Hypodontia and Delayed Dentition as the Primary Manifestation of Cleidocranial Dysplasia Presenting with a Diagnostic Dilemma

Cleidocranial dysplasia is a rare autosomal disorder which manifests as partial or complete absence of clavicles, multiple supernumerary teeth, and delayed closure of fontanelle. Classical cases of cleidocranial dysplasia are easily diagnosed very early in the life. However, cases with partial manif...

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Main Authors: Radhika Chopra, Mohita Marwaha, Payal Chaudhuri, Kalpana Bansal, Saurabh Chopra
Format: Article
Language:English
Published: Wiley 2012-01-01
Series:Case Reports in Dentistry
Online Access:http://dx.doi.org/10.1155/2012/262043
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author Radhika Chopra
Mohita Marwaha
Payal Chaudhuri
Kalpana Bansal
Saurabh Chopra
author_facet Radhika Chopra
Mohita Marwaha
Payal Chaudhuri
Kalpana Bansal
Saurabh Chopra
author_sort Radhika Chopra
collection DOAJ
description Cleidocranial dysplasia is a rare autosomal disorder which manifests as partial or complete absence of clavicles, multiple supernumerary teeth, and delayed closure of fontanelle. Classical cases of cleidocranial dysplasia are easily diagnosed very early in the life. However, cases with partial manifestation of the syndrome and noncontributory family history are difficult to diagnose. Here, we report a case of 8.5-year-old girl child who presented with delayed tooth development (without any supernumerary teeth), anterior open fontanelle, and normal clavicles, thus resulting in a diagnostic dilemma.
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institution Kabale University
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publishDate 2012-01-01
publisher Wiley
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series Case Reports in Dentistry
spelling doaj-art-73f24eaa77e04eb59d52bfb08604e8c22025-08-20T03:33:54ZengWileyCase Reports in Dentistry2090-64472090-64552012-01-01201210.1155/2012/262043262043Hypodontia and Delayed Dentition as the Primary Manifestation of Cleidocranial Dysplasia Presenting with a Diagnostic DilemmaRadhika Chopra0Mohita Marwaha1Payal Chaudhuri2Kalpana Bansal3Saurabh Chopra4Department of Pedodontics and Preventive Dentistry, SGT Dental College & Research Institute, Budhera 123505, Gurgaon, Haryana, IndiaDepartment of Pedodontics and Preventive Dentistry, SGT Dental College & Research Institute, Budhera 123505, Gurgaon, Haryana, IndiaDepartment of Pedodontics and Preventive Dentistry, SGT Dental College & Research Institute, Budhera 123505, Gurgaon, Haryana, IndiaDepartment of Pedodontics and Preventive Dentistry, SGT Dental College & Research Institute, Budhera 123505, Gurgaon, Haryana, IndiaDepartment of Pediatrics, Subharti Medical College, Meerut 250005, IndiaCleidocranial dysplasia is a rare autosomal disorder which manifests as partial or complete absence of clavicles, multiple supernumerary teeth, and delayed closure of fontanelle. Classical cases of cleidocranial dysplasia are easily diagnosed very early in the life. However, cases with partial manifestation of the syndrome and noncontributory family history are difficult to diagnose. Here, we report a case of 8.5-year-old girl child who presented with delayed tooth development (without any supernumerary teeth), anterior open fontanelle, and normal clavicles, thus resulting in a diagnostic dilemma.http://dx.doi.org/10.1155/2012/262043
spellingShingle Radhika Chopra
Mohita Marwaha
Payal Chaudhuri
Kalpana Bansal
Saurabh Chopra
Hypodontia and Delayed Dentition as the Primary Manifestation of Cleidocranial Dysplasia Presenting with a Diagnostic Dilemma
Case Reports in Dentistry
title Hypodontia and Delayed Dentition as the Primary Manifestation of Cleidocranial Dysplasia Presenting with a Diagnostic Dilemma
title_full Hypodontia and Delayed Dentition as the Primary Manifestation of Cleidocranial Dysplasia Presenting with a Diagnostic Dilemma
title_fullStr Hypodontia and Delayed Dentition as the Primary Manifestation of Cleidocranial Dysplasia Presenting with a Diagnostic Dilemma
title_full_unstemmed Hypodontia and Delayed Dentition as the Primary Manifestation of Cleidocranial Dysplasia Presenting with a Diagnostic Dilemma
title_short Hypodontia and Delayed Dentition as the Primary Manifestation of Cleidocranial Dysplasia Presenting with a Diagnostic Dilemma
title_sort hypodontia and delayed dentition as the primary manifestation of cleidocranial dysplasia presenting with a diagnostic dilemma
url http://dx.doi.org/10.1155/2012/262043
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