Femoral intraosseous rhabdomyosarcoma: a case report and literature review
Introduction: Rhabdomyosarcoma is the most common soft tissue sarcoma in childhood. However, primary bone rhabdomyosarcoma is a rare entity with some few cases reported. Case Report: We present a case of a 19-year-old female patient referred from another service with three months histor...
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| Format: | Article |
| Language: | English |
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Thieme Revinter Publicações Ltda.
2021-10-01
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| Series: | Brazilian Journal of Oncology |
| Subjects: | |
| Online Access: | http://www.brazilianjournalofoncology.com.br/details/167/en-US/femoral-intraosseous-rhabdomyosarcoma--a-case-report-and-literature-review |
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| _version_ | 1850251969783922688 |
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| author | Dan Carai Maia Viola Nathalia Sundin Palmeira de Oliveira Jairo Greco Garcia Marcelo de Toledo Petrilli Carla Renata Pacheco Donato Macedo Maria Teresa Seixas Alves Reynaldo JesusGarcia |
| author_facet | Dan Carai Maia Viola Nathalia Sundin Palmeira de Oliveira Jairo Greco Garcia Marcelo de Toledo Petrilli Carla Renata Pacheco Donato Macedo Maria Teresa Seixas Alves Reynaldo JesusGarcia |
| author_sort | Dan Carai Maia Viola |
| collection | DOAJ |
| description | Introduction: Rhabdomyosarcoma is the most common soft tissue sarcoma in childhood. However, primary bone rhabdomyosarcoma is a rare entity with some few cases reported.
Case Report: We present a case of a 19-year-old female patient referred from another service with three months history of a bone tumor on the femur. The first anatomopathological study was consistent with high-grade osteogenic sarcoma. After revision exams and analysis of surgically resected tumor, the primary osseous rhabdomyosarcoma was confirmed. The patient had undergone tumor resection and reconstruction with mega prosthesis. After surgery, she received chemotherapy following rhabdomyosarcoma protocol.
Conclusion: Primary osseous rhabdomyosarcoma is a rare but important differential diagnosis to be thought on atypical presentation of primary bone sarcomas. |
| format | Article |
| id | doaj-art-7445cfe711a64b8abd16b991bbc4b384 |
| institution | OA Journals |
| issn | 2526-8732 |
| language | English |
| publishDate | 2021-10-01 |
| publisher | Thieme Revinter Publicações Ltda. |
| record_format | Article |
| series | Brazilian Journal of Oncology |
| spelling | doaj-art-7445cfe711a64b8abd16b991bbc4b3842025-08-20T01:57:47ZengThieme Revinter Publicações Ltda.Brazilian Journal of Oncology2526-87322021-10-01170010.5935/2526-8732.20210021Femoral intraosseous rhabdomyosarcoma: a case report and literature reviewDan Carai Maia Viola0https://orcid.org/0000-0002-6173-8004Nathalia Sundin Palmeira de Oliveira1Jairo Greco Garcia2Marcelo de Toledo Petrilli3Carla Renata Pacheco Donato Macedo4Maria Teresa Seixas Alves5Reynaldo JesusGarcia6Universidade Federal De Sao Paulo, Ortopedia E Traumatologia - Sao Paulo - SP - BrazilUniversidade Federal De Sao Paulo, Ortopedia E Traumatologia - Sao Paulo - SP - BrazilUniversidade Federal De Sao Paulo, Ortopedia E Traumatologia - Sao Paulo - SP - BrazilUniversidade Federal De Sao Paulo, Ortopedia E Traumatologia - Sao Paulo - SP - BrazilInstituto De Oncologia Pediatrica / Iop-Graacc, Oncologia Pediatrica - Sao Paulo - SP - BrazilUniversidade Federal De Sao Paulo, Patologia - Sao Paulo - SP - BrazilUniversidade Federal De Sao Paulo, Ortopedia E Traumatologia - Sao Paulo - SP - BrazilIntroduction: Rhabdomyosarcoma is the most common soft tissue sarcoma in childhood. However, primary bone rhabdomyosarcoma is a rare entity with some few cases reported. Case Report: We present a case of a 19-year-old female patient referred from another service with three months history of a bone tumor on the femur. The first anatomopathological study was consistent with high-grade osteogenic sarcoma. After revision exams and analysis of surgically resected tumor, the primary osseous rhabdomyosarcoma was confirmed. The patient had undergone tumor resection and reconstruction with mega prosthesis. After surgery, she received chemotherapy following rhabdomyosarcoma protocol. Conclusion: Primary osseous rhabdomyosarcoma is a rare but important differential diagnosis to be thought on atypical presentation of primary bone sarcomas.http://www.brazilianjournalofoncology.com.br/details/167/en-US/femoral-intraosseous-rhabdomyosarcoma--a-case-report-and-literature-reviewrhabdomyosarcomabone neoplasmachemotherapy |
| spellingShingle | Dan Carai Maia Viola Nathalia Sundin Palmeira de Oliveira Jairo Greco Garcia Marcelo de Toledo Petrilli Carla Renata Pacheco Donato Macedo Maria Teresa Seixas Alves Reynaldo JesusGarcia Femoral intraosseous rhabdomyosarcoma: a case report and literature review Brazilian Journal of Oncology rhabdomyosarcoma bone neoplasma chemotherapy |
| title | Femoral intraosseous rhabdomyosarcoma: a case report and literature review |
| title_full | Femoral intraosseous rhabdomyosarcoma: a case report and literature review |
| title_fullStr | Femoral intraosseous rhabdomyosarcoma: a case report and literature review |
| title_full_unstemmed | Femoral intraosseous rhabdomyosarcoma: a case report and literature review |
| title_short | Femoral intraosseous rhabdomyosarcoma: a case report and literature review |
| title_sort | femoral intraosseous rhabdomyosarcoma a case report and literature review |
| topic | rhabdomyosarcoma bone neoplasma chemotherapy |
| url | http://www.brazilianjournalofoncology.com.br/details/167/en-US/femoral-intraosseous-rhabdomyosarcoma--a-case-report-and-literature-review |
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