Sjögren syndrome from a dermatological perspective: A retrospective study of 185 SSA‐Ro positive patients

Abstract Background Sjögren syndrome (SS) is a systemic autoimmune disease characterised by oral and ocular mucosal dryness. Objectives Our study focused on skin manifestations of SS. The differences between primary SS (pSS) and secondary SS (sSS) were investigated. Furthermore, we elucidated factor...

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Main Authors: Fiona André, Martha Bujak, Nina Frischhut, Andreas Kronbichler, Norbert Sepp, Gudrun Ratzinger, Barbara Böckle
Format: Article
Language:English
Published: Wiley 2024-12-01
Series:JEADV Clinical Practice
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Online Access:https://doi.org/10.1002/jvc2.498
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author Fiona André
Martha Bujak
Nina Frischhut
Andreas Kronbichler
Norbert Sepp
Gudrun Ratzinger
Barbara Böckle
author_facet Fiona André
Martha Bujak
Nina Frischhut
Andreas Kronbichler
Norbert Sepp
Gudrun Ratzinger
Barbara Böckle
author_sort Fiona André
collection DOAJ
description Abstract Background Sjögren syndrome (SS) is a systemic autoimmune disease characterised by oral and ocular mucosal dryness. Objectives Our study focused on skin manifestations of SS. The differences between primary SS (pSS) and secondary SS (sSS) were investigated. Furthermore, we elucidated factors predicting internal organ involvement. Methods This was a single centre retrospective cohort study. We analysed clinical and laboratory data from 185 Ro‐SSA positive SS patients between January 2000 and December 2016. Results Skin manifestations were present in 74.9% (n = 137) of SS patients. Dermatitis and Lupus erythematosus (LE)‐specific skin manifestations were present in 34.1% (n = 63) and 21.6% (n = 40) of SS patients respectively. 65.9% (n = 122) of SS patients had internal organ involvement, with 53% (n = 98) presenting neuropsychiatric manifestations. Several risk factors for internal organ involvement were identified: presence of myalgia/arthralgia (odds ratio [OR] = 3.05, confidence interval [CI] 1.29−7.22), fatigue (OR = 2.53, CI 1.11−5.73) and age older than 50 years (OR = 2.23, CI 1.01−4.93). Conclusions Internal organ involvement is frequent in SS, however there is no significant difference between pSS and sSS concerning its occurrence.
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spelling doaj-art-6f2f90ce039945eaaed88971f7c7b7f92025-08-20T02:18:20ZengWileyJEADV Clinical Practice2768-65662024-12-01351478148610.1002/jvc2.498Sjögren syndrome from a dermatological perspective: A retrospective study of 185 SSA‐Ro positive patientsFiona André0Martha Bujak1Nina Frischhut2Andreas Kronbichler3Norbert Sepp4Gudrun Ratzinger5Barbara Böckle6Department of Dermatology, Venereology and Allergology Medical University of Innsbruck Innsbruck AustriaDepartment of Nephrology Klinik Ottakring Wien AustriaDepartment of Dermatology, Venereology and Allergology Medical University of Innsbruck Innsbruck AustriaDepartment of Internal Medicine IV Medical University of Innsbruck Innsbruck AustriaDepartment of Dermatology and Venereology Ordensklinikum Linz—Elisabethinen, Ordensklinikum Linz Linz AustriaDepartment of Dermatology, Venereology and Allergology Medical University of Innsbruck Innsbruck AustriaDepartment of Dermatology, Venereology and Allergology Medical University of Innsbruck Innsbruck AustriaAbstract Background Sjögren syndrome (SS) is a systemic autoimmune disease characterised by oral and ocular mucosal dryness. Objectives Our study focused on skin manifestations of SS. The differences between primary SS (pSS) and secondary SS (sSS) were investigated. Furthermore, we elucidated factors predicting internal organ involvement. Methods This was a single centre retrospective cohort study. We analysed clinical and laboratory data from 185 Ro‐SSA positive SS patients between January 2000 and December 2016. Results Skin manifestations were present in 74.9% (n = 137) of SS patients. Dermatitis and Lupus erythematosus (LE)‐specific skin manifestations were present in 34.1% (n = 63) and 21.6% (n = 40) of SS patients respectively. 65.9% (n = 122) of SS patients had internal organ involvement, with 53% (n = 98) presenting neuropsychiatric manifestations. Several risk factors for internal organ involvement were identified: presence of myalgia/arthralgia (odds ratio [OR] = 3.05, confidence interval [CI] 1.29−7.22), fatigue (OR = 2.53, CI 1.11−5.73) and age older than 50 years (OR = 2.23, CI 1.01−4.93). Conclusions Internal organ involvement is frequent in SS, however there is no significant difference between pSS and sSS concerning its occurrence.https://doi.org/10.1002/jvc2.498internal organ involvementSjögren syndromeskin manifestations
spellingShingle Fiona André
Martha Bujak
Nina Frischhut
Andreas Kronbichler
Norbert Sepp
Gudrun Ratzinger
Barbara Böckle
Sjögren syndrome from a dermatological perspective: A retrospective study of 185 SSA‐Ro positive patients
JEADV Clinical Practice
internal organ involvement
Sjögren syndrome
skin manifestations
title Sjögren syndrome from a dermatological perspective: A retrospective study of 185 SSA‐Ro positive patients
title_full Sjögren syndrome from a dermatological perspective: A retrospective study of 185 SSA‐Ro positive patients
title_fullStr Sjögren syndrome from a dermatological perspective: A retrospective study of 185 SSA‐Ro positive patients
title_full_unstemmed Sjögren syndrome from a dermatological perspective: A retrospective study of 185 SSA‐Ro positive patients
title_short Sjögren syndrome from a dermatological perspective: A retrospective study of 185 SSA‐Ro positive patients
title_sort sjogren syndrome from a dermatological perspective a retrospective study of 185 ssa ro positive patients
topic internal organ involvement
Sjögren syndrome
skin manifestations
url https://doi.org/10.1002/jvc2.498
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