Metachondromatosis: Clinical and radiological diagnosis and differential diagnosis

The clinical case of a 9-year-old patient derived from Orthopedics to the Institute of Genetics at Universidad Nacional de Colombia due to a longstanding medical history of multiple bony outgrowths that required surgical management without etiologic diagnosis is presented in this paper. A possible...

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Main Authors: Karym Zahir Halaby -Hernández, Elia María Jiménez-Acosta, Silvia Juliana Maradei-Anaya, Juan José Yunis Londoño, Clara Eugenia Arteaga Diaz
Format: Article
Language:English
Published: Universidad Nacional de Colombia 2016-01-01
Series:Case Reports
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Online Access:https://revistas.unal.edu.co/index.php/care/article/view/49478
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author Karym Zahir Halaby -Hernández
Elia María Jiménez-Acosta
Silvia Juliana Maradei-Anaya
Juan José Yunis Londoño
Clara Eugenia Arteaga Diaz
author_facet Karym Zahir Halaby -Hernández
Elia María Jiménez-Acosta
Silvia Juliana Maradei-Anaya
Juan José Yunis Londoño
Clara Eugenia Arteaga Diaz
author_sort Karym Zahir Halaby -Hernández
collection DOAJ
description The clinical case of a 9-year-old patient derived from Orthopedics to the Institute of Genetics at Universidad Nacional de Colombia due to a longstanding medical history of multiple bony outgrowths that required surgical management without etiologic diagnosis is presented in this paper. A possible diagnosis of metachondromatosis is suggested based on the clinical course, the family history, and the findings of the biopsy and regular growth parameters. On the other hand, differential diagnoses were compared taking into account the most common enchondromatosis type, based on data obtained during physical examination, radiological signs and other variables. This comparison was grounded on the review of existing literature on this type of entities.
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issn 2462-8522
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publishDate 2016-01-01
publisher Universidad Nacional de Colombia
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series Case Reports
spelling doaj-art-780a1cb2f7c04596b358c6a789fdc3da2025-08-20T01:52:46ZengUniversidad Nacional de ColombiaCase Reports2462-85222016-01-012143212Metachondromatosis: Clinical and radiological diagnosis and differential diagnosisKarym Zahir Halaby -Hernández0Elia María Jiménez-Acosta1Silvia Juliana Maradei-Anaya2Juan José Yunis Londoño3Clara Eugenia Arteaga Diaz4Universidad Nacional de ColombiaUniversidad Nacional de ColombiaUniversidad Nacional de Colombia.Universidad Nacional de ColombiaUniversidad Nacional de Colombia. The clinical case of a 9-year-old patient derived from Orthopedics to the Institute of Genetics at Universidad Nacional de Colombia due to a longstanding medical history of multiple bony outgrowths that required surgical management without etiologic diagnosis is presented in this paper. A possible diagnosis of metachondromatosis is suggested based on the clinical course, the family history, and the findings of the biopsy and regular growth parameters. On the other hand, differential diagnoses were compared taking into account the most common enchondromatosis type, based on data obtained during physical examination, radiological signs and other variables. This comparison was grounded on the review of existing literature on this type of entities. https://revistas.unal.edu.co/index.php/care/article/view/49478EnchondromatosisMetachondromatosisExostosisOsteochondromaPPT11 gene
spellingShingle Karym Zahir Halaby -Hernández
Elia María Jiménez-Acosta
Silvia Juliana Maradei-Anaya
Juan José Yunis Londoño
Clara Eugenia Arteaga Diaz
Metachondromatosis: Clinical and radiological diagnosis and differential diagnosis
Case Reports
Enchondromatosis
Metachondromatosis
Exostosis
Osteochondroma
PPT11 gene
title Metachondromatosis: Clinical and radiological diagnosis and differential diagnosis
title_full Metachondromatosis: Clinical and radiological diagnosis and differential diagnosis
title_fullStr Metachondromatosis: Clinical and radiological diagnosis and differential diagnosis
title_full_unstemmed Metachondromatosis: Clinical and radiological diagnosis and differential diagnosis
title_short Metachondromatosis: Clinical and radiological diagnosis and differential diagnosis
title_sort metachondromatosis clinical and radiological diagnosis and differential diagnosis
topic Enchondromatosis
Metachondromatosis
Exostosis
Osteochondroma
PPT11 gene
url https://revistas.unal.edu.co/index.php/care/article/view/49478
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AT eliamariajimenezacosta metachondromatosisclinicalandradiologicaldiagnosisanddifferentialdiagnosis
AT silviajulianamaradeianaya metachondromatosisclinicalandradiologicaldiagnosisanddifferentialdiagnosis
AT juanjoseyunislondono metachondromatosisclinicalandradiologicaldiagnosisanddifferentialdiagnosis
AT claraeugeniaarteagadiaz metachondromatosisclinicalandradiologicaldiagnosisanddifferentialdiagnosis