Hydronephrosis-Induced Polycythemia with Low Erythropoietin Level: A Case Report and Literature Review

Introduction: Polycythemia is a rare condition that can be either primary or secondary. We report a case of an adolescent with progressive hydronephrosis-induced polycythemia and low erythropoietin levels, along with a thorough literature review. Report of a Case: A 17-year-old girl with epilepsy ha...

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Main Authors: Chia-Cheng Chang, Jiann-Shiuh Chen, Chao-Ching Huang, Yuan-Ning Yang, Chih-Chia Chen
Format: Article
Language:English
Published: MDPI AG 2024-12-01
Series:Children
Subjects:
Online Access:https://www.mdpi.com/2227-9067/11/12/1534
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author Chia-Cheng Chang
Jiann-Shiuh Chen
Chao-Ching Huang
Yuan-Ning Yang
Chih-Chia Chen
author_facet Chia-Cheng Chang
Jiann-Shiuh Chen
Chao-Ching Huang
Yuan-Ning Yang
Chih-Chia Chen
author_sort Chia-Cheng Chang
collection DOAJ
description Introduction: Polycythemia is a rare condition that can be either primary or secondary. We report a case of an adolescent with progressive hydronephrosis-induced polycythemia and low erythropoietin levels, along with a thorough literature review. Report of a Case: A 17-year-old girl with epilepsy had progressively elevated hemoglobin levels and low erythropoietin levels. Initial investigations, including genetic surveys and bone marrow studies, showed no evidence of polycythemia vera or myeloproliferative disorders. Further imaging studies revealed severe hydronephrosis on the left side caused by ureteropelvic junction stenosis. Following nephroureterectomy, her hemoglobin levels gradually returned to normal. Conclusions: This case highlights the potential association between hydronephrosis and polycythemia, even with low erythropoietin levels. Renal abnormalities should be considered in the differential diagnosis of pediatric patients with polycythemia, even in the absence of elevation of erythropoietin. Further research is needed to clarify this association and its pathophysiology.
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institution OA Journals
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language English
publishDate 2024-12-01
publisher MDPI AG
record_format Article
series Children
spelling doaj-art-6968380cd53648e5a7e6de2b6cee5a342025-08-20T02:00:19ZengMDPI AGChildren2227-90672024-12-011112153410.3390/children11121534Hydronephrosis-Induced Polycythemia with Low Erythropoietin Level: A Case Report and Literature ReviewChia-Cheng Chang0Jiann-Shiuh Chen1Chao-Ching Huang2Yuan-Ning Yang3Chih-Chia Chen4Department of Pediatrics, National Cheng Kung University Hospital, College of Medicine, National Cheng Kung University, Tainan 704302, TaiwanDepartment of Pediatrics, National Cheng Kung University Hospital, College of Medicine, National Cheng Kung University, Tainan 704302, TaiwanDepartment of Pediatrics, National Cheng Kung University Hospital, College of Medicine, National Cheng Kung University, Tainan 704302, TaiwanDepartment of Pediatrics, National Cheng Kung University Hospital, College of Medicine, National Cheng Kung University, Tainan 704302, TaiwanDepartment of Pediatrics, National Cheng Kung University Hospital, College of Medicine, National Cheng Kung University, Tainan 704302, TaiwanIntroduction: Polycythemia is a rare condition that can be either primary or secondary. We report a case of an adolescent with progressive hydronephrosis-induced polycythemia and low erythropoietin levels, along with a thorough literature review. Report of a Case: A 17-year-old girl with epilepsy had progressively elevated hemoglobin levels and low erythropoietin levels. Initial investigations, including genetic surveys and bone marrow studies, showed no evidence of polycythemia vera or myeloproliferative disorders. Further imaging studies revealed severe hydronephrosis on the left side caused by ureteropelvic junction stenosis. Following nephroureterectomy, her hemoglobin levels gradually returned to normal. Conclusions: This case highlights the potential association between hydronephrosis and polycythemia, even with low erythropoietin levels. Renal abnormalities should be considered in the differential diagnosis of pediatric patients with polycythemia, even in the absence of elevation of erythropoietin. Further research is needed to clarify this association and its pathophysiology.https://www.mdpi.com/2227-9067/11/12/1534polycythemiahydronephrosiserythropoietin
spellingShingle Chia-Cheng Chang
Jiann-Shiuh Chen
Chao-Ching Huang
Yuan-Ning Yang
Chih-Chia Chen
Hydronephrosis-Induced Polycythemia with Low Erythropoietin Level: A Case Report and Literature Review
Children
polycythemia
hydronephrosis
erythropoietin
title Hydronephrosis-Induced Polycythemia with Low Erythropoietin Level: A Case Report and Literature Review
title_full Hydronephrosis-Induced Polycythemia with Low Erythropoietin Level: A Case Report and Literature Review
title_fullStr Hydronephrosis-Induced Polycythemia with Low Erythropoietin Level: A Case Report and Literature Review
title_full_unstemmed Hydronephrosis-Induced Polycythemia with Low Erythropoietin Level: A Case Report and Literature Review
title_short Hydronephrosis-Induced Polycythemia with Low Erythropoietin Level: A Case Report and Literature Review
title_sort hydronephrosis induced polycythemia with low erythropoietin level a case report and literature review
topic polycythemia
hydronephrosis
erythropoietin
url https://www.mdpi.com/2227-9067/11/12/1534
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AT jiannshiuhchen hydronephrosisinducedpolycythemiawithlowerythropoietinlevelacasereportandliteraturereview
AT chaochinghuang hydronephrosisinducedpolycythemiawithlowerythropoietinlevelacasereportandliteraturereview
AT yuanningyang hydronephrosisinducedpolycythemiawithlowerythropoietinlevelacasereportandliteraturereview
AT chihchiachen hydronephrosisinducedpolycythemiawithlowerythropoietinlevelacasereportandliteraturereview