AXL and SRC in clear cell renal cell carcinoma: absence of mutations, rare alternative splicing events, but association of protein expression with poor prognosis

Abstract Novel treatment options for metastatic renal cell carcinomas (RCC) include specific MET inhibitors, GAS6/AXL inhibitors, and SRC inhibitors. The interplay between c‐MET, SRC, AXL expression, and their gene mutation patterns in different renal carcinoma subtypes is unclear. To improve the un...

Full description

Saved in:
Bibliographic Details
Main Authors: Muriel D Brada, Tülay Karakulak, Peter Schraml, Martina Haberecker, Dorothea Rutishauser, Jeffrey S Ross, Daniel Eberli, Holger Moch
Format: Article
Language:English
Published: Wiley 2025-05-01
Series:The Journal of Pathology: Clinical Research
Subjects:
Online Access:https://doi.org/10.1002/2056-4538.70028
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1849325507006431232
author Muriel D Brada
Tülay Karakulak
Peter Schraml
Martina Haberecker
Dorothea Rutishauser
Jeffrey S Ross
Daniel Eberli
Holger Moch
author_facet Muriel D Brada
Tülay Karakulak
Peter Schraml
Martina Haberecker
Dorothea Rutishauser
Jeffrey S Ross
Daniel Eberli
Holger Moch
author_sort Muriel D Brada
collection DOAJ
description Abstract Novel treatment options for metastatic renal cell carcinomas (RCC) include specific MET inhibitors, GAS6/AXL inhibitors, and SRC inhibitors. The interplay between c‐MET, SRC, AXL expression, and their gene mutation patterns in different renal carcinoma subtypes is unclear. To improve the understanding of these signaling pathways, we analyzed c‐MET, AXL, and SRC expression in 590 clear cell RCC (ccRCC) and 127 papillary RCC (pRCC) by immunohistochemistry and integrated sequencing data to investigate the frequency of MET, AXL, and SRC gene mutations, their expression levels, and the presence of splice variants. In TCGA and in Foundation Medicine, Inc. (FMI) datasets, AXL and SRC gene alterations were extremely rare (<2%) or absent in ccRCC (n = 531 and 2,781, respectively) and pRCC (n = 290 and 566, respectively). On the other hand, MET mutations or amplifications were found in 9.7% (TCGA) and 10.2% (FMI) of pRCC. We show that strong SRC staining intensity by immunohistochemistry is associated with high tumor stage, high grade, and shorter survival in ccRCC (p < 0.001 each). AXL expression correlates with high stage and grade in ccRCC (p < 0.001 each). Both SRC and AXL expression were independent prognostic parameters in multivariate analysis (p < 0.05). MET expression is associated with longer survival in pRCC (p < 0.05). Our TCGA data analysis aligns with SRC immunohistochemistry findings on tumor stage and shorter survival in ccRCC. TCGA expression data showed a moderate positive correlation between AXL and c‐MET in pRCC. In addition, we identified alternative splicing events reported for AXL in pRCC, and MET and SRC in ccRCC, across various alternative splicing databases. In conclusion, we identified high SRC expression as a biomarker for poor prognosis of ccRCC. Our data demonstrate c‐MET, AXL, and SRC signaling pathway interactions independent of c‐MET, AXL, and SRC mutations in ccRCC.
format Article
id doaj-art-7e92da4e6c534064a3f6a0a47aa4435c
institution Kabale University
issn 2056-4538
language English
publishDate 2025-05-01
publisher Wiley
record_format Article
series The Journal of Pathology: Clinical Research
spelling doaj-art-7e92da4e6c534064a3f6a0a47aa4435c2025-08-20T03:48:23ZengWileyThe Journal of Pathology: Clinical Research2056-45382025-05-01113n/an/a10.1002/2056-4538.70028AXL and SRC in clear cell renal cell carcinoma: absence of mutations, rare alternative splicing events, but association of protein expression with poor prognosisMuriel D Brada0Tülay Karakulak1Peter Schraml2Martina Haberecker3Dorothea Rutishauser4Jeffrey S Ross5Daniel Eberli6Holger Moch7Department of Pathology and Molecular Pathology University Hospital Zurich Zurich SwitzerlandDepartment of Pathology and Molecular Pathology University Hospital Zurich Zurich SwitzerlandDepartment of Pathology and Molecular Pathology University Hospital Zurich Zurich SwitzerlandDepartment of Pathology and Molecular Pathology University Hospital Zurich Zurich SwitzerlandDepartment of Pathology and Molecular Pathology University Hospital Zurich Zurich SwitzerlandFoundation Medicine, Inc. Cambridge MA USADepartment of Urology University Hospital Zurich Zurich SwitzerlandDepartment of Pathology and Molecular Pathology University Hospital Zurich Zurich SwitzerlandAbstract Novel treatment options for metastatic renal cell carcinomas (RCC) include specific MET inhibitors, GAS6/AXL inhibitors, and SRC inhibitors. The interplay between c‐MET, SRC, AXL expression, and their gene mutation patterns in different renal carcinoma subtypes is unclear. To improve the understanding of these signaling pathways, we analyzed c‐MET, AXL, and SRC expression in 590 clear cell RCC (ccRCC) and 127 papillary RCC (pRCC) by immunohistochemistry and integrated sequencing data to investigate the frequency of MET, AXL, and SRC gene mutations, their expression levels, and the presence of splice variants. In TCGA and in Foundation Medicine, Inc. (FMI) datasets, AXL and SRC gene alterations were extremely rare (<2%) or absent in ccRCC (n = 531 and 2,781, respectively) and pRCC (n = 290 and 566, respectively). On the other hand, MET mutations or amplifications were found in 9.7% (TCGA) and 10.2% (FMI) of pRCC. We show that strong SRC staining intensity by immunohistochemistry is associated with high tumor stage, high grade, and shorter survival in ccRCC (p < 0.001 each). AXL expression correlates with high stage and grade in ccRCC (p < 0.001 each). Both SRC and AXL expression were independent prognostic parameters in multivariate analysis (p < 0.05). MET expression is associated with longer survival in pRCC (p < 0.05). Our TCGA data analysis aligns with SRC immunohistochemistry findings on tumor stage and shorter survival in ccRCC. TCGA expression data showed a moderate positive correlation between AXL and c‐MET in pRCC. In addition, we identified alternative splicing events reported for AXL in pRCC, and MET and SRC in ccRCC, across various alternative splicing databases. In conclusion, we identified high SRC expression as a biomarker for poor prognosis of ccRCC. Our data demonstrate c‐MET, AXL, and SRC signaling pathway interactions independent of c‐MET, AXL, and SRC mutations in ccRCC.https://doi.org/10.1002/2056-4538.70028renal cell carcinomagene expressiontyrosine kinase inhibitor
spellingShingle Muriel D Brada
Tülay Karakulak
Peter Schraml
Martina Haberecker
Dorothea Rutishauser
Jeffrey S Ross
Daniel Eberli
Holger Moch
AXL and SRC in clear cell renal cell carcinoma: absence of mutations, rare alternative splicing events, but association of protein expression with poor prognosis
The Journal of Pathology: Clinical Research
renal cell carcinoma
gene expression
tyrosine kinase inhibitor
title AXL and SRC in clear cell renal cell carcinoma: absence of mutations, rare alternative splicing events, but association of protein expression with poor prognosis
title_full AXL and SRC in clear cell renal cell carcinoma: absence of mutations, rare alternative splicing events, but association of protein expression with poor prognosis
title_fullStr AXL and SRC in clear cell renal cell carcinoma: absence of mutations, rare alternative splicing events, but association of protein expression with poor prognosis
title_full_unstemmed AXL and SRC in clear cell renal cell carcinoma: absence of mutations, rare alternative splicing events, but association of protein expression with poor prognosis
title_short AXL and SRC in clear cell renal cell carcinoma: absence of mutations, rare alternative splicing events, but association of protein expression with poor prognosis
title_sort axl and src in clear cell renal cell carcinoma absence of mutations rare alternative splicing events but association of protein expression with poor prognosis
topic renal cell carcinoma
gene expression
tyrosine kinase inhibitor
url https://doi.org/10.1002/2056-4538.70028
work_keys_str_mv AT murieldbrada axlandsrcinclearcellrenalcellcarcinomaabsenceofmutationsrarealternativesplicingeventsbutassociationofproteinexpressionwithpoorprognosis
AT tulaykarakulak axlandsrcinclearcellrenalcellcarcinomaabsenceofmutationsrarealternativesplicingeventsbutassociationofproteinexpressionwithpoorprognosis
AT peterschraml axlandsrcinclearcellrenalcellcarcinomaabsenceofmutationsrarealternativesplicingeventsbutassociationofproteinexpressionwithpoorprognosis
AT martinahaberecker axlandsrcinclearcellrenalcellcarcinomaabsenceofmutationsrarealternativesplicingeventsbutassociationofproteinexpressionwithpoorprognosis
AT dorothearutishauser axlandsrcinclearcellrenalcellcarcinomaabsenceofmutationsrarealternativesplicingeventsbutassociationofproteinexpressionwithpoorprognosis
AT jeffreysross axlandsrcinclearcellrenalcellcarcinomaabsenceofmutationsrarealternativesplicingeventsbutassociationofproteinexpressionwithpoorprognosis
AT danieleberli axlandsrcinclearcellrenalcellcarcinomaabsenceofmutationsrarealternativesplicingeventsbutassociationofproteinexpressionwithpoorprognosis
AT holgermoch axlandsrcinclearcellrenalcellcarcinomaabsenceofmutationsrarealternativesplicingeventsbutassociationofproteinexpressionwithpoorprognosis