Paroxysmal Autonomic Instability with Dystonia after Pneumococcal Meningoencephalitis

Streptococcus pneumoniae is a common cause of bacterial meningitis, frequently resulting in severe neurological impairment. A seven-month-old child presenting with Streptococcus pneumoniae meningoencephalitis developed right basal ganglia and hypothalamic infarctions. Daily episodes of agitation, hy...

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Main Authors: Layal Safadieh, Rana Sharara-Chami, Omar Dabbagh
Format: Article
Language:English
Published: Wiley 2012-01-01
Series:Case Reports in Medicine
Online Access:http://dx.doi.org/10.1155/2012/965932
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author Layal Safadieh
Rana Sharara-Chami
Omar Dabbagh
author_facet Layal Safadieh
Rana Sharara-Chami
Omar Dabbagh
author_sort Layal Safadieh
collection DOAJ
description Streptococcus pneumoniae is a common cause of bacterial meningitis, frequently resulting in severe neurological impairment. A seven-month-old child presenting with Streptococcus pneumoniae meningoencephalitis developed right basal ganglia and hypothalamic infarctions. Daily episodes of agitation, hypertension, tachycardia, diaphoresis, hyperthermia, and decerebrate posturing were observed. The diagnosis of paroxysmal autonomic instability with dystonia was established. The patient responded to clonidine, baclofen, and benzodiazepines. Although this entity has been reported in association with traumatic brain injury, and as a sequel to some nervous system infections, this is the first case, to our knowledge, associated with pneumococcal meningoencephalitis.
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spelling doaj-art-88fb4838acce408aa4d16bef09abe4c52025-08-20T02:09:11ZengWileyCase Reports in Medicine1687-96271687-96352012-01-01201210.1155/2012/965932965932Paroxysmal Autonomic Instability with Dystonia after Pneumococcal MeningoencephalitisLayal Safadieh0Rana Sharara-Chami1Omar Dabbagh2Division of Neurology, Department of Pediatrics and Adolescent Medicine, American University of Beirut Medical Center, P.O. Box 11-0236, Riad El Solh, Beirut 1107 2020, LebanonDivision of Critical Care Medicine, Department of Pediatrics and Adolescent Medicine, American University of Beirut Medical Center, Beirut 1107 2020, LebanonDivision of Neurology, Department of Pediatrics and Adolescent Medicine, American University of Beirut Medical Center, P.O. Box 11-0236, Riad El Solh, Beirut 1107 2020, LebanonStreptococcus pneumoniae is a common cause of bacterial meningitis, frequently resulting in severe neurological impairment. A seven-month-old child presenting with Streptococcus pneumoniae meningoencephalitis developed right basal ganglia and hypothalamic infarctions. Daily episodes of agitation, hypertension, tachycardia, diaphoresis, hyperthermia, and decerebrate posturing were observed. The diagnosis of paroxysmal autonomic instability with dystonia was established. The patient responded to clonidine, baclofen, and benzodiazepines. Although this entity has been reported in association with traumatic brain injury, and as a sequel to some nervous system infections, this is the first case, to our knowledge, associated with pneumococcal meningoencephalitis.http://dx.doi.org/10.1155/2012/965932
spellingShingle Layal Safadieh
Rana Sharara-Chami
Omar Dabbagh
Paroxysmal Autonomic Instability with Dystonia after Pneumococcal Meningoencephalitis
Case Reports in Medicine
title Paroxysmal Autonomic Instability with Dystonia after Pneumococcal Meningoencephalitis
title_full Paroxysmal Autonomic Instability with Dystonia after Pneumococcal Meningoencephalitis
title_fullStr Paroxysmal Autonomic Instability with Dystonia after Pneumococcal Meningoencephalitis
title_full_unstemmed Paroxysmal Autonomic Instability with Dystonia after Pneumococcal Meningoencephalitis
title_short Paroxysmal Autonomic Instability with Dystonia after Pneumococcal Meningoencephalitis
title_sort paroxysmal autonomic instability with dystonia after pneumococcal meningoencephalitis
url http://dx.doi.org/10.1155/2012/965932
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