Blastic Plasmacytoid Dendritic Cell Neoplasm Mimicking Erythema Nodosum: A Case Report
Blastic plasmacytoid dendritic cell neoplasm (BPDCN), previously known as blastic natural killer cell lymphoma, is a rare, difficult-to-diagnose, and aggressive hematologic malignancy. Skin lesions are the initial presentation of BPDCN in 64% to 77% of cases, characterized by brown to purple nodular...
Saved in:
| Main Authors: | , , , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
American College of Physicians
2023-02-01
|
| Series: | Annals of Internal Medicine: Clinical Cases |
| Online Access: | https://www.acpjournals.org/doi/10.7326/aimcc.2022.0920 |
| Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
| _version_ | 1850198080947748864 |
|---|---|
| author | Marino Hirata Nozomu Yoshino Maya Takazawa Hisashi Oshiro Shinichi Kako Hitoshi Sugawara |
| author_facet | Marino Hirata Nozomu Yoshino Maya Takazawa Hisashi Oshiro Shinichi Kako Hitoshi Sugawara |
| author_sort | Marino Hirata |
| collection | DOAJ |
| description | Blastic plasmacytoid dendritic cell neoplasm (BPDCN), previously known as blastic natural killer cell lymphoma, is a rare, difficult-to-diagnose, and aggressive hematologic malignancy. Skin lesions are the initial presentation of BPDCN in 64% to 77% of cases, characterized by brown to purple nodular or bruised macular lesions in solitary or multiple locations. Here, we report the case of a 57-year-old man who initially presented with refractory erythema nodosum symptoms, including fever, arthritis, and painful erythema, and was finally diagnosed with BPDCN after a second skin biopsy. This case illustrates that skin lesions caused by BPDCN mimic ordinary erythema nodosum. |
| format | Article |
| id | doaj-art-6ff878b320914132a8f6944d1c8d2b9e |
| institution | OA Journals |
| issn | 2767-7664 |
| language | English |
| publishDate | 2023-02-01 |
| publisher | American College of Physicians |
| record_format | Article |
| series | Annals of Internal Medicine: Clinical Cases |
| spelling | doaj-art-6ff878b320914132a8f6944d1c8d2b9e2025-08-20T02:12:58ZengAmerican College of PhysiciansAnnals of Internal Medicine: Clinical Cases2767-76642023-02-012210.7326/aimcc.2022.0920Blastic Plasmacytoid Dendritic Cell Neoplasm Mimicking Erythema Nodosum: A Case ReportMarino Hirata0Nozomu Yoshino1Maya Takazawa2Hisashi Oshiro3Shinichi Kako4Hitoshi Sugawara51Saitama Medical Center, Jichi Medical University, Saitama City, Japan1Saitama Medical Center, Jichi Medical University, Saitama City, Japan1Saitama Medical Center, Jichi Medical University, Saitama City, Japan1Saitama Medical Center, Jichi Medical University, Saitama City, Japan1Saitama Medical Center, Jichi Medical University, Saitama City, Japan1Saitama Medical Center, Jichi Medical University, Saitama City, JapanBlastic plasmacytoid dendritic cell neoplasm (BPDCN), previously known as blastic natural killer cell lymphoma, is a rare, difficult-to-diagnose, and aggressive hematologic malignancy. Skin lesions are the initial presentation of BPDCN in 64% to 77% of cases, characterized by brown to purple nodular or bruised macular lesions in solitary or multiple locations. Here, we report the case of a 57-year-old man who initially presented with refractory erythema nodosum symptoms, including fever, arthritis, and painful erythema, and was finally diagnosed with BPDCN after a second skin biopsy. This case illustrates that skin lesions caused by BPDCN mimic ordinary erythema nodosum.https://www.acpjournals.org/doi/10.7326/aimcc.2022.0920 |
| spellingShingle | Marino Hirata Nozomu Yoshino Maya Takazawa Hisashi Oshiro Shinichi Kako Hitoshi Sugawara Blastic Plasmacytoid Dendritic Cell Neoplasm Mimicking Erythema Nodosum: A Case Report Annals of Internal Medicine: Clinical Cases |
| title | Blastic Plasmacytoid Dendritic Cell Neoplasm Mimicking Erythema Nodosum: A Case Report |
| title_full | Blastic Plasmacytoid Dendritic Cell Neoplasm Mimicking Erythema Nodosum: A Case Report |
| title_fullStr | Blastic Plasmacytoid Dendritic Cell Neoplasm Mimicking Erythema Nodosum: A Case Report |
| title_full_unstemmed | Blastic Plasmacytoid Dendritic Cell Neoplasm Mimicking Erythema Nodosum: A Case Report |
| title_short | Blastic Plasmacytoid Dendritic Cell Neoplasm Mimicking Erythema Nodosum: A Case Report |
| title_sort | blastic plasmacytoid dendritic cell neoplasm mimicking erythema nodosum a case report |
| url | https://www.acpjournals.org/doi/10.7326/aimcc.2022.0920 |
| work_keys_str_mv | AT marinohirata blasticplasmacytoiddendriticcellneoplasmmimickingerythemanodosumacasereport AT nozomuyoshino blasticplasmacytoiddendriticcellneoplasmmimickingerythemanodosumacasereport AT mayatakazawa blasticplasmacytoiddendriticcellneoplasmmimickingerythemanodosumacasereport AT hisashioshiro blasticplasmacytoiddendriticcellneoplasmmimickingerythemanodosumacasereport AT shinichikako blasticplasmacytoiddendriticcellneoplasmmimickingerythemanodosumacasereport AT hitoshisugawara blasticplasmacytoiddendriticcellneoplasmmimickingerythemanodosumacasereport |