Computed tomography and magnetic resonance imaging features of primary liver perivascular epithelioid cell tumor with renal angiomyolipoma: a case report and literature review

Hepatic perivascular epithelioid cell tumor (PEComa) is an extremely rare mesenchymal tumor. The disease has few specific clinical symptoms and imaging manifestations, making its accurate diagnosis an intractable clinical challenge. This is a report of a female patient diagnosed with lesions and a m...

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Main Authors: Ruoling Gao, Jiaying Liu, Qingdian Cong, Zhilan Huang, Guoping Zhu, Xuan Jin, Jibo Hu
Format: Article
Language:English
Published: Frontiers Media S.A. 2025-06-01
Series:Frontiers in Oncology
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Online Access:https://www.frontiersin.org/articles/10.3389/fonc.2025.1534250/full
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author Ruoling Gao
Jiaying Liu
Qingdian Cong
Zhilan Huang
Guoping Zhu
Xuan Jin
Jibo Hu
author_facet Ruoling Gao
Jiaying Liu
Qingdian Cong
Zhilan Huang
Guoping Zhu
Xuan Jin
Jibo Hu
author_sort Ruoling Gao
collection DOAJ
description Hepatic perivascular epithelioid cell tumor (PEComa) is an extremely rare mesenchymal tumor. The disease has few specific clinical symptoms and imaging manifestations, making its accurate diagnosis an intractable clinical challenge. This is a report of a female patient diagnosed with lesions and a mass in the left lobe of the liver. The computed tomography (CT) findings showed that the scan without a contrast agent had a slightly low density, and significant enhancement was seen in the arterial phase of the enhanced scan, with numerous tortuous arteries. The enhancement slightly decreased in the equilibrium phase and the delayed phase. The magnetic resonance imaging (MRI) findings were low signal for T1-weighted images (T1WI) and high signal for T2-weighted images (T2WI), and the enhancement pattern of the enhanced scan was similar to that of CT. Subsequently, the patient underwent surgical excision to remove the tumor. Based on the positive immunohistochemical staining for human melanoma black 45 (HMB45), smooth muscle actin (SMA), and melanin-A (Melan-A), a definitive diagnosis was made. Given that the pathological findings indicate low-grade malignancy, regular follow-up should be conducted. The patient presented with multiple fatty lesions in both kidneys, with the larger one located in the lower part of the left kidney, which was eventually confirmed as angiomyolipoma through surgical pathology. A literature review was carried out on the clinical features and imaging findings of the hepatic perivascular epithelioma, and cases with liver PEComa and kidney AML were described.
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spelling doaj-art-7e980f0778cc4aa5b47e360cd644aee32025-08-20T02:40:29ZengFrontiers Media S.A.Frontiers in Oncology2234-943X2025-06-011510.3389/fonc.2025.15342501534250Computed tomography and magnetic resonance imaging features of primary liver perivascular epithelioid cell tumor with renal angiomyolipoma: a case report and literature reviewRuoling GaoJiaying LiuQingdian CongZhilan HuangGuoping ZhuXuan JinJibo HuHepatic perivascular epithelioid cell tumor (PEComa) is an extremely rare mesenchymal tumor. The disease has few specific clinical symptoms and imaging manifestations, making its accurate diagnosis an intractable clinical challenge. This is a report of a female patient diagnosed with lesions and a mass in the left lobe of the liver. The computed tomography (CT) findings showed that the scan without a contrast agent had a slightly low density, and significant enhancement was seen in the arterial phase of the enhanced scan, with numerous tortuous arteries. The enhancement slightly decreased in the equilibrium phase and the delayed phase. The magnetic resonance imaging (MRI) findings were low signal for T1-weighted images (T1WI) and high signal for T2-weighted images (T2WI), and the enhancement pattern of the enhanced scan was similar to that of CT. Subsequently, the patient underwent surgical excision to remove the tumor. Based on the positive immunohistochemical staining for human melanoma black 45 (HMB45), smooth muscle actin (SMA), and melanin-A (Melan-A), a definitive diagnosis was made. Given that the pathological findings indicate low-grade malignancy, regular follow-up should be conducted. The patient presented with multiple fatty lesions in both kidneys, with the larger one located in the lower part of the left kidney, which was eventually confirmed as angiomyolipoma through surgical pathology. A literature review was carried out on the clinical features and imaging findings of the hepatic perivascular epithelioma, and cases with liver PEComa and kidney AML were described.https://www.frontiersin.org/articles/10.3389/fonc.2025.1534250/fullliverperivascular epithelioid cell tumorPEComarenal angiomyolipomaimaging manifestationsCT
spellingShingle Ruoling Gao
Jiaying Liu
Qingdian Cong
Zhilan Huang
Guoping Zhu
Xuan Jin
Jibo Hu
Computed tomography and magnetic resonance imaging features of primary liver perivascular epithelioid cell tumor with renal angiomyolipoma: a case report and literature review
Frontiers in Oncology
liver
perivascular epithelioid cell tumor
PEComa
renal angiomyolipoma
imaging manifestations
CT
title Computed tomography and magnetic resonance imaging features of primary liver perivascular epithelioid cell tumor with renal angiomyolipoma: a case report and literature review
title_full Computed tomography and magnetic resonance imaging features of primary liver perivascular epithelioid cell tumor with renal angiomyolipoma: a case report and literature review
title_fullStr Computed tomography and magnetic resonance imaging features of primary liver perivascular epithelioid cell tumor with renal angiomyolipoma: a case report and literature review
title_full_unstemmed Computed tomography and magnetic resonance imaging features of primary liver perivascular epithelioid cell tumor with renal angiomyolipoma: a case report and literature review
title_short Computed tomography and magnetic resonance imaging features of primary liver perivascular epithelioid cell tumor with renal angiomyolipoma: a case report and literature review
title_sort computed tomography and magnetic resonance imaging features of primary liver perivascular epithelioid cell tumor with renal angiomyolipoma a case report and literature review
topic liver
perivascular epithelioid cell tumor
PEComa
renal angiomyolipoma
imaging manifestations
CT
url https://www.frontiersin.org/articles/10.3389/fonc.2025.1534250/full
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