Median Mandibular Cleft in SAMS Syndrome – A Rare Case Report
Rationale: SAMS syndrome is a rare genetic disorder characterized by midline facial clefting, skeletal anomalies, and other defects. Salient Features: Among the craniofacial manifestations of SAMS syndrome is the presence of a median mandibular cleft (MMC). MMC is a rare occurrence and in this syndr...
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| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Wolters Kluwer Medknow Publications
2023-04-01
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| Series: | Indian Journal of Dental Research |
| Subjects: | |
| Online Access: | https://journals.lww.com/10.4103/ijdr.ijdr_461_23 |
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| Summary: | Rationale:
SAMS syndrome is a rare genetic disorder characterized by midline facial clefting, skeletal anomalies, and other defects.
Salient Features:
Among the craniofacial manifestations of SAMS syndrome is the presence of a median mandibular cleft (MMC). MMC is a rare occurrence and in this syndrome, it poses a complex challenge for both functional and aesthetic reasons. Patient
Findings:
This rare case report describes the successful correction of an MMC in an 18-month-old child diagnosed with SAMS syndrome.
Treatment:
This report describes the presentation, diagnosis and treatment. The surgical intervention involved a meticulous, single stage, osseous reconstruction. The mechanism of MMC in SAMS syndrome is discussed.
Outcomes:
Early intervention for MMC in SAMS syndrome patients can offer promising outcomes. |
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| ISSN: | 0970-9290 1998-3603 |