STRchive: a dynamic resource detailing population-level and locus-specific insights at tandem repeat disease loci

Abstract Approximately 8% of the human genome consists of repetitive elements called tandem repeats (TRs): short tandem repeats (STRs) of 1–6 bp motifs and variable number tandem repeats (VNTRs) of 7 + bp motifs. TR variants contribute to several dozen monogenic diseases but remain understudied and...

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Main Authors: Laurel Hiatt, Ben Weisburd, Egor Dolzhenko, Vincent Rubinetti, Akshay K. Avvaru, Grace E. VanNoy, Nehir Edibe Kurtas, Heidi L. Rehm, Aaron R. Quinlan, Harriet Dashnow
Format: Article
Language:English
Published: BMC 2025-03-01
Series:Genome Medicine
Online Access:https://doi.org/10.1186/s13073-025-01454-4
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author Laurel Hiatt
Ben Weisburd
Egor Dolzhenko
Vincent Rubinetti
Akshay K. Avvaru
Grace E. VanNoy
Nehir Edibe Kurtas
Heidi L. Rehm
Aaron R. Quinlan
Harriet Dashnow
author_facet Laurel Hiatt
Ben Weisburd
Egor Dolzhenko
Vincent Rubinetti
Akshay K. Avvaru
Grace E. VanNoy
Nehir Edibe Kurtas
Heidi L. Rehm
Aaron R. Quinlan
Harriet Dashnow
author_sort Laurel Hiatt
collection DOAJ
description Abstract Approximately 8% of the human genome consists of repetitive elements called tandem repeats (TRs): short tandem repeats (STRs) of 1–6 bp motifs and variable number tandem repeats (VNTRs) of 7 + bp motifs. TR variants contribute to several dozen monogenic diseases but remain understudied and enigmatic. It remains comparatively challenging to interpret the clinical significance of TR variants, particularly relative to single nucleotide variants. We present STRchive ( http://strchive.org/ ), a dynamic resource consolidating information on TR disease loci from the research literature, up-to-date clinical resources, and large-scale genomic databases, streamlining TR variant interpretation at disease-associated loci.
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institution Kabale University
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series Genome Medicine
spelling doaj-art-6fbd064dceef43f386062cf2f22fb55c2025-08-20T03:40:50ZengBMCGenome Medicine1756-994X2025-03-0117111910.1186/s13073-025-01454-4STRchive: a dynamic resource detailing population-level and locus-specific insights at tandem repeat disease lociLaurel Hiatt0Ben Weisburd1Egor Dolzhenko2Vincent Rubinetti3Akshay K. Avvaru4Grace E. VanNoy5Nehir Edibe Kurtas6Heidi L. Rehm7Aaron R. Quinlan8Harriet Dashnow9Department of Human Genetics, University of UtahProgram in Medical and Population Genetics, Broad Institute of MIT and HarvardPacific Biosciences of CaliforniaDepartment of Biomedical Informatics, University of Colorado Anschutz Medical CampusDepartment of Biomedical Informatics, University of Colorado Anschutz Medical CampusProgram in Medical and Population Genetics, Broad Institute of MIT and HarvardProgram in Medical and Population Genetics, Broad Institute of MIT and HarvardProgram in Medical and Population Genetics, Broad Institute of MIT and HarvardDepartment of Human Genetics, University of UtahDepartment of Human Genetics, University of UtahAbstract Approximately 8% of the human genome consists of repetitive elements called tandem repeats (TRs): short tandem repeats (STRs) of 1–6 bp motifs and variable number tandem repeats (VNTRs) of 7 + bp motifs. TR variants contribute to several dozen monogenic diseases but remain understudied and enigmatic. It remains comparatively challenging to interpret the clinical significance of TR variants, particularly relative to single nucleotide variants. We present STRchive ( http://strchive.org/ ), a dynamic resource consolidating information on TR disease loci from the research literature, up-to-date clinical resources, and large-scale genomic databases, streamlining TR variant interpretation at disease-associated loci.https://doi.org/10.1186/s13073-025-01454-4
spellingShingle Laurel Hiatt
Ben Weisburd
Egor Dolzhenko
Vincent Rubinetti
Akshay K. Avvaru
Grace E. VanNoy
Nehir Edibe Kurtas
Heidi L. Rehm
Aaron R. Quinlan
Harriet Dashnow
STRchive: a dynamic resource detailing population-level and locus-specific insights at tandem repeat disease loci
Genome Medicine
title STRchive: a dynamic resource detailing population-level and locus-specific insights at tandem repeat disease loci
title_full STRchive: a dynamic resource detailing population-level and locus-specific insights at tandem repeat disease loci
title_fullStr STRchive: a dynamic resource detailing population-level and locus-specific insights at tandem repeat disease loci
title_full_unstemmed STRchive: a dynamic resource detailing population-level and locus-specific insights at tandem repeat disease loci
title_short STRchive: a dynamic resource detailing population-level and locus-specific insights at tandem repeat disease loci
title_sort strchive a dynamic resource detailing population level and locus specific insights at tandem repeat disease loci
url https://doi.org/10.1186/s13073-025-01454-4
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