An Unusual Cause of Hypoxia: Ventricular Septal Defect, Pulmonary Artery Atresia, and Major Aortopulmonary Collaterals Diagnosed in the Adult Cardiac Catheterization Lab
The association of pulmonary atresia, ventricular septal defect (VSD) and major aortopulmonary collaterals (MAPCA) is an extreme form of tetralogy of Fallot (TOF). It carries a high mortality risk if not intervened on during infancy with only 20% of unoperated patients surviving into adulthood. We p...
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| Format: | Article |
| Language: | English |
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Wiley
2020-01-01
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| Series: | Case Reports in Cardiology |
| Online Access: | http://dx.doi.org/10.1155/2020/4726529 |
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| author | Katia Bravo-Jaimes Brian Walton Poyee Tung Richard W. Smalling |
| author_facet | Katia Bravo-Jaimes Brian Walton Poyee Tung Richard W. Smalling |
| author_sort | Katia Bravo-Jaimes |
| collection | DOAJ |
| description | The association of pulmonary atresia, ventricular septal defect (VSD) and major aortopulmonary collaterals (MAPCA) is an extreme form of tetralogy of Fallot (TOF). It carries a high mortality risk if not intervened on during infancy with only 20% of unoperated patients surviving into adulthood. We present the case of a 40-year-old man who presented for evaluation prior to retinal surgery and was found to have hypoxia and a loud murmur. Cardiac catheterization was performed in the general catheterization laboratory, demonstrating a membranous VSD, pulmonary atresia, and MAPCA. We highlight the challenges and limitations that an adult interventional cardiologist may have when encountering these patients. |
| format | Article |
| id | doaj-art-83166e4dcd244fc3afdb3e86035c19d8 |
| institution | OA Journals |
| issn | 2090-6404 2090-6412 |
| language | English |
| publishDate | 2020-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Cardiology |
| spelling | doaj-art-83166e4dcd244fc3afdb3e86035c19d82025-08-20T02:09:00ZengWileyCase Reports in Cardiology2090-64042090-64122020-01-01202010.1155/2020/47265294726529An Unusual Cause of Hypoxia: Ventricular Septal Defect, Pulmonary Artery Atresia, and Major Aortopulmonary Collaterals Diagnosed in the Adult Cardiac Catheterization LabKatia Bravo-Jaimes0Brian Walton1Poyee Tung2Richard W. Smalling3Division of Cardiology, University of Texas Health Science Center at Houston, Houston, Texas, USADivision of Cardiology, University of Texas Health Science Center at Houston, Houston, Texas, USADivision of Cardiology, University of Texas Health Science Center at Houston, Houston, Texas, USADivision of Cardiology, University of Texas Health Science Center at Houston, Houston, Texas, USAThe association of pulmonary atresia, ventricular septal defect (VSD) and major aortopulmonary collaterals (MAPCA) is an extreme form of tetralogy of Fallot (TOF). It carries a high mortality risk if not intervened on during infancy with only 20% of unoperated patients surviving into adulthood. We present the case of a 40-year-old man who presented for evaluation prior to retinal surgery and was found to have hypoxia and a loud murmur. Cardiac catheterization was performed in the general catheterization laboratory, demonstrating a membranous VSD, pulmonary atresia, and MAPCA. We highlight the challenges and limitations that an adult interventional cardiologist may have when encountering these patients.http://dx.doi.org/10.1155/2020/4726529 |
| spellingShingle | Katia Bravo-Jaimes Brian Walton Poyee Tung Richard W. Smalling An Unusual Cause of Hypoxia: Ventricular Septal Defect, Pulmonary Artery Atresia, and Major Aortopulmonary Collaterals Diagnosed in the Adult Cardiac Catheterization Lab Case Reports in Cardiology |
| title | An Unusual Cause of Hypoxia: Ventricular Septal Defect, Pulmonary Artery Atresia, and Major Aortopulmonary Collaterals Diagnosed in the Adult Cardiac Catheterization Lab |
| title_full | An Unusual Cause of Hypoxia: Ventricular Septal Defect, Pulmonary Artery Atresia, and Major Aortopulmonary Collaterals Diagnosed in the Adult Cardiac Catheterization Lab |
| title_fullStr | An Unusual Cause of Hypoxia: Ventricular Septal Defect, Pulmonary Artery Atresia, and Major Aortopulmonary Collaterals Diagnosed in the Adult Cardiac Catheterization Lab |
| title_full_unstemmed | An Unusual Cause of Hypoxia: Ventricular Septal Defect, Pulmonary Artery Atresia, and Major Aortopulmonary Collaterals Diagnosed in the Adult Cardiac Catheterization Lab |
| title_short | An Unusual Cause of Hypoxia: Ventricular Septal Defect, Pulmonary Artery Atresia, and Major Aortopulmonary Collaterals Diagnosed in the Adult Cardiac Catheterization Lab |
| title_sort | unusual cause of hypoxia ventricular septal defect pulmonary artery atresia and major aortopulmonary collaterals diagnosed in the adult cardiac catheterization lab |
| url | http://dx.doi.org/10.1155/2020/4726529 |
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