SHERESHEVSKY-TURNER SYNDROME IN AORTIC SURGERY: AN EXAMPLE OF HYBRID ANEURISM TREATMENT AND DISSECTION OF THORACOABDOMINAL AORTA
Shereshevsky-Turner syndrome — is chromosome anomaly, the monosomia by X-chromosome (cariotype 45, X0) that has prevalence 1:2000-1:2500 newborn girls. It is well known that these patients very often have cardiovascular pathology. Aortic aneurysm is 100 times more common than in general population....
Saved in:
| Main Authors: | , , , , , , , , , |
|---|---|
| Format: | Article |
| Language: | Russian |
| Published: |
«FIRMA «SILICEA» LLC
2015-05-01
|
| Series: | Российский кардиологический журнал |
| Subjects: | |
| Online Access: | https://russjcardiol.elpub.ru/jour/article/view/329 |
| Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
| _version_ | 1849410273451966464 |
|---|---|
| author | E. R. Tchartchan S. A. Abugov R. S. Polyakov E. V. Zaklyazminskaya V. A. Rumyantseva V. V. Khovrin A. A. Skvortsov M. N. Kabanova Z. R. Khatchatryan N. V. Oparina |
| author_facet | E. R. Tchartchan S. A. Abugov R. S. Polyakov E. V. Zaklyazminskaya V. A. Rumyantseva V. V. Khovrin A. A. Skvortsov M. N. Kabanova Z. R. Khatchatryan N. V. Oparina |
| author_sort | E. R. Tchartchan |
| collection | DOAJ |
| description | Shereshevsky-Turner syndrome — is chromosome anomaly, the monosomia by X-chromosome (cariotype 45, X0) that has prevalence 1:2000-1:2500 newborn girls. It is well known that these patients very often have cardiovascular pathology. Aortic aneurysm is 100 times more common than in general population. Another significant specifics is the high risk of aortic dissection even with relatively small diameter of aorta, than in average for the dissections. Currently it is common to concern a variety of aortic pathology treatment ways in patients with the syndrome: traditional open-chest interventions, endovascular treatment, hybrid operations. The article provides an example of successful usage of the hybrid method in women 58 years old with Shereshevsky-Turner syndrome, thoracoabdominal aortic aneurysm and dissection of descending thoracal and abdominal aorta parts. The clinical example shows that hybrid method makes it to perform radical intervention on aorta, decreasing traumaticity of operation, mortality and complications rate in postoperation period. |
| format | Article |
| id | doaj-art-78475614e8c94c5ea737b40181d12b05 |
| institution | Kabale University |
| issn | 1560-4071 2618-7620 |
| language | Russian |
| publishDate | 2015-05-01 |
| publisher | «FIRMA «SILICEA» LLC |
| record_format | Article |
| series | Российский кардиологический журнал |
| spelling | doaj-art-78475614e8c94c5ea737b40181d12b052025-08-20T03:35:11Zrus«FIRMA «SILICEA» LLCРоссийский кардиологический журнал1560-40712618-76202015-05-010511111710.15829/1560-4071-2015-5-111-117329SHERESHEVSKY-TURNER SYNDROME IN AORTIC SURGERY: AN EXAMPLE OF HYBRID ANEURISM TREATMENT AND DISSECTION OF THORACOABDOMINAL AORTAE. R. Tchartchan0S. A. Abugov1R. S. Polyakov2E. V. Zaklyazminskaya3V. A. Rumyantseva4V. V. Khovrin5A. A. Skvortsov6M. N. Kabanova7Z. R. Khatchatryan8N. V. Oparina9FSBSI Russian Scientific Center for Surgery n.a. Petrovsky B. P., MoscowFSBSI Russian Scientific Center for Surgery n.a. Petrovsky B. P., Moscow; SBEI Additional Professional Education of Russian Medical Academy of Postdiploma Education, Moscow, Russia.FSBSI Russian Scientific Center for Surgery n.a. Petrovsky B. P., Moscow; SBEI Additional Professional Education of Russian Medical Academy of Postdiploma Education, Moscow, Russia.FSBSI Russian Scientific Center for Surgery n.a. Petrovsky B. P., MoscowFSBSI Russian Scientific Center for Surgery n.a. Petrovsky B. P., MoscowFSBSI Russian Scientific Center for Surgery n.a. Petrovsky B. P., MoscowFSBSI Russian Scientific Center for Surgery n.a. Petrovsky B. P., MoscowFSBSI Russian Scientific Center for Surgery n.a. Petrovsky B. P., MoscowFSBSI Russian Scientific Center for Surgery n.a. Petrovsky B. P., MoscowFSBSI Russian Scientific Center for Surgery n.a. Petrovsky B. P., MoscowShereshevsky-Turner syndrome — is chromosome anomaly, the monosomia by X-chromosome (cariotype 45, X0) that has prevalence 1:2000-1:2500 newborn girls. It is well known that these patients very often have cardiovascular pathology. Aortic aneurysm is 100 times more common than in general population. Another significant specifics is the high risk of aortic dissection even with relatively small diameter of aorta, than in average for the dissections. Currently it is common to concern a variety of aortic pathology treatment ways in patients with the syndrome: traditional open-chest interventions, endovascular treatment, hybrid operations. The article provides an example of successful usage of the hybrid method in women 58 years old with Shereshevsky-Turner syndrome, thoracoabdominal aortic aneurysm and dissection of descending thoracal and abdominal aorta parts. The clinical example shows that hybrid method makes it to perform radical intervention on aorta, decreasing traumaticity of operation, mortality and complications rate in postoperation period.https://russjcardiol.elpub.ru/jour/article/view/329shereshevsky-turner syndromehybrid operationsvisceral de-branching. |
| spellingShingle | E. R. Tchartchan S. A. Abugov R. S. Polyakov E. V. Zaklyazminskaya V. A. Rumyantseva V. V. Khovrin A. A. Skvortsov M. N. Kabanova Z. R. Khatchatryan N. V. Oparina SHERESHEVSKY-TURNER SYNDROME IN AORTIC SURGERY: AN EXAMPLE OF HYBRID ANEURISM TREATMENT AND DISSECTION OF THORACOABDOMINAL AORTA Российский кардиологический журнал shereshevsky-turner syndrome hybrid operations visceral de-branching. |
| title | SHERESHEVSKY-TURNER SYNDROME IN AORTIC SURGERY: AN EXAMPLE OF HYBRID ANEURISM TREATMENT AND DISSECTION OF THORACOABDOMINAL AORTA |
| title_full | SHERESHEVSKY-TURNER SYNDROME IN AORTIC SURGERY: AN EXAMPLE OF HYBRID ANEURISM TREATMENT AND DISSECTION OF THORACOABDOMINAL AORTA |
| title_fullStr | SHERESHEVSKY-TURNER SYNDROME IN AORTIC SURGERY: AN EXAMPLE OF HYBRID ANEURISM TREATMENT AND DISSECTION OF THORACOABDOMINAL AORTA |
| title_full_unstemmed | SHERESHEVSKY-TURNER SYNDROME IN AORTIC SURGERY: AN EXAMPLE OF HYBRID ANEURISM TREATMENT AND DISSECTION OF THORACOABDOMINAL AORTA |
| title_short | SHERESHEVSKY-TURNER SYNDROME IN AORTIC SURGERY: AN EXAMPLE OF HYBRID ANEURISM TREATMENT AND DISSECTION OF THORACOABDOMINAL AORTA |
| title_sort | shereshevsky turner syndrome in aortic surgery an example of hybrid aneurism treatment and dissection of thoracoabdominal aorta |
| topic | shereshevsky-turner syndrome hybrid operations visceral de-branching. |
| url | https://russjcardiol.elpub.ru/jour/article/view/329 |
| work_keys_str_mv | AT ertchartchan shereshevskyturnersyndromeinaorticsurgeryanexampleofhybridaneurismtreatmentanddissectionofthoracoabdominalaorta AT saabugov shereshevskyturnersyndromeinaorticsurgeryanexampleofhybridaneurismtreatmentanddissectionofthoracoabdominalaorta AT rspolyakov shereshevskyturnersyndromeinaorticsurgeryanexampleofhybridaneurismtreatmentanddissectionofthoracoabdominalaorta AT evzaklyazminskaya shereshevskyturnersyndromeinaorticsurgeryanexampleofhybridaneurismtreatmentanddissectionofthoracoabdominalaorta AT varumyantseva shereshevskyturnersyndromeinaorticsurgeryanexampleofhybridaneurismtreatmentanddissectionofthoracoabdominalaorta AT vvkhovrin shereshevskyturnersyndromeinaorticsurgeryanexampleofhybridaneurismtreatmentanddissectionofthoracoabdominalaorta AT aaskvortsov shereshevskyturnersyndromeinaorticsurgeryanexampleofhybridaneurismtreatmentanddissectionofthoracoabdominalaorta AT mnkabanova shereshevskyturnersyndromeinaorticsurgeryanexampleofhybridaneurismtreatmentanddissectionofthoracoabdominalaorta AT zrkhatchatryan shereshevskyturnersyndromeinaorticsurgeryanexampleofhybridaneurismtreatmentanddissectionofthoracoabdominalaorta AT nvoparina shereshevskyturnersyndromeinaorticsurgeryanexampleofhybridaneurismtreatmentanddissectionofthoracoabdominalaorta |