Gastrointestinal stromal tumors: advances in molecular characterization and therapeutic implications

Recognition of the molecular basis of gastrointestinal stromal tumors has paved the way for significant breakthroughs in the diagnosis and treatment of this disease as well as positioned gastrointestinal stromal tumors as a framework for the concept of precision oncology in solid tumors. The incorpo...

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Main Authors: Nildevande Firmino Lima-Jr, Marcello Moro Queiroz, Julia Sousa Leal Franco, Domingos Savio do Rego Lins-Junior, Eduardo Felício de Campos, Beatriz Mendes Awni, Luiz Guilherme Cernaglia Aureliano de Lima, Frederico Teixeira, Fábio de Oliveira Ferreira, Eduardo Hiroshi Akaishi, Fernanda Cunha Capareli, Rodrigo Ramella Munhoz
Format: Article
Language:English
Published: Thieme Revinter Publicações Ltda. 2024-05-01
Series:Brazilian Journal of Oncology
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Online Access:https://www.brazilianjournalofoncology.com.br/details/278/en-US/gastrointestinal-stromal-tumors--advances-in-molecular-characterization-and-therapeutic-implications
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author Nildevande Firmino Lima-Jr
Marcello Moro Queiroz
Julia Sousa Leal Franco
Domingos Savio do Rego Lins-Junior
Eduardo Felício de Campos
Beatriz Mendes Awni
Luiz Guilherme Cernaglia Aureliano de Lima
Frederico Teixeira
Fábio de Oliveira Ferreira
Eduardo Hiroshi Akaishi
Fernanda Cunha Capareli
Rodrigo Ramella Munhoz
author_facet Nildevande Firmino Lima-Jr
Marcello Moro Queiroz
Julia Sousa Leal Franco
Domingos Savio do Rego Lins-Junior
Eduardo Felício de Campos
Beatriz Mendes Awni
Luiz Guilherme Cernaglia Aureliano de Lima
Frederico Teixeira
Fábio de Oliveira Ferreira
Eduardo Hiroshi Akaishi
Fernanda Cunha Capareli
Rodrigo Ramella Munhoz
author_sort Nildevande Firmino Lima-Jr
collection DOAJ
description Recognition of the molecular basis of gastrointestinal stromal tumors has paved the way for significant breakthroughs in the diagnosis and treatment of this disease as well as positioned gastrointestinal stromal tumors as a framework for the concept of precision oncology in solid tumors. The incorporation of novel targeted agents for molecularly defined subgroups has led to significant improvements in treatment outcomes; however, the characterization of heterogeneous KIT or PDGFRA mutations and the emergence of resistance mechanisms highlight the need for a broader use of comprehensive molecular profiling and emphasize the importance of molecularly driven adaptive treatment strategies. Such a molecular background is critical for developing personalized and effective interventions and optimizing outcomes. The present review summarizes key studies that provide the basis for standard-of-care management options as well as provides molecular insights into the management of gastrointestinal stromal tumors, with an emphasis on recent advances.
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institution Kabale University
issn 2526-8732
language English
publishDate 2024-05-01
publisher Thieme Revinter Publicações Ltda.
record_format Article
series Brazilian Journal of Oncology
spelling doaj-art-7b4c4e8796894a1da09e29d39411e70c2025-08-20T03:35:03ZengThieme Revinter Publicações Ltda.Brazilian Journal of Oncology2526-87322024-05-012010.5935/2526-8732.20240468Gastrointestinal stromal tumors: advances in molecular characterization and therapeutic implicationsNildevande Firmino Lima-Jr0Marcello Moro Queiroz1Julia Sousa Leal Franco2Domingos Savio do Rego Lins-Junior3Eduardo Felício de Campos4Beatriz Mendes Awni5Luiz Guilherme Cernaglia Aureliano de Lima6Frederico Teixeira7Fábio de Oliveira Ferreira8Eduardo Hiroshi Akaishi9Fernanda Cunha Capareli10Rodrigo Ramella Munhoz11Hospital Sirio Libanês, Oncologia Clínica - São Paulo - SP - BrazilHospital Sirio Libanês, Oncologia Clínica - São Paulo - SP - BrazilHospital Sirio Libanês, Oncologia Clínica - São Paulo - SP - BrazilHospital Sirio Libanês, Oncologia Clínica - São Paulo - SP - BrazilHospital Sirio Libanês, Oncologia Clínica - São Paulo - SP - BrazilHospital Sirio Libanês, Oncologia Clínica - São Paulo - SP - BrazilHospital Sirio Libanês, Oncologia Clínica - São Paulo - SP - BrazilHospital Sirio Libanês, Oncologia Clínica - São Paulo - SP - BrazilHospital Sirio Libanês, Oncologia Clínica - São Paulo - SP - BrazilHospital Sirio Libanês, Oncologia Clínica - São Paulo - SP - BrazilHospital Sirio Libanês, Oncologia Clínica - São Paulo - SP - BrazilHospital Sirio Libanês, Oncologia Clínica - São Paulo - SP - BrazilRecognition of the molecular basis of gastrointestinal stromal tumors has paved the way for significant breakthroughs in the diagnosis and treatment of this disease as well as positioned gastrointestinal stromal tumors as a framework for the concept of precision oncology in solid tumors. The incorporation of novel targeted agents for molecularly defined subgroups has led to significant improvements in treatment outcomes; however, the characterization of heterogeneous KIT or PDGFRA mutations and the emergence of resistance mechanisms highlight the need for a broader use of comprehensive molecular profiling and emphasize the importance of molecularly driven adaptive treatment strategies. Such a molecular background is critical for developing personalized and effective interventions and optimizing outcomes. The present review summarizes key studies that provide the basis for standard-of-care management options as well as provides molecular insights into the management of gastrointestinal stromal tumors, with an emphasis on recent advances.https://www.brazilianjournalofoncology.com.br/details/278/en-US/gastrointestinal-stromal-tumors--advances-in-molecular-characterization-and-therapeutic-implicationsgastrointestinal stromal tumorssarcomatyrosine kinase inhibitorsproto-oncogene proteins c-kitplatelet-derived growth factor
spellingShingle Nildevande Firmino Lima-Jr
Marcello Moro Queiroz
Julia Sousa Leal Franco
Domingos Savio do Rego Lins-Junior
Eduardo Felício de Campos
Beatriz Mendes Awni
Luiz Guilherme Cernaglia Aureliano de Lima
Frederico Teixeira
Fábio de Oliveira Ferreira
Eduardo Hiroshi Akaishi
Fernanda Cunha Capareli
Rodrigo Ramella Munhoz
Gastrointestinal stromal tumors: advances in molecular characterization and therapeutic implications
Brazilian Journal of Oncology
gastrointestinal stromal tumors
sarcoma
tyrosine kinase inhibitors
proto-oncogene proteins c-kit
platelet-derived growth factor
title Gastrointestinal stromal tumors: advances in molecular characterization and therapeutic implications
title_full Gastrointestinal stromal tumors: advances in molecular characterization and therapeutic implications
title_fullStr Gastrointestinal stromal tumors: advances in molecular characterization and therapeutic implications
title_full_unstemmed Gastrointestinal stromal tumors: advances in molecular characterization and therapeutic implications
title_short Gastrointestinal stromal tumors: advances in molecular characterization and therapeutic implications
title_sort gastrointestinal stromal tumors advances in molecular characterization and therapeutic implications
topic gastrointestinal stromal tumors
sarcoma
tyrosine kinase inhibitors
proto-oncogene proteins c-kit
platelet-derived growth factor
url https://www.brazilianjournalofoncology.com.br/details/278/en-US/gastrointestinal-stromal-tumors--advances-in-molecular-characterization-and-therapeutic-implications
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