Cardiac Sarcoidosis and Troponin T-Related Cardiomyopathy

Background: Cardiac sarcoidosis and genetic cardiomyopathy are both rare causes of heart disease with often similar presentations that can be difficult to diagnose. Case Summary: We describe a previously healthy 43-year-old woman with progressive cardiomyopathy despite thorough investigation and sev...

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Bibliographic Details
Main Authors: Alec Chu Ming Yu, MD, Anto Sedlic, MD, Harmanjot Singh, MD, Kathryn Darras, MD, Brian Clarke, MD, Thomas M. Roston, MD, PhD
Format: Article
Language:English
Published: Elsevier 2025-07-01
Series:JACC: Case Reports
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Online Access:http://www.sciencedirect.com/science/article/pii/S2666084925006576
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Summary:Background: Cardiac sarcoidosis and genetic cardiomyopathy are both rare causes of heart disease with often similar presentations that can be difficult to diagnose. Case Summary: We describe a previously healthy 43-year-old woman with progressive cardiomyopathy despite thorough investigation and several trials of therapy. She was eventually diagnosed with both cardiac sarcoidosis and a familial cardiac troponin type 2 (TNNT2) variant encoding cardiac troponin type 2. Discussion: Previous studies demonstrate that a proportion of patients diagnosed with isolated cardiac sarcoidosis or idiopathic myocarditis have pathogenic variants linked to genetic cardiomyopathy. Our case highlights the challenging journey of a patient who was eventually found to have both sarcoidosis and genetic cardiomyopathy, and we discuss relevant principles in diagnosing and managing these concurrent pathologies.
ISSN:2666-0849