Orthodontic Treatment and Maxillary Anterior Segmental Distraction Osteogenesis of a Subject with Williams–Beuren Syndrome and Isolated Cleft Palate: A Long-Term Follow-Up from the Age of 5 to 24 Years
Williams–Beuren syndrome (WBS) is a rare multisystem disorder caused by a hemizygous deletion of the elastin gene on chromosome 7q11.23. WBS patients have characteristic skeletal features and dental anomalies accompanied by mental retardation, a friendly outgoing personality, and mild to moderate in...
Saved in:
| Main Authors: | , , , , , , , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Wiley
2017-01-01
|
| Series: | Case Reports in Dentistry |
| Online Access: | http://dx.doi.org/10.1155/2017/7019045 |
| Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
| _version_ | 1832560738825142272 |
|---|---|
| author | Tetsutaro Yamaguchi Tatsuo Shirota Mohamed Adel Masahiro Takahashi Shugo Haga Ryo Nagahama Misato Nakashima Mayu Furuhata Takaaki Kamatani Koutaro Maki |
| author_facet | Tetsutaro Yamaguchi Tatsuo Shirota Mohamed Adel Masahiro Takahashi Shugo Haga Ryo Nagahama Misato Nakashima Mayu Furuhata Takaaki Kamatani Koutaro Maki |
| author_sort | Tetsutaro Yamaguchi |
| collection | DOAJ |
| description | Williams–Beuren syndrome (WBS) is a rare multisystem disorder caused by a hemizygous deletion of the elastin gene on chromosome 7q11.23. WBS patients have characteristic skeletal features and dental anomalies accompanied by mental retardation, a friendly outgoing personality, and mild to moderate intellectual disability or learning problems. In this case report, we present the combined orthodontic and surgical treatment of a WBS patient with an isolated cleft palate through a long-term follow-up from the age of 5 to 24 years. During the period of active treatment, comprehensive orthodontic treatment combined with maxillary anterior segmental distraction osteogenesis and prosthetic treatment using dental implants were effective in dramatically improving the patient’s malocclusion. The patient’s mental abilities and the cooperation shown by the patient and her family were crucial for the success of this complex and long-term treatment course. |
| format | Article |
| id | doaj-art-72ba67e1acd74853a4f89ad287507742 |
| institution | Kabale University |
| issn | 2090-6447 2090-6455 |
| language | English |
| publishDate | 2017-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Dentistry |
| spelling | doaj-art-72ba67e1acd74853a4f89ad2875077422025-02-03T01:26:52ZengWileyCase Reports in Dentistry2090-64472090-64552017-01-01201710.1155/2017/70190457019045Orthodontic Treatment and Maxillary Anterior Segmental Distraction Osteogenesis of a Subject with Williams–Beuren Syndrome and Isolated Cleft Palate: A Long-Term Follow-Up from the Age of 5 to 24 YearsTetsutaro Yamaguchi0Tatsuo Shirota1Mohamed Adel2Masahiro Takahashi3Shugo Haga4Ryo Nagahama5Misato Nakashima6Mayu Furuhata7Takaaki Kamatani8Koutaro Maki9Department of Orthodontics, School of Dentistry, Showa University, 2-1-1 Kitasenzoku, Ohta-ku, Tokyo 145-8515, JapanDepartment of Oral and Maxillofacial Surgery, School of Dentistry, Showa University, 2-1-1 Kitasenzoku, Ohta-ku, Tokyo 145-8515, JapanDepartment of Orthodontics, School of Dentistry, Showa University, 2-1-1 Kitasenzoku, Ohta-ku, Tokyo 145-8515, JapanDepartment of Orthodontics, School of Dentistry, Showa University, 2-1-1 Kitasenzoku, Ohta-ku, Tokyo 145-8515, JapanDepartment of Orthodontics, School of Dentistry, Showa University, 2-1-1 Kitasenzoku, Ohta-ku, Tokyo 145-8515, JapanDepartment of Orthodontics, School of Dentistry, Showa University, 2-1-1 Kitasenzoku, Ohta-ku, Tokyo 145-8515, JapanDepartment of Orthodontics, School of Dentistry, Showa University, 2-1-1 Kitasenzoku, Ohta-ku, Tokyo 145-8515, JapanDepartment of Orthodontics, School of Dentistry, Showa University, 2-1-1 Kitasenzoku, Ohta-ku, Tokyo 145-8515, JapanDepartment of Oral and Maxillofacial Surgery, School of Dentistry, Showa University, 2-1-1 Kitasenzoku, Ohta-ku, Tokyo 145-8515, JapanDepartment of Orthodontics, School of Dentistry, Showa University, 2-1-1 Kitasenzoku, Ohta-ku, Tokyo 145-8515, JapanWilliams–Beuren syndrome (WBS) is a rare multisystem disorder caused by a hemizygous deletion of the elastin gene on chromosome 7q11.23. WBS patients have characteristic skeletal features and dental anomalies accompanied by mental retardation, a friendly outgoing personality, and mild to moderate intellectual disability or learning problems. In this case report, we present the combined orthodontic and surgical treatment of a WBS patient with an isolated cleft palate through a long-term follow-up from the age of 5 to 24 years. During the period of active treatment, comprehensive orthodontic treatment combined with maxillary anterior segmental distraction osteogenesis and prosthetic treatment using dental implants were effective in dramatically improving the patient’s malocclusion. The patient’s mental abilities and the cooperation shown by the patient and her family were crucial for the success of this complex and long-term treatment course.http://dx.doi.org/10.1155/2017/7019045 |
| spellingShingle | Tetsutaro Yamaguchi Tatsuo Shirota Mohamed Adel Masahiro Takahashi Shugo Haga Ryo Nagahama Misato Nakashima Mayu Furuhata Takaaki Kamatani Koutaro Maki Orthodontic Treatment and Maxillary Anterior Segmental Distraction Osteogenesis of a Subject with Williams–Beuren Syndrome and Isolated Cleft Palate: A Long-Term Follow-Up from the Age of 5 to 24 Years Case Reports in Dentistry |
| title | Orthodontic Treatment and Maxillary Anterior Segmental Distraction Osteogenesis of a Subject with Williams–Beuren Syndrome and Isolated Cleft Palate: A Long-Term Follow-Up from the Age of 5 to 24 Years |
| title_full | Orthodontic Treatment and Maxillary Anterior Segmental Distraction Osteogenesis of a Subject with Williams–Beuren Syndrome and Isolated Cleft Palate: A Long-Term Follow-Up from the Age of 5 to 24 Years |
| title_fullStr | Orthodontic Treatment and Maxillary Anterior Segmental Distraction Osteogenesis of a Subject with Williams–Beuren Syndrome and Isolated Cleft Palate: A Long-Term Follow-Up from the Age of 5 to 24 Years |
| title_full_unstemmed | Orthodontic Treatment and Maxillary Anterior Segmental Distraction Osteogenesis of a Subject with Williams–Beuren Syndrome and Isolated Cleft Palate: A Long-Term Follow-Up from the Age of 5 to 24 Years |
| title_short | Orthodontic Treatment and Maxillary Anterior Segmental Distraction Osteogenesis of a Subject with Williams–Beuren Syndrome and Isolated Cleft Palate: A Long-Term Follow-Up from the Age of 5 to 24 Years |
| title_sort | orthodontic treatment and maxillary anterior segmental distraction osteogenesis of a subject with williams beuren syndrome and isolated cleft palate a long term follow up from the age of 5 to 24 years |
| url | http://dx.doi.org/10.1155/2017/7019045 |
| work_keys_str_mv | AT tetsutaroyamaguchi orthodontictreatmentandmaxillaryanteriorsegmentaldistractionosteogenesisofasubjectwithwilliamsbeurensyndromeandisolatedcleftpalatealongtermfollowupfromtheageof5to24years AT tatsuoshirota orthodontictreatmentandmaxillaryanteriorsegmentaldistractionosteogenesisofasubjectwithwilliamsbeurensyndromeandisolatedcleftpalatealongtermfollowupfromtheageof5to24years AT mohamedadel orthodontictreatmentandmaxillaryanteriorsegmentaldistractionosteogenesisofasubjectwithwilliamsbeurensyndromeandisolatedcleftpalatealongtermfollowupfromtheageof5to24years AT masahirotakahashi orthodontictreatmentandmaxillaryanteriorsegmentaldistractionosteogenesisofasubjectwithwilliamsbeurensyndromeandisolatedcleftpalatealongtermfollowupfromtheageof5to24years AT shugohaga orthodontictreatmentandmaxillaryanteriorsegmentaldistractionosteogenesisofasubjectwithwilliamsbeurensyndromeandisolatedcleftpalatealongtermfollowupfromtheageof5to24years AT ryonagahama orthodontictreatmentandmaxillaryanteriorsegmentaldistractionosteogenesisofasubjectwithwilliamsbeurensyndromeandisolatedcleftpalatealongtermfollowupfromtheageof5to24years AT misatonakashima orthodontictreatmentandmaxillaryanteriorsegmentaldistractionosteogenesisofasubjectwithwilliamsbeurensyndromeandisolatedcleftpalatealongtermfollowupfromtheageof5to24years AT mayufuruhata orthodontictreatmentandmaxillaryanteriorsegmentaldistractionosteogenesisofasubjectwithwilliamsbeurensyndromeandisolatedcleftpalatealongtermfollowupfromtheageof5to24years AT takaakikamatani orthodontictreatmentandmaxillaryanteriorsegmentaldistractionosteogenesisofasubjectwithwilliamsbeurensyndromeandisolatedcleftpalatealongtermfollowupfromtheageof5to24years AT koutaromaki orthodontictreatmentandmaxillaryanteriorsegmentaldistractionosteogenesisofasubjectwithwilliamsbeurensyndromeandisolatedcleftpalatealongtermfollowupfromtheageof5to24years |