A Case of Noncompaction at All Segments of Both Right and Left Ventricles

Background. Noncompaction/hypertrabeculation left ventricle (NCM/HVM) is most commonly reported in one or more segments of left ventricle and sometimes both ventricles. In this case, we present noncompaction of all segments of right and left ventricle, in a young man with mental retardation. Case Pr...

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Main Authors: Ali Pourmoghaddas, Reihaneh Zavar, Mohaddeseh Behjati
Format: Article
Language:English
Published: Wiley 2014-01-01
Series:Case Reports in Cardiology
Online Access:http://dx.doi.org/10.1155/2014/325257
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author Ali Pourmoghaddas
Reihaneh Zavar
Mohaddeseh Behjati
author_facet Ali Pourmoghaddas
Reihaneh Zavar
Mohaddeseh Behjati
author_sort Ali Pourmoghaddas
collection DOAJ
description Background. Noncompaction/hypertrabeculation left ventricle (NCM/HVM) is most commonly reported in one or more segments of left ventricle and sometimes both ventricles. In this case, we present noncompaction of all segments of right and left ventricle, in a young man with mental retardation. Case Presentation. A 19-year-old male was referred to us with sudden dyspnea at rest and chest discomfort. He was a known case of mental retardation. He was born full term with birth weight = 1250 grams. On physical examination. A systolic murmur (II/VI) at left sternal border was heard. ECG showed increased voltage in precordial lead and deep ST segment depression. Chest X-ray (CXR) was within normal limits. Transthoracic echocardiography showed situs solitus, D loop, normal connection of great vessels, noncompaction LV at all segments (noncompaction/compaction = 2.5/0.5) with moderate systolic dysfunction (LVEF = 40%), diastolic dysfunction grade II, normal RV size with mild systolic dysfunction and hypertrabeculation, mild tricuspid regurgitation (TR), and normal pulmonary artery systolic pressure. After injection of agitated saline some bubbles were passed from right to left through patent foramen oval (PFO). Conclusions. Extensive sinusoid formation and trabeculation of RV and nearby all LV segments and its association with mental retardation suggest presence of strong genetic background.
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spelling doaj-art-787403c76f614b2786f2bfa0d6e5b12b2025-02-03T07:25:34ZengWileyCase Reports in Cardiology2090-64042090-64122014-01-01201410.1155/2014/325257325257A Case of Noncompaction at All Segments of Both Right and Left VentriclesAli Pourmoghaddas0Reihaneh Zavar1Mohaddeseh Behjati2Cardiology, Isfahan University of Medical Sciences, Isfahan, IranCardiology, Isfahan University of Medical Sciences, Isfahan, IranHeart Failure Research Center, Cardiovascular Research Center, Cardiovascular Research Institute, Isfahan University of Medical Sciences, Isfahan, IranBackground. Noncompaction/hypertrabeculation left ventricle (NCM/HVM) is most commonly reported in one or more segments of left ventricle and sometimes both ventricles. In this case, we present noncompaction of all segments of right and left ventricle, in a young man with mental retardation. Case Presentation. A 19-year-old male was referred to us with sudden dyspnea at rest and chest discomfort. He was a known case of mental retardation. He was born full term with birth weight = 1250 grams. On physical examination. A systolic murmur (II/VI) at left sternal border was heard. ECG showed increased voltage in precordial lead and deep ST segment depression. Chest X-ray (CXR) was within normal limits. Transthoracic echocardiography showed situs solitus, D loop, normal connection of great vessels, noncompaction LV at all segments (noncompaction/compaction = 2.5/0.5) with moderate systolic dysfunction (LVEF = 40%), diastolic dysfunction grade II, normal RV size with mild systolic dysfunction and hypertrabeculation, mild tricuspid regurgitation (TR), and normal pulmonary artery systolic pressure. After injection of agitated saline some bubbles were passed from right to left through patent foramen oval (PFO). Conclusions. Extensive sinusoid formation and trabeculation of RV and nearby all LV segments and its association with mental retardation suggest presence of strong genetic background.http://dx.doi.org/10.1155/2014/325257
spellingShingle Ali Pourmoghaddas
Reihaneh Zavar
Mohaddeseh Behjati
A Case of Noncompaction at All Segments of Both Right and Left Ventricles
Case Reports in Cardiology
title A Case of Noncompaction at All Segments of Both Right and Left Ventricles
title_full A Case of Noncompaction at All Segments of Both Right and Left Ventricles
title_fullStr A Case of Noncompaction at All Segments of Both Right and Left Ventricles
title_full_unstemmed A Case of Noncompaction at All Segments of Both Right and Left Ventricles
title_short A Case of Noncompaction at All Segments of Both Right and Left Ventricles
title_sort case of noncompaction at all segments of both right and left ventricles
url http://dx.doi.org/10.1155/2014/325257
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