Progressive demyelinating childhood cerebral adrenoleukodystrophy : Assessment of communication impairment

Adrenoleukodystrophy (ALD) is a rare demyelinating genetic disorder occurring due to mutation in the gene ABCD1. The current case study involved detailed evaluation of communication skills including audiological and speech-language evaluations of a 6 year old diagnosed with ALD. The child evidenced...

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Main Authors: Mangal Chandra Yadav, Bhavani Venkatachalam, Akshay Parmar, M. Aparna Krishnan, Reheema Thasli, Sachchidanand Sinha
Format: Article
Language:English
Published: Elsevier 2024-01-01
Series:Rare
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2950008724000127
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author Mangal Chandra Yadav
Bhavani Venkatachalam
Akshay Parmar
M. Aparna Krishnan
Reheema Thasli
Sachchidanand Sinha
author_facet Mangal Chandra Yadav
Bhavani Venkatachalam
Akshay Parmar
M. Aparna Krishnan
Reheema Thasli
Sachchidanand Sinha
author_sort Mangal Chandra Yadav
collection DOAJ
description Adrenoleukodystrophy (ALD) is a rare demyelinating genetic disorder occurring due to mutation in the gene ABCD1. The current case study involved detailed evaluation of communication skills including audiological and speech-language evaluations of a 6 year old diagnosed with ALD. The child evidenced severely restricted communication skills along with several other subsystems affected.
format Article
id doaj-art-7cdbf5d40fcc4852a5cb0c3dde389c28
institution DOAJ
issn 2950-0087
language English
publishDate 2024-01-01
publisher Elsevier
record_format Article
series Rare
spelling doaj-art-7cdbf5d40fcc4852a5cb0c3dde389c282025-08-20T02:49:02ZengElsevierRare2950-00872024-01-01210002910.1016/j.rare.2024.100029Progressive demyelinating childhood cerebral adrenoleukodystrophy : Assessment of communication impairmentMangal Chandra Yadav0Bhavani Venkatachalam1Akshay Parmar2M. Aparna Krishnan3Reheema Thasli4Sachchidanand Sinha5Department of ENT, All India Institute of Medical Sciences, Rishikesh, India; Corresponding author.Department of Speech Language Pathology, All India Institute of Speech and Hearing, Mysuru, IndiaDepartment of Audiology, All India Institute of Speech and Hearing, Mysuru, IndiaUniversity of Queensland Australia, AustraliaDepartment of Audiology, All India Institute of Speech and Hearing, Mysuru, IndiaPandit Jawaharlal Nehru Memorial Medical College, Raipur, IndiaAdrenoleukodystrophy (ALD) is a rare demyelinating genetic disorder occurring due to mutation in the gene ABCD1. The current case study involved detailed evaluation of communication skills including audiological and speech-language evaluations of a 6 year old diagnosed with ALD. The child evidenced severely restricted communication skills along with several other subsystems affected.http://www.sciencedirect.com/science/article/pii/S2950008724000127AdrenoleukodystrophyCommunicationHearing impairmentSpeech and languageALD
spellingShingle Mangal Chandra Yadav
Bhavani Venkatachalam
Akshay Parmar
M. Aparna Krishnan
Reheema Thasli
Sachchidanand Sinha
Progressive demyelinating childhood cerebral adrenoleukodystrophy : Assessment of communication impairment
Rare
Adrenoleukodystrophy
Communication
Hearing impairment
Speech and language
ALD
title Progressive demyelinating childhood cerebral adrenoleukodystrophy : Assessment of communication impairment
title_full Progressive demyelinating childhood cerebral adrenoleukodystrophy : Assessment of communication impairment
title_fullStr Progressive demyelinating childhood cerebral adrenoleukodystrophy : Assessment of communication impairment
title_full_unstemmed Progressive demyelinating childhood cerebral adrenoleukodystrophy : Assessment of communication impairment
title_short Progressive demyelinating childhood cerebral adrenoleukodystrophy : Assessment of communication impairment
title_sort progressive demyelinating childhood cerebral adrenoleukodystrophy assessment of communication impairment
topic Adrenoleukodystrophy
Communication
Hearing impairment
Speech and language
ALD
url http://www.sciencedirect.com/science/article/pii/S2950008724000127
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