Dermatomyositis: A Multifaceted Autoimmune Connective Tissue Disorder: Series of Seven Cases
Dermatomyositis is a rare connective tissue disorder having a wide array of characteristic cutaneous and systemic manifestations. There is an established paraneoplastic association of malignancy with dermatomyositis which is seen in adult patients as compared to juvenile (with an increased risk of m...
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2025-04-01
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| Series: | Clinical Dermatology Review |
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| Online Access: | https://journals.lww.com/10.4103/cdr.cdr_108_24 |
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| author | Mrunali Anil Joshi Pooja Agarwal Kalgi Baxi Raju Gisaram Chaudhary Vama Vijay Patel |
| author_facet | Mrunali Anil Joshi Pooja Agarwal Kalgi Baxi Raju Gisaram Chaudhary Vama Vijay Patel |
| author_sort | Mrunali Anil Joshi |
| collection | DOAJ |
| description | Dermatomyositis is a rare connective tissue disorder having a wide array of characteristic cutaneous and systemic manifestations. There is an established paraneoplastic association of malignancy with dermatomyositis which is seen in adult patients as compared to juvenile (with an increased risk of malignancy in 15%–30% cases in adult dermatomyositis, without any increased risk of association in juvenile dermatomyositis), which can be seen in our case series. There is also a case linking neurological associations of dermatomyositis to generalized tonic–clonic seizures. We discuss the importance of dermatomyositis, as a potential differential diagnosis among the cases presenting with bulbar symptoms such as dyspnea and dysphagia which can be life-threatening. |
| format | Article |
| id | doaj-art-700ea96476bb4dfaa5ddfd5ecbd40a55 |
| institution | OA Journals |
| issn | 2542-551X 2542-5528 |
| language | English |
| publishDate | 2025-04-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Clinical Dermatology Review |
| spelling | doaj-art-700ea96476bb4dfaa5ddfd5ecbd40a552025-08-20T01:47:32ZengWolters Kluwer Medknow PublicationsClinical Dermatology Review2542-551X2542-55282025-04-019216116610.4103/cdr.cdr_108_24Dermatomyositis: A Multifaceted Autoimmune Connective Tissue Disorder: Series of Seven CasesMrunali Anil JoshiPooja AgarwalKalgi BaxiRaju Gisaram ChaudharyVama Vijay PatelDermatomyositis is a rare connective tissue disorder having a wide array of characteristic cutaneous and systemic manifestations. There is an established paraneoplastic association of malignancy with dermatomyositis which is seen in adult patients as compared to juvenile (with an increased risk of malignancy in 15%–30% cases in adult dermatomyositis, without any increased risk of association in juvenile dermatomyositis), which can be seen in our case series. There is also a case linking neurological associations of dermatomyositis to generalized tonic–clonic seizures. We discuss the importance of dermatomyositis, as a potential differential diagnosis among the cases presenting with bulbar symptoms such as dyspnea and dysphagia which can be life-threatening.https://journals.lww.com/10.4103/cdr.cdr_108_24adultautoimmunedermatomyositisdrugjuvenilemalignancyseizures |
| spellingShingle | Mrunali Anil Joshi Pooja Agarwal Kalgi Baxi Raju Gisaram Chaudhary Vama Vijay Patel Dermatomyositis: A Multifaceted Autoimmune Connective Tissue Disorder: Series of Seven Cases Clinical Dermatology Review adult autoimmune dermatomyositis drug juvenile malignancy seizures |
| title | Dermatomyositis: A Multifaceted Autoimmune Connective Tissue Disorder: Series of Seven Cases |
| title_full | Dermatomyositis: A Multifaceted Autoimmune Connective Tissue Disorder: Series of Seven Cases |
| title_fullStr | Dermatomyositis: A Multifaceted Autoimmune Connective Tissue Disorder: Series of Seven Cases |
| title_full_unstemmed | Dermatomyositis: A Multifaceted Autoimmune Connective Tissue Disorder: Series of Seven Cases |
| title_short | Dermatomyositis: A Multifaceted Autoimmune Connective Tissue Disorder: Series of Seven Cases |
| title_sort | dermatomyositis a multifaceted autoimmune connective tissue disorder series of seven cases |
| topic | adult autoimmune dermatomyositis drug juvenile malignancy seizures |
| url | https://journals.lww.com/10.4103/cdr.cdr_108_24 |
| work_keys_str_mv | AT mrunalianiljoshi dermatomyositisamultifacetedautoimmuneconnectivetissuedisorderseriesofsevencases AT poojaagarwal dermatomyositisamultifacetedautoimmuneconnectivetissuedisorderseriesofsevencases AT kalgibaxi dermatomyositisamultifacetedautoimmuneconnectivetissuedisorderseriesofsevencases AT rajugisaramchaudhary dermatomyositisamultifacetedautoimmuneconnectivetissuedisorderseriesofsevencases AT vamavijaypatel dermatomyositisamultifacetedautoimmuneconnectivetissuedisorderseriesofsevencases |