HAIR-AN Syndrome: A Rare Cause of Hyper Insulinemic State

Insulin resistance is categorized as type A or type B, depending on the etiology. HAIRAN syndrome is a subtype of type A insulin resistance. It is characterized by high insulin resistance, hyperandrogenemia, and hyperinsulinemia. Here, we present a 12-year-old girl who was lean during her first dec...

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Main Authors: Sriram Mudraje, Nancy Garg, Jaideep Khare, Sushil Jindal
Format: Article
Language:English
Published: Tehran University of Medical Sciences 2025-07-01
Series:Case Reports in Clinical Practice
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Online Access:https://crcp.tums.ac.ir/index.php/crcp/article/view/1033
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author Sriram Mudraje
Nancy Garg
Jaideep Khare
Sushil Jindal
author_facet Sriram Mudraje
Nancy Garg
Jaideep Khare
Sushil Jindal
author_sort Sriram Mudraje
collection DOAJ
description Insulin resistance is categorized as type A or type B, depending on the etiology. HAIRAN syndrome is a subtype of type A insulin resistance. It is characterized by high insulin resistance, hyperandrogenemia, and hyperinsulinemia. Here, we present a 12-year-old girl who was lean during her first decade of life and came with complaints of gradual-onset weight gain, darkening of her neck and limbs, and roughening of her skin. Menarche had not been attained. She had Grade 4 acanthosis nigricans, thick coarse skin, and hirsutism. Investigations revealed raised blood glucose, elevated testosterone, elevated fasting insulin, and raised HOMA-IR. With biochemical evidence of hyperandrogenemia, insulin resistance, and the presence of acanthosis nigricans, the diagnosis of HAIR-AN syndrome was made.
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issn 2538-2683
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publishDate 2025-07-01
publisher Tehran University of Medical Sciences
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series Case Reports in Clinical Practice
spelling doaj-art-7392ba37d4844a85a3867bd487d04d062025-08-20T03:03:04ZengTehran University of Medical SciencesCase Reports in Clinical Practice2538-26832538-26912025-07-019610.18502/crcp.v9i6.18947HAIR-AN Syndrome: A Rare Cause of Hyper Insulinemic StateSriram Mudraje0Nancy Garg1Jaideep Khare2Sushil Jindal3Department of Endocrinology, People’s College of Medical Sciences and Research Centre, People’s University, Bhopal, India.Department of Endocrinology, People’s College of Medical Sciences and Research Centre, People’s University, Bhopal, India.Department of Endocrinology, People’s College of Medical Sciences and Research Centre, People’s University, Bhopal, India.Department of Endocrinology, People’s College of Medical Sciences and Research Centre, People’s University, Bhopal, India. Insulin resistance is categorized as type A or type B, depending on the etiology. HAIRAN syndrome is a subtype of type A insulin resistance. It is characterized by high insulin resistance, hyperandrogenemia, and hyperinsulinemia. Here, we present a 12-year-old girl who was lean during her first decade of life and came with complaints of gradual-onset weight gain, darkening of her neck and limbs, and roughening of her skin. Menarche had not been attained. She had Grade 4 acanthosis nigricans, thick coarse skin, and hirsutism. Investigations revealed raised blood glucose, elevated testosterone, elevated fasting insulin, and raised HOMA-IR. With biochemical evidence of hyperandrogenemia, insulin resistance, and the presence of acanthosis nigricans, the diagnosis of HAIR-AN syndrome was made. https://crcp.tums.ac.ir/index.php/crcp/article/view/1033HAIR-AN syndromeHyperinsulinemiaInsulin resistanceHyperandrogenemia
spellingShingle Sriram Mudraje
Nancy Garg
Jaideep Khare
Sushil Jindal
HAIR-AN Syndrome: A Rare Cause of Hyper Insulinemic State
Case Reports in Clinical Practice
HAIR-AN syndrome
Hyperinsulinemia
Insulin resistance
Hyperandrogenemia
title HAIR-AN Syndrome: A Rare Cause of Hyper Insulinemic State
title_full HAIR-AN Syndrome: A Rare Cause of Hyper Insulinemic State
title_fullStr HAIR-AN Syndrome: A Rare Cause of Hyper Insulinemic State
title_full_unstemmed HAIR-AN Syndrome: A Rare Cause of Hyper Insulinemic State
title_short HAIR-AN Syndrome: A Rare Cause of Hyper Insulinemic State
title_sort hair an syndrome a rare cause of hyper insulinemic state
topic HAIR-AN syndrome
Hyperinsulinemia
Insulin resistance
Hyperandrogenemia
url https://crcp.tums.ac.ir/index.php/crcp/article/view/1033
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AT jaideepkhare hairansyndromeararecauseofhyperinsulinemicstate
AT sushiljindal hairansyndromeararecauseofhyperinsulinemicstate