Modern View on Very Early Onset and Early Onset Inflammatory Bowel Diseases in Children

Nowadays, an urgent problem of pediatric gastroenterology is the study of inflammatory bowel diseases with very early onset (VEO-IBD), which have unique genetic, clinical, immunological, morphological, and laboratory sings. Early VEO-IBD is usually considered as monogenic disease, especially in comb...

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Main Authors: Anatoly I. Khavkin, Anastasiya A. Permyakova, Mariya O. Tsepilova, Aleksandra V. Kaplina, Stanislav I. Sitkin, Andrey N. Surkov, Stanislav D. Getmanov
Format: Article
Language:English
Published: "Paediatrician" Publishers LLC 2024-07-01
Series:Вопросы современной педиатрии
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Online Access:https://vsp.spr-journal.ru/jour/article/view/3519
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author Anatoly I. Khavkin
Anastasiya A. Permyakova
Mariya O. Tsepilova
Aleksandra V. Kaplina
Stanislav I. Sitkin
Andrey N. Surkov
Stanislav D. Getmanov
author_facet Anatoly I. Khavkin
Anastasiya A. Permyakova
Mariya O. Tsepilova
Aleksandra V. Kaplina
Stanislav I. Sitkin
Andrey N. Surkov
Stanislav D. Getmanov
author_sort Anatoly I. Khavkin
collection DOAJ
description Nowadays, an urgent problem of pediatric gastroenterology is the study of inflammatory bowel diseases with very early onset (VEO-IBD), which have unique genetic, clinical, immunological, morphological, and laboratory sings. Early VEO-IBD is usually considered as monogenic disease, especially in combination with congenital immune defects, which leads to difficulties in diagnosis and management this pathology. Despite this, systematization of information about this group of nosological forms of IBD is practically not carried out. This article presents a review of the available information on etiological factors, course variants, and therapeutic options for VEO-IBD.
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publishDate 2024-07-01
publisher "Paediatrician" Publishers LLC
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series Вопросы современной педиатрии
spelling doaj-art-842641a971ca452f885777c08f4d09082025-08-20T03:21:55Zeng"Paediatrician" Publishers LLCВопросы современной педиатрии1682-55271682-55352024-07-0123314515110.15690/vsp.v23i3.27682173Modern View on Very Early Onset and Early Onset Inflammatory Bowel Diseases in ChildrenAnatoly I. Khavkin0Anastasiya A. Permyakova1Mariya O. Tsepilova2Aleksandra V. Kaplina3Stanislav I. Sitkin4Andrey N. Surkov5Stanislav D. Getmanov6Research and Clinical Institute for Children; Belgorod State UniversitySaint Petersburg State Pediatric Medical UniversitySaint Petersburg State Pediatric Medical UniversityAlmazov National Medical Research CentreAlmazov National Medical Research Centre; North-Western State Medical University named after I.I. MechnikovResearch Institute of Pediatrics and Children’s Health in Petrovsky National Research Centre of Surgery; Pirogov Russian National Research Medical UniversityPirogov Russian National Research Medical UniversityNowadays, an urgent problem of pediatric gastroenterology is the study of inflammatory bowel diseases with very early onset (VEO-IBD), which have unique genetic, clinical, immunological, morphological, and laboratory sings. Early VEO-IBD is usually considered as monogenic disease, especially in combination with congenital immune defects, which leads to difficulties in diagnosis and management this pathology. Despite this, systematization of information about this group of nosological forms of IBD is practically not carried out. This article presents a review of the available information on etiological factors, course variants, and therapeutic options for VEO-IBD.https://vsp.spr-journal.ru/jour/article/view/3519early onset inflammatory bowel diseasevery early onset inflammatory bowel diseasecrohn's diseaseulcerative colitisindeterminate colitisnecrotizing enterocolitis
spellingShingle Anatoly I. Khavkin
Anastasiya A. Permyakova
Mariya O. Tsepilova
Aleksandra V. Kaplina
Stanislav I. Sitkin
Andrey N. Surkov
Stanislav D. Getmanov
Modern View on Very Early Onset and Early Onset Inflammatory Bowel Diseases in Children
Вопросы современной педиатрии
early onset inflammatory bowel disease
very early onset inflammatory bowel disease
crohn's disease
ulcerative colitis
indeterminate colitis
necrotizing enterocolitis
title Modern View on Very Early Onset and Early Onset Inflammatory Bowel Diseases in Children
title_full Modern View on Very Early Onset and Early Onset Inflammatory Bowel Diseases in Children
title_fullStr Modern View on Very Early Onset and Early Onset Inflammatory Bowel Diseases in Children
title_full_unstemmed Modern View on Very Early Onset and Early Onset Inflammatory Bowel Diseases in Children
title_short Modern View on Very Early Onset and Early Onset Inflammatory Bowel Diseases in Children
title_sort modern view on very early onset and early onset inflammatory bowel diseases in children
topic early onset inflammatory bowel disease
very early onset inflammatory bowel disease
crohn's disease
ulcerative colitis
indeterminate colitis
necrotizing enterocolitis
url https://vsp.spr-journal.ru/jour/article/view/3519
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