Acquired Factor XI Inhibitor Presenting as Spontaneous Bilateral Subdural Hematoma in an Elderly Patient

Development of autoantibodies against coagulation factors is an uncommon bleeding disorder associated with cancer, autoimmune conditions, pregnancy, or no apparent disease. Spontaneous FVIII inhibitors are the most frequently encountered; those against FXI have been only anecdotally reported. We rep...

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Main Authors: Natale Vazzana, Luca Scarti, Chiara Beltrame, Antonella Picchi, Gianni Taccetti, Alberto Fortini
Format: Article
Language:English
Published: Wiley 2014-01-01
Series:Case Reports in Hematology
Online Access:http://dx.doi.org/10.1155/2014/626831
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author Natale Vazzana
Luca Scarti
Chiara Beltrame
Antonella Picchi
Gianni Taccetti
Alberto Fortini
author_facet Natale Vazzana
Luca Scarti
Chiara Beltrame
Antonella Picchi
Gianni Taccetti
Alberto Fortini
author_sort Natale Vazzana
collection DOAJ
description Development of autoantibodies against coagulation factors is an uncommon bleeding disorder associated with cancer, autoimmune conditions, pregnancy, or no apparent disease. Spontaneous FVIII inhibitors are the most frequently encountered; those against FXI have been only anecdotally reported. We report a case of acquired FXI inhibitor presenting as fatal intracranial spontaneous bleeding in an elderly patient with history of cancer and previous transfusions. Few cases of acquired FXI inhibitor have been reported in association with connective tissue disease, cancer, or surgery. Bleeding includes mucocutaneous bleeding, postsurgical hemorrhage, or life-threatening events. Treatment consists of arresting the bleeding and inhibitor eradication. High degree of suspicion is essential to promptly diagnose and treat this uncommon condition.
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2090-6579
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publishDate 2014-01-01
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series Case Reports in Hematology
spelling doaj-art-74c8f49ec7b44d62ae01ccd536b520b12025-08-20T02:07:20ZengWileyCase Reports in Hematology2090-65602090-65792014-01-01201410.1155/2014/626831626831Acquired Factor XI Inhibitor Presenting as Spontaneous Bilateral Subdural Hematoma in an Elderly PatientNatale Vazzana0Luca Scarti1Chiara Beltrame2Antonella Picchi3Gianni Taccetti4Alberto Fortini5Department of Internal Medicine, “S. Giovanni di Dio” Hospital, Via di Torregalli, 3-50143 Florence, ItalyDepartment of Internal Medicine, “S. Giovanni di Dio” Hospital, Via di Torregalli, 3-50143 Florence, ItalyDepartment of Internal Medicine, “S. Giovanni di Dio” Hospital, Via di Torregalli, 3-50143 Florence, ItalyDepartment of Clinical Chemistry, “S. Giovanni di Dio” Hospital, Via di Torregalli, 3-50143 Florence, ItalyDepartment of Internal Medicine, “S. Giovanni di Dio” Hospital, Via di Torregalli, 3-50143 Florence, ItalyDepartment of Internal Medicine, “S. Giovanni di Dio” Hospital, Via di Torregalli, 3-50143 Florence, ItalyDevelopment of autoantibodies against coagulation factors is an uncommon bleeding disorder associated with cancer, autoimmune conditions, pregnancy, or no apparent disease. Spontaneous FVIII inhibitors are the most frequently encountered; those against FXI have been only anecdotally reported. We report a case of acquired FXI inhibitor presenting as fatal intracranial spontaneous bleeding in an elderly patient with history of cancer and previous transfusions. Few cases of acquired FXI inhibitor have been reported in association with connective tissue disease, cancer, or surgery. Bleeding includes mucocutaneous bleeding, postsurgical hemorrhage, or life-threatening events. Treatment consists of arresting the bleeding and inhibitor eradication. High degree of suspicion is essential to promptly diagnose and treat this uncommon condition.http://dx.doi.org/10.1155/2014/626831
spellingShingle Natale Vazzana
Luca Scarti
Chiara Beltrame
Antonella Picchi
Gianni Taccetti
Alberto Fortini
Acquired Factor XI Inhibitor Presenting as Spontaneous Bilateral Subdural Hematoma in an Elderly Patient
Case Reports in Hematology
title Acquired Factor XI Inhibitor Presenting as Spontaneous Bilateral Subdural Hematoma in an Elderly Patient
title_full Acquired Factor XI Inhibitor Presenting as Spontaneous Bilateral Subdural Hematoma in an Elderly Patient
title_fullStr Acquired Factor XI Inhibitor Presenting as Spontaneous Bilateral Subdural Hematoma in an Elderly Patient
title_full_unstemmed Acquired Factor XI Inhibitor Presenting as Spontaneous Bilateral Subdural Hematoma in an Elderly Patient
title_short Acquired Factor XI Inhibitor Presenting as Spontaneous Bilateral Subdural Hematoma in an Elderly Patient
title_sort acquired factor xi inhibitor presenting as spontaneous bilateral subdural hematoma in an elderly patient
url http://dx.doi.org/10.1155/2014/626831
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