Eosinophilic pustular folliculitis associated with IgA deficiency
Abstract Eosinophilic pustular folliculitis (EPF) is a noninfectious follicular based inflammatory dermatosis. We present a case of a 57‐year‐old female of Indian ethnicity who developed a pustular eruption, with certain lesions displaying Koebnerization. Given that the morphologic distribution most...
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| Format: | Article |
| Language: | English |
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Wiley
2025-03-01
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| Series: | JEADV Clinical Practice |
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| Online Access: | https://doi.org/10.1002/jvc2.560 |
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| author | L. E. Flowers S. Subhadarshani S. Quinter C. Shaughnessy |
| author_facet | L. E. Flowers S. Subhadarshani S. Quinter C. Shaughnessy |
| author_sort | L. E. Flowers |
| collection | DOAJ |
| description | Abstract Eosinophilic pustular folliculitis (EPF) is a noninfectious follicular based inflammatory dermatosis. We present a case of a 57‐year‐old female of Indian ethnicity who developed a pustular eruption, with certain lesions displaying Koebnerization. Given that the morphologic distribution most represented the immunosuppressant EPF subtype, additional testing led to the discovery of concurrent IgA deficiency. This case highlights a particularly unusual presentation of EPF associated with IgA deficiency and Koebner phenomenon. |
| format | Article |
| id | doaj-art-72bb0e6a9c2d4ce6870b333cece46d30 |
| institution | Kabale University |
| issn | 2768-6566 |
| language | English |
| publishDate | 2025-03-01 |
| publisher | Wiley |
| record_format | Article |
| series | JEADV Clinical Practice |
| spelling | doaj-art-72bb0e6a9c2d4ce6870b333cece46d302025-08-20T03:40:25ZengWileyJEADV Clinical Practice2768-65662025-03-014124424710.1002/jvc2.560Eosinophilic pustular folliculitis associated with IgA deficiencyL. E. Flowers0S. Subhadarshani1S. Quinter2C. Shaughnessy3School of Medicine University of Missouri‐Columbia Columbia Missouri USADepartment of Dermatology University of Cincinnati Cincinnati Ohio USADepartment of Dermatology University of Cincinnati Cincinnati Ohio USADepartment of Dermatology University of Cincinnati Cincinnati Ohio USAAbstract Eosinophilic pustular folliculitis (EPF) is a noninfectious follicular based inflammatory dermatosis. We present a case of a 57‐year‐old female of Indian ethnicity who developed a pustular eruption, with certain lesions displaying Koebnerization. Given that the morphologic distribution most represented the immunosuppressant EPF subtype, additional testing led to the discovery of concurrent IgA deficiency. This case highlights a particularly unusual presentation of EPF associated with IgA deficiency and Koebner phenomenon.https://doi.org/10.1002/jvc2.560eosinophilic pustular folliculitisIgA deficiencyKoebner phenomenonOfuji's disease |
| spellingShingle | L. E. Flowers S. Subhadarshani S. Quinter C. Shaughnessy Eosinophilic pustular folliculitis associated with IgA deficiency JEADV Clinical Practice eosinophilic pustular folliculitis IgA deficiency Koebner phenomenon Ofuji's disease |
| title | Eosinophilic pustular folliculitis associated with IgA deficiency |
| title_full | Eosinophilic pustular folliculitis associated with IgA deficiency |
| title_fullStr | Eosinophilic pustular folliculitis associated with IgA deficiency |
| title_full_unstemmed | Eosinophilic pustular folliculitis associated with IgA deficiency |
| title_short | Eosinophilic pustular folliculitis associated with IgA deficiency |
| title_sort | eosinophilic pustular folliculitis associated with iga deficiency |
| topic | eosinophilic pustular folliculitis IgA deficiency Koebner phenomenon Ofuji's disease |
| url | https://doi.org/10.1002/jvc2.560 |
| work_keys_str_mv | AT leflowers eosinophilicpustularfolliculitisassociatedwithigadeficiency AT ssubhadarshani eosinophilicpustularfolliculitisassociatedwithigadeficiency AT squinter eosinophilicpustularfolliculitisassociatedwithigadeficiency AT cshaughnessy eosinophilicpustularfolliculitisassociatedwithigadeficiency |