IgG4-Related Hepatic Pseudotumor Masquerading as a Klatskin Tumor
Immunoglobulin G subclass 4 (IgG-4)-related disease (IgG4-RD) is an uncommon immune-mediated, fibro-inflammatory disease which has garnered recognition as a systemic condition. One manifestation of the disease in the hepatobiliary system is the development of hepatic inflammatory pseudotumors. These...
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| Format: | Article |
| Language: | English |
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Wiley
2022-01-01
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| Series: | Case Reports in Hepatology |
| Online Access: | http://dx.doi.org/10.1155/2022/5765116 |
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| _version_ | 1832554714950008832 |
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| author | Jennifer Yoon Steve Hu Daniel Phillips Amir Fathi Adnan Ameer |
| author_facet | Jennifer Yoon Steve Hu Daniel Phillips Amir Fathi Adnan Ameer |
| author_sort | Jennifer Yoon |
| collection | DOAJ |
| description | Immunoglobulin G subclass 4 (IgG-4)-related disease (IgG4-RD) is an uncommon immune-mediated, fibro-inflammatory disease which has garnered recognition as a systemic condition. One manifestation of the disease in the hepatobiliary system is the development of hepatic inflammatory pseudotumors. These benign tumors are often misdiagnosed as malignant tumors and undergo unnecessary hepatic resections. We present a case of IgG4-related hepatic inflammatory pseudotumor (IPT) mimicking a Klatskin tumor. A high degree of clinical suspicion and extensive workup is imperative in reaching the correct diagnosis. IgG4-related inflammatory pseudotumor is a rare entity, but an important consideration in evaluating hepatic tumors. |
| format | Article |
| id | doaj-art-8257ea4bc78a4f1fa60210deec9578ec |
| institution | Kabale University |
| issn | 2090-6595 |
| language | English |
| publishDate | 2022-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Hepatology |
| spelling | doaj-art-8257ea4bc78a4f1fa60210deec9578ec2025-02-03T05:50:40ZengWileyCase Reports in Hepatology2090-65952022-01-01202210.1155/2022/5765116IgG4-Related Hepatic Pseudotumor Masquerading as a Klatskin TumorJennifer Yoon0Steve Hu1Daniel Phillips2Amir Fathi3Adnan Ameer4Department of Internal MedicineDepartment of Gastroenterology and HepatologyDepartment of PathologyDepartment of SurgeryDepartment of Gastroenterology and HepatologyImmunoglobulin G subclass 4 (IgG-4)-related disease (IgG4-RD) is an uncommon immune-mediated, fibro-inflammatory disease which has garnered recognition as a systemic condition. One manifestation of the disease in the hepatobiliary system is the development of hepatic inflammatory pseudotumors. These benign tumors are often misdiagnosed as malignant tumors and undergo unnecessary hepatic resections. We present a case of IgG4-related hepatic inflammatory pseudotumor (IPT) mimicking a Klatskin tumor. A high degree of clinical suspicion and extensive workup is imperative in reaching the correct diagnosis. IgG4-related inflammatory pseudotumor is a rare entity, but an important consideration in evaluating hepatic tumors.http://dx.doi.org/10.1155/2022/5765116 |
| spellingShingle | Jennifer Yoon Steve Hu Daniel Phillips Amir Fathi Adnan Ameer IgG4-Related Hepatic Pseudotumor Masquerading as a Klatskin Tumor Case Reports in Hepatology |
| title | IgG4-Related Hepatic Pseudotumor Masquerading as a Klatskin Tumor |
| title_full | IgG4-Related Hepatic Pseudotumor Masquerading as a Klatskin Tumor |
| title_fullStr | IgG4-Related Hepatic Pseudotumor Masquerading as a Klatskin Tumor |
| title_full_unstemmed | IgG4-Related Hepatic Pseudotumor Masquerading as a Klatskin Tumor |
| title_short | IgG4-Related Hepatic Pseudotumor Masquerading as a Klatskin Tumor |
| title_sort | igg4 related hepatic pseudotumor masquerading as a klatskin tumor |
| url | http://dx.doi.org/10.1155/2022/5765116 |
| work_keys_str_mv | AT jenniferyoon igg4relatedhepaticpseudotumormasqueradingasaklatskintumor AT stevehu igg4relatedhepaticpseudotumormasqueradingasaklatskintumor AT danielphillips igg4relatedhepaticpseudotumormasqueradingasaklatskintumor AT amirfathi igg4relatedhepaticpseudotumormasqueradingasaklatskintumor AT adnanameer igg4relatedhepaticpseudotumormasqueradingasaklatskintumor |