Heterotaxy Syndrome and Spectrum of Cardiac Involvement

Heterotaxy syndrome, a birth defect characterized by abnormal arrangement of organs, is strongly associated with complex congenital heart disease (CHD). This syndrome, which arises from disruptions in early embryonic development, particularly in the establishment of left-right asymmetry, leads to a...

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Main Authors: Munesh Tomar, Maitri Chaudhuri
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2025-01-01
Series:Journal of the Indian Academy of Echocardiography & Cardiovascular Imaging
Subjects:
Online Access:https://journals.lww.com/10.4103/jiae.jiae_10_25
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author Munesh Tomar
Maitri Chaudhuri
author_facet Munesh Tomar
Maitri Chaudhuri
author_sort Munesh Tomar
collection DOAJ
description Heterotaxy syndrome, a birth defect characterized by abnormal arrangement of organs, is strongly associated with complex congenital heart disease (CHD). This syndrome, which arises from disruptions in early embryonic development, particularly in the establishment of left-right asymmetry, leads to a range of cardiac and extracardiac malformations. The severity of CHD in heterotaxy can vary, and individuals may experience both intra- and extracardiac anomalies. Here in this review article, we are discussing various aspects of cardiac involvement in heterotaxy syndrome and role of imaging modalities.
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publisher Wolters Kluwer Medknow Publications
record_format Article
series Journal of the Indian Academy of Echocardiography & Cardiovascular Imaging
spelling doaj-art-6f1e357c975c4ebc82878dc26ea765c32025-08-20T02:32:00ZengWolters Kluwer Medknow PublicationsJournal of the Indian Academy of Echocardiography & Cardiovascular Imaging2543-14632543-14712025-01-0191293710.4103/jiae.jiae_10_25Heterotaxy Syndrome and Spectrum of Cardiac InvolvementMunesh TomarMaitri ChaudhuriHeterotaxy syndrome, a birth defect characterized by abnormal arrangement of organs, is strongly associated with complex congenital heart disease (CHD). This syndrome, which arises from disruptions in early embryonic development, particularly in the establishment of left-right asymmetry, leads to a range of cardiac and extracardiac malformations. The severity of CHD in heterotaxy can vary, and individuals may experience both intra- and extracardiac anomalies. Here in this review article, we are discussing various aspects of cardiac involvement in heterotaxy syndrome and role of imaging modalities.https://journals.lww.com/10.4103/jiae.jiae_10_25cardiac anomaliesheterotaxyisomerism
spellingShingle Munesh Tomar
Maitri Chaudhuri
Heterotaxy Syndrome and Spectrum of Cardiac Involvement
Journal of the Indian Academy of Echocardiography & Cardiovascular Imaging
cardiac anomalies
heterotaxy
isomerism
title Heterotaxy Syndrome and Spectrum of Cardiac Involvement
title_full Heterotaxy Syndrome and Spectrum of Cardiac Involvement
title_fullStr Heterotaxy Syndrome and Spectrum of Cardiac Involvement
title_full_unstemmed Heterotaxy Syndrome and Spectrum of Cardiac Involvement
title_short Heterotaxy Syndrome and Spectrum of Cardiac Involvement
title_sort heterotaxy syndrome and spectrum of cardiac involvement
topic cardiac anomalies
heterotaxy
isomerism
url https://journals.lww.com/10.4103/jiae.jiae_10_25
work_keys_str_mv AT muneshtomar heterotaxysyndromeandspectrumofcardiacinvolvement
AT maitrichaudhuri heterotaxysyndromeandspectrumofcardiacinvolvement