Super Enhancer Regulatory Gene FYB1 Promotes the Progression of T Cell Acute Lymphoblastic Leukemia by Activating IGLL1

Background. Arising from T progenitor cells, T-cell acute lymphoblastic leukemia (T-ALL) is an aggressive hematologic malignant tumor, accounting for 15% of childhood ALL and 25% of adult ALL. Composing of putative enhancers in close genomic proximity, super enhancer (SE) is critical for cell identi...

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Main Authors: Kunlong Zhang, Jun Lu, Fang Fang, Yongping Zhang, Juanjuan Yu, Yanfang Tao, Wenyuan liu, Lihui Lu, Zimu Zhang, Xinran Chu, Jianwei Wang, Xiaolu Li, Yuanyuan Tian, Zhiheng Li, Qian Li, Xu Sang, Li Ma, Ningling Wang, Jian Pan, Shaoyan Hu
Format: Article
Language:English
Published: Wiley 2023-01-01
Series:Journal of Immunology Research
Online Access:http://dx.doi.org/10.1155/2023/3804605
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author Kunlong Zhang
Jun Lu
Fang Fang
Yongping Zhang
Juanjuan Yu
Yanfang Tao
Wenyuan liu
Lihui Lu
Zimu Zhang
Xinran Chu
Jianwei Wang
Xiaolu Li
Yuanyuan Tian
Zhiheng Li
Qian Li
Xu Sang
Li Ma
Ningling Wang
Jian Pan
Shaoyan Hu
author_facet Kunlong Zhang
Jun Lu
Fang Fang
Yongping Zhang
Juanjuan Yu
Yanfang Tao
Wenyuan liu
Lihui Lu
Zimu Zhang
Xinran Chu
Jianwei Wang
Xiaolu Li
Yuanyuan Tian
Zhiheng Li
Qian Li
Xu Sang
Li Ma
Ningling Wang
Jian Pan
Shaoyan Hu
author_sort Kunlong Zhang
collection DOAJ
description Background. Arising from T progenitor cells, T-cell acute lymphoblastic leukemia (T-ALL) is an aggressive hematologic malignant tumor, accounting for 15% of childhood ALL and 25% of adult ALL. Composing of putative enhancers in close genomic proximity, super enhancer (SE) is critical for cell identity and the pathogenesis of multiple cancers. Belonging to the cytosolute linker protein group, FYB1 is essential for TCR signaling and extensively studied in terms of tumor pathogenesis and metastasis. Dissecting the role of FYN binding protein 1 (FYB1) in T-ALL holds the potential to improve the treatment outcome and prognosis of T-ALL. Methods. In this study, SEs were explored using public H3K27ac ChIP-seq data derived from T-ALL cell lines, AML cell lines and hematopoietic stem and progenitor cells (HSPCs). Downstream target of FYB1 gene was identified by RNA-seq. Effects of shRNA-mediated downregulation of FYB1 and immunoglobulin lambda-like polypeptide 1 (IGLL1) on self-renewal of T-ALL cells were evaluated in vitro and/or in vivo. Results. As an SE-driven gene, overexpression of FYB1 was observed in T-ALL, according to the Cancer Cell Line Encyclopedia database. In vitro, knocking down FYB1 led to comprised growth and enhanced apoptosis of T-ALL cells. In vivo, downregulation of FYB1 significantly decreased the disease burden by suppressing tumor growth and improved survival rate. Knocking down FYB1 resulted in significantly decreased expression of IGLL1 that was also an SE-driven gene in T-ALL. As a downstream target of FYB1, IGLL1 exerted similar role as FYB1 in inhibiting growth of T-ALL cells. Conclusion. Our results suggested that FYB1 gene played important role in regulating self-renewal of T-ALL cells by activating IGLL1, representing a promising therapeutic target for T-ALL patients.
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spelling doaj-art-718043b86f6d483cbca6c4e4fc999fc52025-08-20T03:33:57ZengWileyJournal of Immunology Research2314-71562023-01-01202310.1155/2023/3804605Super Enhancer Regulatory Gene FYB1 Promotes the Progression of T Cell Acute Lymphoblastic Leukemia by Activating IGLL1Kunlong Zhang0Jun Lu1Fang Fang2Yongping Zhang3Juanjuan Yu4Yanfang Tao5Wenyuan liu6Lihui Lu7Zimu Zhang8Xinran Chu9Jianwei Wang10Xiaolu Li11Yuanyuan Tian12Zhiheng Li13Qian Li14Xu Sang15Li Ma16Ningling Wang17Jian Pan18Shaoyan Hu19Children’s Hospital of Soochow UniversityDepartment of HematologyInstitute of Pediatric ResearchChildren’s Hospital of Soochow UniversityChildren’s Hospital of Soochow UniversityInstitute of Pediatric ResearchDepartment of PediatricsChildren’s Hospital of Soochow UniversityInstitute of Pediatric ResearchDepartment of HematologyInstitute of Pediatric ResearchInstitute of Pediatric ResearchDepartment of HematologyChildren’s Hospital of Soochow UniversityChildren’s Hospital of Soochow UniversityChildren’s Hospital of Soochow UniversityChildren’s Hospital of Soochow UniversityDepartment of PediatricsInstitute of Pediatric ResearchDepartment of HematologyBackground. Arising from T progenitor cells, T-cell acute lymphoblastic leukemia (T-ALL) is an aggressive hematologic malignant tumor, accounting for 15% of childhood ALL and 25% of adult ALL. Composing of putative enhancers in close genomic proximity, super enhancer (SE) is critical for cell identity and the pathogenesis of multiple cancers. Belonging to the cytosolute linker protein group, FYB1 is essential for TCR signaling and extensively studied in terms of tumor pathogenesis and metastasis. Dissecting the role of FYN binding protein 1 (FYB1) in T-ALL holds the potential to improve the treatment outcome and prognosis of T-ALL. Methods. In this study, SEs were explored using public H3K27ac ChIP-seq data derived from T-ALL cell lines, AML cell lines and hematopoietic stem and progenitor cells (HSPCs). Downstream target of FYB1 gene was identified by RNA-seq. Effects of shRNA-mediated downregulation of FYB1 and immunoglobulin lambda-like polypeptide 1 (IGLL1) on self-renewal of T-ALL cells were evaluated in vitro and/or in vivo. Results. As an SE-driven gene, overexpression of FYB1 was observed in T-ALL, according to the Cancer Cell Line Encyclopedia database. In vitro, knocking down FYB1 led to comprised growth and enhanced apoptosis of T-ALL cells. In vivo, downregulation of FYB1 significantly decreased the disease burden by suppressing tumor growth and improved survival rate. Knocking down FYB1 resulted in significantly decreased expression of IGLL1 that was also an SE-driven gene in T-ALL. As a downstream target of FYB1, IGLL1 exerted similar role as FYB1 in inhibiting growth of T-ALL cells. Conclusion. Our results suggested that FYB1 gene played important role in regulating self-renewal of T-ALL cells by activating IGLL1, representing a promising therapeutic target for T-ALL patients.http://dx.doi.org/10.1155/2023/3804605
spellingShingle Kunlong Zhang
Jun Lu
Fang Fang
Yongping Zhang
Juanjuan Yu
Yanfang Tao
Wenyuan liu
Lihui Lu
Zimu Zhang
Xinran Chu
Jianwei Wang
Xiaolu Li
Yuanyuan Tian
Zhiheng Li
Qian Li
Xu Sang
Li Ma
Ningling Wang
Jian Pan
Shaoyan Hu
Super Enhancer Regulatory Gene FYB1 Promotes the Progression of T Cell Acute Lymphoblastic Leukemia by Activating IGLL1
Journal of Immunology Research
title Super Enhancer Regulatory Gene FYB1 Promotes the Progression of T Cell Acute Lymphoblastic Leukemia by Activating IGLL1
title_full Super Enhancer Regulatory Gene FYB1 Promotes the Progression of T Cell Acute Lymphoblastic Leukemia by Activating IGLL1
title_fullStr Super Enhancer Regulatory Gene FYB1 Promotes the Progression of T Cell Acute Lymphoblastic Leukemia by Activating IGLL1
title_full_unstemmed Super Enhancer Regulatory Gene FYB1 Promotes the Progression of T Cell Acute Lymphoblastic Leukemia by Activating IGLL1
title_short Super Enhancer Regulatory Gene FYB1 Promotes the Progression of T Cell Acute Lymphoblastic Leukemia by Activating IGLL1
title_sort super enhancer regulatory gene fyb1 promotes the progression of t cell acute lymphoblastic leukemia by activating igll1
url http://dx.doi.org/10.1155/2023/3804605
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