Mitochondrial myopathy with respiratory muscle involvement: a case report

A case of a 10-year-old patient with a benign congenital myopathy, suddenly aggravated because of an accentuated deficit in respiratory muscles is reported. The institution of assisted respiration at night allowed the patient to return to her daily activities. Examination of muscular biopsy with ult...

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Main Authors: J. A. Levy, Ana M. Tsanaclis, P. A. P. Saraiva, Carmen C. Mion, Paulo N. B. Salum
Format: Article
Language:English
Published: Thieme Revinter Publicações 1983-03-01
Series:Arquivos de Neuro-Psiquiatria
Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X1983000100008&lng=en&tlng=en
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author J. A. Levy
Ana M. Tsanaclis
P. A. P. Saraiva
Carmen C. Mion
Paulo N. B. Salum
author_facet J. A. Levy
Ana M. Tsanaclis
P. A. P. Saraiva
Carmen C. Mion
Paulo N. B. Salum
author_sort J. A. Levy
collection DOAJ
description A case of a 10-year-old patient with a benign congenital myopathy, suddenly aggravated because of an accentuated deficit in respiratory muscles is reported. The institution of assisted respiration at night allowed the patient to return to her daily activities. Examination of muscular biopsy with ultra-microscope permitted the diagnosis of mitochondrial myopathy.
format Article
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institution Kabale University
issn 1678-4227
language English
publishDate 1983-03-01
publisher Thieme Revinter Publicações
record_format Article
series Arquivos de Neuro-Psiquiatria
spelling doaj-art-8417f4cf2dae49c484934f3fe78dfc722025-08-20T03:37:46ZengThieme Revinter PublicaçõesArquivos de Neuro-Psiquiatria1678-42271983-03-01411869010.1590/S0004-282X1983000100008S0004-282X1983000100008Mitochondrial myopathy with respiratory muscle involvement: a case reportJ. A. Levy0Ana M. Tsanaclis1P. A. P. Saraiva2Carmen C. Mion3Paulo N. B. Salum4Universidade de São PauloUniversidade de São PauloUniversidade de São PauloUniversidade de São PauloUniversidade de São PauloA case of a 10-year-old patient with a benign congenital myopathy, suddenly aggravated because of an accentuated deficit in respiratory muscles is reported. The institution of assisted respiration at night allowed the patient to return to her daily activities. Examination of muscular biopsy with ultra-microscope permitted the diagnosis of mitochondrial myopathy.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X1983000100008&lng=en&tlng=en
spellingShingle J. A. Levy
Ana M. Tsanaclis
P. A. P. Saraiva
Carmen C. Mion
Paulo N. B. Salum
Mitochondrial myopathy with respiratory muscle involvement: a case report
Arquivos de Neuro-Psiquiatria
title Mitochondrial myopathy with respiratory muscle involvement: a case report
title_full Mitochondrial myopathy with respiratory muscle involvement: a case report
title_fullStr Mitochondrial myopathy with respiratory muscle involvement: a case report
title_full_unstemmed Mitochondrial myopathy with respiratory muscle involvement: a case report
title_short Mitochondrial myopathy with respiratory muscle involvement: a case report
title_sort mitochondrial myopathy with respiratory muscle involvement a case report
url http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X1983000100008&lng=en&tlng=en
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AT papsaraiva mitochondrialmyopathywithrespiratorymuscleinvolvementacasereport
AT carmencmion mitochondrialmyopathywithrespiratorymuscleinvolvementacasereport
AT paulonbsalum mitochondrialmyopathywithrespiratorymuscleinvolvementacasereport