Axenfeld-Rieger syndrome associated with truncus arteriosus: a case report

The aim of this presentation was to report a case with Axenfeld-Rieger syndrome (ARS) associated with truncus arteriosus (TA). We present a 14-year-old boy with ARS in whom the diagnosis was confirmed by ophthalmologic examination and developmental defects of the teeth and facial bones. Echoc...

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Main Authors: Ozlem Gürbüz-Köz, Tuba Atalay, Cem Köz, Hatice Ilgin-Ruhi, Alper Yarangümeli, Gülcan Kural
Format: Article
Language:English
Published: Hacettepe University Institute of Child Health 2007-10-01
Series:The Turkish Journal of Pediatrics
Online Access:https://turkjpediatr.org/article/view/2584
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author Ozlem Gürbüz-Köz
Tuba Atalay
Cem Köz
Hatice Ilgin-Ruhi
Alper Yarangümeli
Gülcan Kural
author_facet Ozlem Gürbüz-Köz
Tuba Atalay
Cem Köz
Hatice Ilgin-Ruhi
Alper Yarangümeli
Gülcan Kural
author_sort Ozlem Gürbüz-Köz
collection DOAJ
description The aim of this presentation was to report a case with Axenfeld-Rieger syndrome (ARS) associated with truncus arteriosus (TA). We present a 14-year-old boy with ARS in whom the diagnosis was confirmed by ophthalmologic examination and developmental defects of the teeth and facial bones. Echocardiography revealed TA. With this case demonstrating the association between ARS and TA, the range of reported cardiac malformations is enlarged and the importance of cardiologic evaluation is emphasized in patients with ARS.
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institution DOAJ
issn 0041-4301
2791-6421
language English
publishDate 2007-10-01
publisher Hacettepe University Institute of Child Health
record_format Article
series The Turkish Journal of Pediatrics
spelling doaj-art-6f37957f013d4b46b6be2d21bfeec1e22025-08-20T03:00:54ZengHacettepe University Institute of Child HealthThe Turkish Journal of Pediatrics0041-43012791-64212007-10-01494Axenfeld-Rieger syndrome associated with truncus arteriosus: a case reportOzlem Gürbüz-Köz0Tuba AtalayCem KözHatice Ilgin-RuhiAlper YarangümeliGülcan Kural1st Eye Clinic, Ankara Numune Training and Research Hospital, Turkey. The aim of this presentation was to report a case with Axenfeld-Rieger syndrome (ARS) associated with truncus arteriosus (TA). We present a 14-year-old boy with ARS in whom the diagnosis was confirmed by ophthalmologic examination and developmental defects of the teeth and facial bones. Echocardiography revealed TA. With this case demonstrating the association between ARS and TA, the range of reported cardiac malformations is enlarged and the importance of cardiologic evaluation is emphasized in patients with ARS. https://turkjpediatr.org/article/view/2584
spellingShingle Ozlem Gürbüz-Köz
Tuba Atalay
Cem Köz
Hatice Ilgin-Ruhi
Alper Yarangümeli
Gülcan Kural
Axenfeld-Rieger syndrome associated with truncus arteriosus: a case report
The Turkish Journal of Pediatrics
title Axenfeld-Rieger syndrome associated with truncus arteriosus: a case report
title_full Axenfeld-Rieger syndrome associated with truncus arteriosus: a case report
title_fullStr Axenfeld-Rieger syndrome associated with truncus arteriosus: a case report
title_full_unstemmed Axenfeld-Rieger syndrome associated with truncus arteriosus: a case report
title_short Axenfeld-Rieger syndrome associated with truncus arteriosus: a case report
title_sort axenfeld rieger syndrome associated with truncus arteriosus a case report
url https://turkjpediatr.org/article/view/2584
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AT tubaatalay axenfeldriegersyndromeassociatedwithtruncusarteriosusacasereport
AT cemkoz axenfeldriegersyndromeassociatedwithtruncusarteriosusacasereport
AT haticeilginruhi axenfeldriegersyndromeassociatedwithtruncusarteriosusacasereport
AT alperyarangumeli axenfeldriegersyndromeassociatedwithtruncusarteriosusacasereport
AT gulcankural axenfeldriegersyndromeassociatedwithtruncusarteriosusacasereport