Eosinophilic pustular folliculitis associated with IgA deficiency

Abstract Eosinophilic pustular folliculitis (EPF) is a noninfectious follicular based inflammatory dermatosis. We present a case of a 57‐year‐old female of Indian ethnicity who developed a pustular eruption, with certain lesions displaying Koebnerization. Given that the morphologic distribution most...

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Bibliographic Details
Main Authors: L. E. Flowers, S. Subhadarshani, S. Quinter, C. Shaughnessy
Format: Article
Language:English
Published: Wiley 2025-03-01
Series:JEADV Clinical Practice
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Online Access:https://doi.org/10.1002/jvc2.560
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Summary:Abstract Eosinophilic pustular folliculitis (EPF) is a noninfectious follicular based inflammatory dermatosis. We present a case of a 57‐year‐old female of Indian ethnicity who developed a pustular eruption, with certain lesions displaying Koebnerization. Given that the morphologic distribution most represented the immunosuppressant EPF subtype, additional testing led to the discovery of concurrent IgA deficiency. This case highlights a particularly unusual presentation of EPF associated with IgA deficiency and Koebner phenomenon.
ISSN:2768-6566