Successful correction of hemophilia by CRISPR/Cas9 genome editing in vivo: delivery vector and immune responses are the key to success

Abstract Hemophilia B is a serious hemostasis disorder due to mutations of the factor IX gene in the X chromosome. Gene therapy has gained momentum in recent years as a therapeutic option for hemophilia B. In hemophilia, reconstitution with a mere 1–2% of the clotting factor improves the quality of...

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Main Authors: Tuan Huy Nguyen, Ignacio Anegon
Format: Article
Language:English
Published: Springer Nature 2016-04-01
Series:EMBO Molecular Medicine
Online Access:https://doi.org/10.15252/emmm.201606325
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author Tuan Huy Nguyen
Ignacio Anegon
author_facet Tuan Huy Nguyen
Ignacio Anegon
author_sort Tuan Huy Nguyen
collection DOAJ
description Abstract Hemophilia B is a serious hemostasis disorder due to mutations of the factor IX gene in the X chromosome. Gene therapy has gained momentum in recent years as a therapeutic option for hemophilia B. In hemophilia, reconstitution with a mere 1–2% of the clotting factor improves the quality of life, while 5–20% suffices to ameliorate the bleeding disorder. A paper by Guan et al (2016) in this issue of EMBO Molecular Medicine reports on the direct CRISPRs/Cas9‐mediated correction in the liver of a hemophilia‐causing point mutation in FIX.
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publishDate 2016-04-01
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spelling doaj-art-82cd7f84374d4624bebcce2420092fa32025-08-20T03:05:55ZengSpringer NatureEMBO Molecular Medicine1757-46761757-46842016-04-018543944110.15252/emmm.201606325Successful correction of hemophilia by CRISPR/Cas9 genome editing in vivo: delivery vector and immune responses are the key to successTuan Huy Nguyen0Ignacio Anegon1INSERM, UMR 1064‐Center for Research in Transplantation and ImmunologyINSERM, UMR 1064‐Center for Research in Transplantation and ImmunologyAbstract Hemophilia B is a serious hemostasis disorder due to mutations of the factor IX gene in the X chromosome. Gene therapy has gained momentum in recent years as a therapeutic option for hemophilia B. In hemophilia, reconstitution with a mere 1–2% of the clotting factor improves the quality of life, while 5–20% suffices to ameliorate the bleeding disorder. A paper by Guan et al (2016) in this issue of EMBO Molecular Medicine reports on the direct CRISPRs/Cas9‐mediated correction in the liver of a hemophilia‐causing point mutation in FIX.https://doi.org/10.15252/emmm.201606325
spellingShingle Tuan Huy Nguyen
Ignacio Anegon
Successful correction of hemophilia by CRISPR/Cas9 genome editing in vivo: delivery vector and immune responses are the key to success
EMBO Molecular Medicine
title Successful correction of hemophilia by CRISPR/Cas9 genome editing in vivo: delivery vector and immune responses are the key to success
title_full Successful correction of hemophilia by CRISPR/Cas9 genome editing in vivo: delivery vector and immune responses are the key to success
title_fullStr Successful correction of hemophilia by CRISPR/Cas9 genome editing in vivo: delivery vector and immune responses are the key to success
title_full_unstemmed Successful correction of hemophilia by CRISPR/Cas9 genome editing in vivo: delivery vector and immune responses are the key to success
title_short Successful correction of hemophilia by CRISPR/Cas9 genome editing in vivo: delivery vector and immune responses are the key to success
title_sort successful correction of hemophilia by crispr cas9 genome editing in vivo delivery vector and immune responses are the key to success
url https://doi.org/10.15252/emmm.201606325
work_keys_str_mv AT tuanhuynguyen successfulcorrectionofhemophiliabycrisprcas9genomeeditinginvivodeliveryvectorandimmuneresponsesarethekeytosuccess
AT ignacioanegon successfulcorrectionofhemophiliabycrisprcas9genomeeditinginvivodeliveryvectorandimmuneresponsesarethekeytosuccess