A Case of Immunoglobulin G4-Related Disease with Extensive Multiorgan Involvements
We report a case of IgG4-related disease (IgG4-RD) with multiple ten-organ involvement. This case showed many clinical findings, such as bilateral swelling of salivary and lacrimal glands, autoimmune pancreatitis, interstitial nephritis, retroperitoneal fibrosis, periaortitis, systemic swelling of l...
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| Format: | Article |
| Language: | English |
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Wiley
2015-01-01
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| Series: | Case Reports in Rheumatology |
| Online Access: | http://dx.doi.org/10.1155/2015/392893 |
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| _version_ | 1832564336068919296 |
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| author | Kazuhiko Higashioka Kenji Yoshida Kensuke Oryoji Kazuo Kamada Shinichi Mizuki Hiroshi Tsukamoto Eisuke Yokota Koichi Akashi |
| author_facet | Kazuhiko Higashioka Kenji Yoshida Kensuke Oryoji Kazuo Kamada Shinichi Mizuki Hiroshi Tsukamoto Eisuke Yokota Koichi Akashi |
| author_sort | Kazuhiko Higashioka |
| collection | DOAJ |
| description | We report a case of IgG4-related disease (IgG4-RD) with multiple ten-organ involvement. This case showed many clinical findings, such as bilateral swelling of salivary and lacrimal glands, autoimmune pancreatitis, interstitial nephritis, retroperitoneal fibrosis, periaortitis, systemic swelling of lymph nodes, pulmonary lesions, splenomegaly, and jejunal lesions. He was suspected as having SLE or malignant lymphoma but diagnosed as having IgG4-RD by the elevated serum IgG4 level and histological findings from kidney and lymph node. We report a case of IgG4-RD with multiple ten-organ involvement that was successfully treated with prednisolone therapy. |
| format | Article |
| id | doaj-art-6c8eb1c026894187b8df04aa14585781 |
| institution | Kabale University |
| issn | 2090-6889 2090-6897 |
| language | English |
| publishDate | 2015-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Rheumatology |
| spelling | doaj-art-6c8eb1c026894187b8df04aa145857812025-02-03T01:11:15ZengWileyCase Reports in Rheumatology2090-68892090-68972015-01-01201510.1155/2015/392893392893A Case of Immunoglobulin G4-Related Disease with Extensive Multiorgan InvolvementsKazuhiko Higashioka0Kenji Yoshida1Kensuke Oryoji2Kazuo Kamada3Shinichi Mizuki4Hiroshi Tsukamoto5Eisuke Yokota6Koichi Akashi7Division of Rheumatology, Matsuyama Red Cross Hospital, 1 Bunkyo-tyo, Matsuyama, Ehime 790-0826, JapanDivision of Rheumatology, Matsuyama Red Cross Hospital, 1 Bunkyo-tyo, Matsuyama, Ehime 790-0826, JapanDivision of Rheumatology, Matsuyama Red Cross Hospital, 1 Bunkyo-tyo, Matsuyama, Ehime 790-0826, JapanDivision of Rheumatology, Matsuyama Red Cross Hospital, 1 Bunkyo-tyo, Matsuyama, Ehime 790-0826, JapanDivision of Rheumatology, Matsuyama Red Cross Hospital, 1 Bunkyo-tyo, Matsuyama, Ehime 790-0826, JapanDepartment of Medicine and Biosystemic Science, Graduate School of Medical Sciences, Kyushu University, 3-1-1 Maidashi, Higashi-ku, Fukuoka 812-8582, JapanDivision of Rheumatology, Matsuyama Red Cross Hospital, 1 Bunkyo-tyo, Matsuyama, Ehime 790-0826, JapanDepartment of Medicine and Biosystemic Science, Graduate School of Medical Sciences, Kyushu University, 3-1-1 Maidashi, Higashi-ku, Fukuoka 812-8582, JapanWe report a case of IgG4-related disease (IgG4-RD) with multiple ten-organ involvement. This case showed many clinical findings, such as bilateral swelling of salivary and lacrimal glands, autoimmune pancreatitis, interstitial nephritis, retroperitoneal fibrosis, periaortitis, systemic swelling of lymph nodes, pulmonary lesions, splenomegaly, and jejunal lesions. He was suspected as having SLE or malignant lymphoma but diagnosed as having IgG4-RD by the elevated serum IgG4 level and histological findings from kidney and lymph node. We report a case of IgG4-RD with multiple ten-organ involvement that was successfully treated with prednisolone therapy.http://dx.doi.org/10.1155/2015/392893 |
| spellingShingle | Kazuhiko Higashioka Kenji Yoshida Kensuke Oryoji Kazuo Kamada Shinichi Mizuki Hiroshi Tsukamoto Eisuke Yokota Koichi Akashi A Case of Immunoglobulin G4-Related Disease with Extensive Multiorgan Involvements Case Reports in Rheumatology |
| title | A Case of Immunoglobulin G4-Related Disease with Extensive Multiorgan Involvements |
| title_full | A Case of Immunoglobulin G4-Related Disease with Extensive Multiorgan Involvements |
| title_fullStr | A Case of Immunoglobulin G4-Related Disease with Extensive Multiorgan Involvements |
| title_full_unstemmed | A Case of Immunoglobulin G4-Related Disease with Extensive Multiorgan Involvements |
| title_short | A Case of Immunoglobulin G4-Related Disease with Extensive Multiorgan Involvements |
| title_sort | case of immunoglobulin g4 related disease with extensive multiorgan involvements |
| url | http://dx.doi.org/10.1155/2015/392893 |
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