Clinical and genetic characteristics of Nonaka myopathy (GNE-myopathy) in russian patients

Clinical and genetic characteristics of 9patients with Nonaka myopathy (GNE-myopathy) from Russia are presented. As a result of exom sequencing, 11 different mutations were revealed in the GNE gene, 8 of which were described earlier, and 3 – Сys203Ser, Met263CysfsTer and deletion of the whole gene —...

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Main Authors: E. L. Dadali, I. V. Sharkova, G. E. Rudenskaya, S. S. Nikitin, A. F. Murtazina, O. P. Ryzhkova, A. L. Chukhrova
Format: Article
Language:Russian
Published: ABV-press 2019-11-01
Series:Нервно-мышечные болезни
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Online Access:https://nmb.abvpress.ru/jour/article/view/344
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author E. L. Dadali
I. V. Sharkova
G. E. Rudenskaya
S. S. Nikitin
A. F. Murtazina
O. P. Ryzhkova
A. L. Chukhrova
author_facet E. L. Dadali
I. V. Sharkova
G. E. Rudenskaya
S. S. Nikitin
A. F. Murtazina
O. P. Ryzhkova
A. L. Chukhrova
author_sort E. L. Dadali
collection DOAJ
description Clinical and genetic characteristics of 9patients with Nonaka myopathy (GNE-myopathy) from Russia are presented. As a result of exom sequencing, 11 different mutations were revealed in the GNE gene, 8 of which were described earlier, and 3 – Сys203Ser, Met263CysfsTer and deletion of the whole gene — were detected for the first time. The peculiarities of clinical manifestation of Russian patients with GNE-myopathy are described.
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publishDate 2019-11-01
publisher ABV-press
record_format Article
series Нервно-мышечные болезни
spelling doaj-art-7ad99b2c7a094c959bb1285c35eed8532025-08-20T03:00:39ZrusABV-pressНервно-мышечные болезни2222-87212413-04432019-11-0193566610.17650/2222-8721-2019-9-3-56-66247Clinical and genetic characteristics of Nonaka myopathy (GNE-myopathy) in russian patientsE. L. Dadali0I. V. Sharkova1G. E. Rudenskaya2S. S. Nikitin3A. F. Murtazina4O. P. Ryzhkova5A. L. Chukhrova6Reseasrch Center of Medical Genetics; Pirogov Russian National Research Medical University, Ministry of Health of RussiaReseasrch Center of Medical GeneticsReseasrch Center of Medical GeneticsAssociation of Neuromuscular Disorders Specialists, Medical Center “Practical Neurology”Reseasrch Center of Medical Genetics; Association of Neuromuscular Disorders Specialists, Medical Center “Practical Neurology”Reseasrch Center of Medical GeneticsReseasrch Center of Medical GeneticsClinical and genetic characteristics of 9patients with Nonaka myopathy (GNE-myopathy) from Russia are presented. As a result of exom sequencing, 11 different mutations were revealed in the GNE gene, 8 of which were described earlier, and 3 – Сys203Ser, Met263CysfsTer and deletion of the whole gene — were detected for the first time. The peculiarities of clinical manifestation of Russian patients with GNE-myopathy are described.https://nmb.abvpress.ru/jour/article/view/344nonaka myopathygne genegne-myopathiesomim:605820
spellingShingle E. L. Dadali
I. V. Sharkova
G. E. Rudenskaya
S. S. Nikitin
A. F. Murtazina
O. P. Ryzhkova
A. L. Chukhrova
Clinical and genetic characteristics of Nonaka myopathy (GNE-myopathy) in russian patients
Нервно-мышечные болезни
nonaka myopathy
gne gene
gne-myopathies
omim:605820
title Clinical and genetic characteristics of Nonaka myopathy (GNE-myopathy) in russian patients
title_full Clinical and genetic characteristics of Nonaka myopathy (GNE-myopathy) in russian patients
title_fullStr Clinical and genetic characteristics of Nonaka myopathy (GNE-myopathy) in russian patients
title_full_unstemmed Clinical and genetic characteristics of Nonaka myopathy (GNE-myopathy) in russian patients
title_short Clinical and genetic characteristics of Nonaka myopathy (GNE-myopathy) in russian patients
title_sort clinical and genetic characteristics of nonaka myopathy gne myopathy in russian patients
topic nonaka myopathy
gne gene
gne-myopathies
omim:605820
url https://nmb.abvpress.ru/jour/article/view/344
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