A paracrine activin A–mDia2 axis promotes squamous carcinogenesis via fibroblast reprogramming

Abstract Cancer‐associated fibroblasts (CAFs) are key regulators of tumorigenesis and promising targets for next‐generation therapies. We discovered that cancer cell‐derived activin A reprograms fibroblasts into pro‐tumorigenic CAFs. Mechanistically, this occurs via Smad2‐mediated transcriptional re...

Full description

Saved in:
Bibliographic Details
Main Authors: Michael Cangkrama, Mateusz Wietecha, Nicolas Mathis, Rin Okumura, Luca Ferrarese, Dunja Al‐Nuaimi, Maria Antsiferova, Reinhard Dummer, Metello Innocenti, Sabine Werner
Format: Article
Language:English
Published: Springer Nature 2020-03-01
Series:EMBO Molecular Medicine
Subjects:
Online Access:https://doi.org/10.15252/emmm.201911466
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1849226072477925376
author Michael Cangkrama
Mateusz Wietecha
Nicolas Mathis
Rin Okumura
Luca Ferrarese
Dunja Al‐Nuaimi
Maria Antsiferova
Reinhard Dummer
Metello Innocenti
Sabine Werner
author_facet Michael Cangkrama
Mateusz Wietecha
Nicolas Mathis
Rin Okumura
Luca Ferrarese
Dunja Al‐Nuaimi
Maria Antsiferova
Reinhard Dummer
Metello Innocenti
Sabine Werner
author_sort Michael Cangkrama
collection DOAJ
description Abstract Cancer‐associated fibroblasts (CAFs) are key regulators of tumorigenesis and promising targets for next‐generation therapies. We discovered that cancer cell‐derived activin A reprograms fibroblasts into pro‐tumorigenic CAFs. Mechanistically, this occurs via Smad2‐mediated transcriptional regulation of the formin mDia2, which directly promotes filopodia formation and cell migration. mDia2 also induces expression of CAF marker genes through prevention of p53 nuclear accumulation, resulting in the production of a pro‐tumorigenic matrisome and secretome. The translational relevance of this finding is reflected by activin A overexpression in tumor cells and of mDia2 in the stroma of skin cancer and other malignancies and the correlation of high activin A/mDia2 levels with poor patient survival. Blockade of this signaling axis using inhibitors of activin, activin receptors, or mDia2 suppressed cancer cell malignancy and squamous carcinogenesis in 3D organotypic cultures, ex vivo, and in vivo, providing a rationale for pharmacological inhibition of activin A‐mDia2 signaling in stratified cancer patients.
format Article
id doaj-art-7e9880af155f4dfe920e625f78f674f9
institution Kabale University
issn 1757-4676
1757-4684
language English
publishDate 2020-03-01
publisher Springer Nature
record_format Article
series EMBO Molecular Medicine
spelling doaj-art-7e9880af155f4dfe920e625f78f674f92025-08-24T11:44:13ZengSpringer NatureEMBO Molecular Medicine1757-46761757-46842020-03-0112412110.15252/emmm.201911466A paracrine activin A–mDia2 axis promotes squamous carcinogenesis via fibroblast reprogrammingMichael Cangkrama0Mateusz Wietecha1Nicolas Mathis2Rin Okumura3Luca Ferrarese4Dunja Al‐Nuaimi5Maria Antsiferova6Reinhard Dummer7Metello Innocenti8Sabine Werner9Department of Biology, Institute of Molecular Health Sciences, ETH ZurichDepartment of Biology, Institute of Molecular Health Sciences, ETH ZurichDepartment of Biology, Institute of Molecular Health Sciences, ETH ZurichDepartment of Biology, Institute of Molecular Health Sciences, ETH ZurichDepartment of Biology, Institute of Molecular Health Sciences, ETH ZurichDepartment of Biology, Institute of Molecular Health Sciences, ETH ZurichDepartment of Biology, Institute of Molecular Health Sciences, ETH ZurichDepartment of Dermatology, University Hospital ZurichHeidelberg University Biochemistry Center (BZH), Heidelberg UniversityDepartment of Biology, Institute of Molecular Health Sciences, ETH ZurichAbstract Cancer‐associated fibroblasts (CAFs) are key regulators of tumorigenesis and promising targets for next‐generation therapies. We discovered that cancer cell‐derived activin A reprograms fibroblasts into pro‐tumorigenic CAFs. Mechanistically, this occurs via Smad2‐mediated transcriptional regulation of the formin mDia2, which directly promotes filopodia formation and cell migration. mDia2 also induces expression of CAF marker genes through prevention of p53 nuclear accumulation, resulting in the production of a pro‐tumorigenic matrisome and secretome. The translational relevance of this finding is reflected by activin A overexpression in tumor cells and of mDia2 in the stroma of skin cancer and other malignancies and the correlation of high activin A/mDia2 levels with poor patient survival. Blockade of this signaling axis using inhibitors of activin, activin receptors, or mDia2 suppressed cancer cell malignancy and squamous carcinogenesis in 3D organotypic cultures, ex vivo, and in vivo, providing a rationale for pharmacological inhibition of activin A‐mDia2 signaling in stratified cancer patients.https://doi.org/10.15252/emmm.201911466activinCAFcarcinogenesismDia2tumor microenvironment
spellingShingle Michael Cangkrama
Mateusz Wietecha
Nicolas Mathis
Rin Okumura
Luca Ferrarese
Dunja Al‐Nuaimi
Maria Antsiferova
Reinhard Dummer
Metello Innocenti
Sabine Werner
A paracrine activin A–mDia2 axis promotes squamous carcinogenesis via fibroblast reprogramming
EMBO Molecular Medicine
activin
CAF
carcinogenesis
mDia2
tumor microenvironment
title A paracrine activin A–mDia2 axis promotes squamous carcinogenesis via fibroblast reprogramming
title_full A paracrine activin A–mDia2 axis promotes squamous carcinogenesis via fibroblast reprogramming
title_fullStr A paracrine activin A–mDia2 axis promotes squamous carcinogenesis via fibroblast reprogramming
title_full_unstemmed A paracrine activin A–mDia2 axis promotes squamous carcinogenesis via fibroblast reprogramming
title_short A paracrine activin A–mDia2 axis promotes squamous carcinogenesis via fibroblast reprogramming
title_sort paracrine activin a mdia2 axis promotes squamous carcinogenesis via fibroblast reprogramming
topic activin
CAF
carcinogenesis
mDia2
tumor microenvironment
url https://doi.org/10.15252/emmm.201911466
work_keys_str_mv AT michaelcangkrama aparacrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming
AT mateuszwietecha aparacrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming
AT nicolasmathis aparacrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming
AT rinokumura aparacrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming
AT lucaferrarese aparacrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming
AT dunjaalnuaimi aparacrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming
AT mariaantsiferova aparacrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming
AT reinharddummer aparacrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming
AT metelloinnocenti aparacrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming
AT sabinewerner aparacrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming
AT michaelcangkrama paracrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming
AT mateuszwietecha paracrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming
AT nicolasmathis paracrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming
AT rinokumura paracrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming
AT lucaferrarese paracrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming
AT dunjaalnuaimi paracrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming
AT mariaantsiferova paracrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming
AT reinharddummer paracrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming
AT metelloinnocenti paracrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming
AT sabinewerner paracrineactivinamdia2axispromotessquamouscarcinogenesisviafibroblastreprogramming