Cava Inferior: A Case of Struggle in Open Heart Surgery |
| title_full_unstemmed | Tetralogy of Fallot, Absent Vena Cava Superior, Persistent Left Vena Cava Superior, and Interrupted Vena Cava Inferior: A Case of Struggle in Open Heart Surgery |
| title_short | Tetralogy of Fallot, Absent Vena Cava Superior, Persistent Left Vena Cava Superior, and Interrupted Vena Cava Inferior: A Case of Struggle in Open Heart Surgery |
| title_sort | tetralogy of fallot absent vena cava superior persistent left vena cava superior and interrupted vena cava inferior a case of struggle in open heart surgery |
| topic | superior vena cava inferior vena cava persistent left vena cava superior tetralogy of fallot superior vena kava inferior vena kava persistan sol vena kava superior fallot tetralojisi |
| url | https://dergipark.org.tr/en/download/article-file/4346088 |
| work_keys_str_mv | AT handeistar tetralogyoffallotabsentvenacavasuperiorpersistentleftvenacavasuperiorandinterruptedvenacavainferioracaseofstruggleinopenheartsurgery AT bugraharmandar tetralogyoffallotabsentvenacavasuperiorpersistentleftvenacavasuperiorandinterruptedvenacavainferioracaseofstruggleinopenheartsurgery |