DRESS Syndrome Presents as Leukoencephalopathy

DRESS syndrome (Drug Rash with Eosinophilia and Systemic Symptoms) is a potentially life-threatening syndrome, which reflects a serious hypersensitivity reaction to drugs, presenting by generalized skin rash, fever, eosinophilia, atypical lymphocytosis, and internal organ involvement. Herein...

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Main Authors: Seyed Hasan Tonekaboni, Narjes Jafari, Zahra Chavoshzadeh, Bibi Shahin Shamsian, Nima Rezaei
Format: Article
Language:English
Published: Hacettepe University Institute of Child Health 2015-10-01
Series:The Turkish Journal of Pediatrics
Online Access:https://turkjpediatr.org/article/view/1284
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author Seyed Hasan Tonekaboni
Narjes Jafari
Zahra Chavoshzadeh
Bibi Shahin Shamsian
Nima Rezaei
author_facet Seyed Hasan Tonekaboni
Narjes Jafari
Zahra Chavoshzadeh
Bibi Shahin Shamsian
Nima Rezaei
author_sort Seyed Hasan Tonekaboni
collection DOAJ
description DRESS syndrome (Drug Rash with Eosinophilia and Systemic Symptoms) is a potentially life-threatening syndrome, which reflects a serious hypersensitivity reaction to drugs, presenting by generalized skin rash, fever, eosinophilia, atypical lymphocytosis, and internal organ involvement. Herein a 21-month old male infant with DRESS and Encephalopathy syndrome is presented who complicated after phenobarbital usage that persisted due to phenytoin cream usage. The case received phenobarbital after a seizure disorder presented as "status epilepticus". He developed drug eruption, fever, hepatosplenomegaly, increased liver enzymes, encephalopathy and progressive loss of consciousness with extensive hyperintense white matter lesions in brain MRI. After discontinuation of phenobarbital and phenytoin, all symptoms were resolved, while brain MRI became normal after two months. To our best knowledge, this is the first reported case that developed leukoencephalopathy along with DRESS syndrome.
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issn 0041-4301
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language English
publishDate 2015-10-01
publisher Hacettepe University Institute of Child Health
record_format Article
series The Turkish Journal of Pediatrics
spelling doaj-art-72dffa8af1084d61b585dce3ea38011e2025-08-20T02:01:47ZengHacettepe University Institute of Child HealthThe Turkish Journal of Pediatrics0041-43012791-64212015-10-01575DRESS Syndrome Presents as LeukoencephalopathySeyed Hasan Tonekaboni0Narjes JafariZahra ChavoshzadehBibi Shahin ShamsianNima RezaeiPediatric Neurology Research Center, Shahid Beheshti University of Medical Sciences, Tehran, Iran. zahra_chavoshzadeh@yahoo.com. DRESS syndrome (Drug Rash with Eosinophilia and Systemic Symptoms) is a potentially life-threatening syndrome, which reflects a serious hypersensitivity reaction to drugs, presenting by generalized skin rash, fever, eosinophilia, atypical lymphocytosis, and internal organ involvement. Herein a 21-month old male infant with DRESS and Encephalopathy syndrome is presented who complicated after phenobarbital usage that persisted due to phenytoin cream usage. The case received phenobarbital after a seizure disorder presented as "status epilepticus". He developed drug eruption, fever, hepatosplenomegaly, increased liver enzymes, encephalopathy and progressive loss of consciousness with extensive hyperintense white matter lesions in brain MRI. After discontinuation of phenobarbital and phenytoin, all symptoms were resolved, while brain MRI became normal after two months. To our best knowledge, this is the first reported case that developed leukoencephalopathy along with DRESS syndrome. https://turkjpediatr.org/article/view/1284
spellingShingle Seyed Hasan Tonekaboni
Narjes Jafari
Zahra Chavoshzadeh
Bibi Shahin Shamsian
Nima Rezaei
DRESS Syndrome Presents as Leukoencephalopathy
The Turkish Journal of Pediatrics
title DRESS Syndrome Presents as Leukoencephalopathy
title_full DRESS Syndrome Presents as Leukoencephalopathy
title_fullStr DRESS Syndrome Presents as Leukoencephalopathy
title_full_unstemmed DRESS Syndrome Presents as Leukoencephalopathy
title_short DRESS Syndrome Presents as Leukoencephalopathy
title_sort dress syndrome presents as leukoencephalopathy
url https://turkjpediatr.org/article/view/1284
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