CONGENITAL AND ACQUIRED INTERFERONOPATHIES: DIFFERENTIATED APPROACHES TO THE INTERFERON-CORRECTIVE THERAPY

Various disturbances in the interferon system (IFN) — interferonopathy are considered. The classification of developed by the author is given. The clinical features of Type I interferonopathy associated with the overexpression of type I interferons in the rare Mendelian genetic diseases, some autoim...

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Main Author: I. V. Nesterova
Format: Article
Language:Russian
Published: LLC "Diagnostics and Vaccines" 2017-07-01
Series:Детские инфекции (Москва)
Subjects:
Online Access:https://detinf.elpub.ru/jour/article/view/295
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author I. V. Nesterova
author_facet I. V. Nesterova
author_sort I. V. Nesterova
collection DOAJ
description Various disturbances in the interferon system (IFN) — interferonopathy are considered. The classification of developed by the author is given. The clinical features of Type I interferonopathy associated with the overexpression of type I interferons in the rare Mendelian genetic diseases, some autoimmune diseases, the immune dysregulation syndrome, are characterized. The developed methods of targeted therapy of type I interferonopathies aimed at blocking overexpression of type I interferons as hyperproduction IFNa are described. Interferonopathies most often occur as IFN deficiency: congenital or acquired IFNa/b and IFNg deficiencies in children and adults who are associated with atypical viral or mycobacterial infections. Patients with congenital IFNa deficiency are shown to have replacement interferon therapy. With the acquired deficiency of IFNa, differentiated interferon-corrective therapy is performed. For replacement and interferon-corrective therapy, it is used with good clinical efficacy, safe, no side effects, recombinant human IFNa2b in combination with antioxidants — VIFERONR.
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spelling doaj-art-68e405a135b64b5aa9dd6bda5a444dae2025-08-20T02:03:13ZrusLLC "Diagnostics and Vaccines"Детские инфекции (Москва)2072-81072017-07-01162505310.22627/2072-8107-2017-16-2-50-53285CONGENITAL AND ACQUIRED INTERFERONOPATHIES: DIFFERENTIATED APPROACHES TO THE INTERFERON-CORRECTIVE THERAPYI. V. Nesterova0People’s Friendship University of RussiaVarious disturbances in the interferon system (IFN) — interferonopathy are considered. The classification of developed by the author is given. The clinical features of Type I interferonopathy associated with the overexpression of type I interferons in the rare Mendelian genetic diseases, some autoimmune diseases, the immune dysregulation syndrome, are characterized. The developed methods of targeted therapy of type I interferonopathies aimed at blocking overexpression of type I interferons as hyperproduction IFNa are described. Interferonopathies most often occur as IFN deficiency: congenital or acquired IFNa/b and IFNg deficiencies in children and adults who are associated with atypical viral or mycobacterial infections. Patients with congenital IFNa deficiency are shown to have replacement interferon therapy. With the acquired deficiency of IFNa, differentiated interferon-corrective therapy is performed. For replacement and interferon-corrective therapy, it is used with good clinical efficacy, safe, no side effects, recombinant human IFNa2b in combination with antioxidants — VIFERONR.https://detinf.elpub.ru/jour/article/view/295interferonopathyoverexpression of type i interferonscongenital or acquired ifn/and ifndeficienciestargeted therapyreplacementcorrective interferon-therapy
spellingShingle I. V. Nesterova
CONGENITAL AND ACQUIRED INTERFERONOPATHIES: DIFFERENTIATED APPROACHES TO THE INTERFERON-CORRECTIVE THERAPY
Детские инфекции (Москва)
interferonopathy
overexpression of type i interferons
congenital or acquired ifn/and ifndeficiencies
targeted therapy
replacement
corrective interferon-therapy
title CONGENITAL AND ACQUIRED INTERFERONOPATHIES: DIFFERENTIATED APPROACHES TO THE INTERFERON-CORRECTIVE THERAPY
title_full CONGENITAL AND ACQUIRED INTERFERONOPATHIES: DIFFERENTIATED APPROACHES TO THE INTERFERON-CORRECTIVE THERAPY
title_fullStr CONGENITAL AND ACQUIRED INTERFERONOPATHIES: DIFFERENTIATED APPROACHES TO THE INTERFERON-CORRECTIVE THERAPY
title_full_unstemmed CONGENITAL AND ACQUIRED INTERFERONOPATHIES: DIFFERENTIATED APPROACHES TO THE INTERFERON-CORRECTIVE THERAPY
title_short CONGENITAL AND ACQUIRED INTERFERONOPATHIES: DIFFERENTIATED APPROACHES TO THE INTERFERON-CORRECTIVE THERAPY
title_sort congenital and acquired interferonopathies differentiated approaches to the interferon corrective therapy
topic interferonopathy
overexpression of type i interferons
congenital or acquired ifn/and ifndeficiencies
targeted therapy
replacement
corrective interferon-therapy
url https://detinf.elpub.ru/jour/article/view/295
work_keys_str_mv AT ivnesterova congenitalandacquiredinterferonopathiesdifferentiatedapproachestotheinterferoncorrectivetherapy