The nonconventional MHC class II molecule DM governs diabetes susceptibility in NOD mice.

The spontaneous destruction of insulin producing pancreatic beta cells in non-obese diabetic (NOD) mice provides a valuable model of type 1 diabetes. As in humans, disease susceptibility is controlled by the classical MHC class II genes that guide CD4(+) T cell responses to self and foreign antigens...

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Main Authors: Marc A J Morgan, Pari S S Muller, Arne Mould, Stephen A Newland, Jennifer Nichols, Elizabeth J Robertson, Anne Cooke, Elizabeth K Bikoff
Format: Article
Language:English
Published: Public Library of Science (PLoS) 2013-01-01
Series:PLoS ONE
Online Access:https://journals.plos.org/plosone/article/file?id=10.1371/journal.pone.0056738&type=printable
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author Marc A J Morgan
Pari S S Muller
Arne Mould
Stephen A Newland
Jennifer Nichols
Elizabeth J Robertson
Anne Cooke
Elizabeth K Bikoff
author_facet Marc A J Morgan
Pari S S Muller
Arne Mould
Stephen A Newland
Jennifer Nichols
Elizabeth J Robertson
Anne Cooke
Elizabeth K Bikoff
author_sort Marc A J Morgan
collection DOAJ
description The spontaneous destruction of insulin producing pancreatic beta cells in non-obese diabetic (NOD) mice provides a valuable model of type 1 diabetes. As in humans, disease susceptibility is controlled by the classical MHC class II genes that guide CD4(+) T cell responses to self and foreign antigens. It has long been suspected that the dedicated class II chaperone designated HLA-DM in humans or H-2M in mice also makes an important contribution, but due to tight linkage within the MHC, a possible role played by DM peptide editing has not been previously tested by conventional genetic approaches. Here we exploited newly established germ-line competent NOD ES cells to engineer a loss of function allele. DM deficient NOD mice display defective class II peptide occupancy and surface expression, and are completely protected against type 1 diabetes. Interestingly the mutation results in increased proportional representation of CD4(+)Foxp3(+) regulatory T cells and the absence of pathogenic CD4(+) T effectors. Overall, this striking phenotype establishes that DM-mediated peptide selection plays an essential role in the development of autoimmune diabetes in NOD mice.
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spelling doaj-art-7eebef782171470eb7208f3e17de928d2025-08-20T02:30:38ZengPublic Library of Science (PLoS)PLoS ONE1932-62032013-01-0182e5673810.1371/journal.pone.0056738The nonconventional MHC class II molecule DM governs diabetes susceptibility in NOD mice.Marc A J MorganPari S S MullerArne MouldStephen A NewlandJennifer NicholsElizabeth J RobertsonAnne CookeElizabeth K BikoffThe spontaneous destruction of insulin producing pancreatic beta cells in non-obese diabetic (NOD) mice provides a valuable model of type 1 diabetes. As in humans, disease susceptibility is controlled by the classical MHC class II genes that guide CD4(+) T cell responses to self and foreign antigens. It has long been suspected that the dedicated class II chaperone designated HLA-DM in humans or H-2M in mice also makes an important contribution, but due to tight linkage within the MHC, a possible role played by DM peptide editing has not been previously tested by conventional genetic approaches. Here we exploited newly established germ-line competent NOD ES cells to engineer a loss of function allele. DM deficient NOD mice display defective class II peptide occupancy and surface expression, and are completely protected against type 1 diabetes. Interestingly the mutation results in increased proportional representation of CD4(+)Foxp3(+) regulatory T cells and the absence of pathogenic CD4(+) T effectors. Overall, this striking phenotype establishes that DM-mediated peptide selection plays an essential role in the development of autoimmune diabetes in NOD mice.https://journals.plos.org/plosone/article/file?id=10.1371/journal.pone.0056738&type=printable
spellingShingle Marc A J Morgan
Pari S S Muller
Arne Mould
Stephen A Newland
Jennifer Nichols
Elizabeth J Robertson
Anne Cooke
Elizabeth K Bikoff
The nonconventional MHC class II molecule DM governs diabetes susceptibility in NOD mice.
PLoS ONE
title The nonconventional MHC class II molecule DM governs diabetes susceptibility in NOD mice.
title_full The nonconventional MHC class II molecule DM governs diabetes susceptibility in NOD mice.
title_fullStr The nonconventional MHC class II molecule DM governs diabetes susceptibility in NOD mice.
title_full_unstemmed The nonconventional MHC class II molecule DM governs diabetes susceptibility in NOD mice.
title_short The nonconventional MHC class II molecule DM governs diabetes susceptibility in NOD mice.
title_sort nonconventional mhc class ii molecule dm governs diabetes susceptibility in nod mice
url https://journals.plos.org/plosone/article/file?id=10.1371/journal.pone.0056738&type=printable
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